Appendiceal neoplasm

disease
On this page

Also known as appendix neoplasmappendix tumorappendix tumourneoplasm of appendixneoplasm of the appendixneoplasm of vermiform appendixtumor of appendixtumor of the appendixtumor of vermiform appendixtumour of appendixtumour of the appendixtumour of vermiform appendixvermiform appendix neoplasmvermiform appendix neoplasm (disease)vermiform appendix tumorvermiform appendix tumour

Summary

Appendiceal neoplasm (MONDO:0001236) is a cancer and 13 clinical trials. Top therapeutic interventions include irinotecan. A subtype of cecal neoplasm — broader associated-gene and molecular evidence is on the parent page (see Disease family below).

At a glance

  • Classification: Cancer
  • Clinical trials: 13

Clinical features

No curated clinical features (Orphanet) for this disease.

Identifiers

Disease identifiers

FieldValue
Canonical nameappendiceal neoplasm
Mondo IDMONDO:0001236
EFOEFO:0003880
MeSHD001063
DOIDDOID:11240
NCITC4434
SNOMED CT126846004
UMLSC0003614
MedGen1629
GARD0027340
Anatomy (UBERON)UBERON:0001154
Is cancer (heuristic)yes

Also known as: appendix neoplasm · appendix tumor · appendix tumour · neoplasm of appendix · neoplasm of the appendix · neoplasm of vermiform appendix · tumor of appendix · tumor of the appendix · tumor of vermiform appendix · tumour of appendix · tumour of the appendix · tumour of vermiform appendix · vermiform appendix neoplasm · vermiform appendix neoplasm (disease) · vermiform appendix tumor · vermiform appendix tumour

Disease family

An umbrella term covering 4 Mondo subtypes.

Classification path: disease › human disease › disease by body system or component › digestive system disorderintestinal disorder › large intestine disorder › colonic disorder › cecal disorder › cecal neoplasm › appendiceal neoplasm

Related subtypes (4): cecum villous adenoma, cecum cancer, cecum neuroendocrine tumor G1, benign neoplasm of cecum

Subtypes (4): appendix cancer, epithelial tumor of the appendix, benign neoplasm of appendix, appendix neuroendocrine neoplasm

Genetics & variants

GWAS landscape

No GWAS associations recorded — common-variant (GWAS) studies don’t cover this disease (typical for Mendelian / rare diseases). See the curated gene cohort and Mendelian overlap below.

Variant details and genetic-evidence tiers

No tiered GWAS variants or ClinVar records for this disease.

Genes & proteins

No associated-gene cohort resolved for this disease. Atlas builds the molecular and therapeutic sections — associated genes, protein families, druggability, pathways, interactions, and drug associations — by aggregating over a disease’s associated genes (resolved via GWAS / GenCC / ClinVar / CIViC), and none resolved here. This is expected for antibody-mediated, autoimmune, or otherwise non-gene-defined conditions; the curated evidence for this disease is its clinical features, GWAS susceptibility, and clinical trials (above).

Function

No pathway enrichment — requires an associated-gene cohort.

Therapeutics

Drugs indicated or in trials for this disease

No drug has an approved disease-direct ChEMBL indication for this disease.

3 drugs in clinical trials for this disease (phase 2–3, investigational): efficacy not established — a trial record, not an indication.

DrugHighest phase
MitomycinPhase 2
NintedanibPhase 2
ThalidomidePhase 2

Clinical trials & evidence

Clinical trials

Clinical trials: 13.

Phase distribution (across all retrieved trials)

PhaseTrials
Not specified8
PHASE25

Top trials by phase / activity

NCTPhaseStatusTitle
NCT02387203PHASE2ACTIVE_NOT_RECRUITINGAntibiotic Treatment and Long-term Outcomes of Patients With Pseudomyxoma Peritonei of Appendiceal Origin
NCT05913674PHASE2RECRUITINGTechnical Feasibility of Modified Early Post-Operative Intraperitoneal Chemotherapy (mEPIC)
NCT00180960PHASE2TERMINATEDTreatment of a Cancerous Disease of the Peritoneum With Complete Cytoreductive Surgery and Intraperitoneal Chemohyperthermia
NCT03246321PHASE2COMPLETEDPIPAC for Peritoneal Metastases of Colorectal Cancer
NCT05185947PHASE2COMPLETEDIntravenous and Intraperitoneal Paclitaxel and Oral Nilotinib for Peritoneal Carcinomatosis
NCT04634448Not specifiedNOT_YET_RECRUITINGThe Prevalence of Appendiceal Tumours in Periappendicular Abscess
NCT05623787Not specifiedACTIVE_NOT_RECRUITINGDiagnostic Value of Diffusion-weighted Magnetic Resonance in High-risk Colorectal and Appendiceal Neoplasms
NCT05734430Not specifiedRECRUITINGGenetics of Appendix Cancer Study
NCT02374411Not specifiedCOMPLETEDKnowledge, Attitudes, and Practice of Surgeons Toward Nutrition Support in HIPEC Patients
NCT02599116Not specifiedUNKNOWNGastrointestinal Microbiome Study of Appendiceal Cancer
NCT03510923Not specifiedCOMPLETEDSelective Rather Than Routine Histopathological Examination Following Appendectomy and Cholecystectomy
NCT05202600Not specifiedUNKNOWNJustification of Incidental Appendectomy With Respect to Pathohistological Findings
NCT05513183Not specifiedCOMPLETEDSevere Neutropenia After HIPEC Using Mitomycin-C

Drugs tested across these trials (top 30)

MoleculeMax phaseTrials referencing
IRINOTECAN41
CHEMBL45429901