Bone cancer

disease
On this page

Also known as bone neoplasmbone tumorbone tumourcancer of bonecancer of skeletal elementcancer of the bonemalignant bone neoplasmmalignant bone tumormalignant neoplasm of bonemalignant neoplasm of skeletal elementmalignant neoplasm of the bonemalignant osseous neoplasmmalignant osseous tumormalignant osseous tumourmalignant skeletal element neoplasmmalignant tumor of bonemalignant tumor of the bonemalignant tumour of bonemalignant tumour of the bone

Summary

Bone cancer (MONDO:0002129) is a cancer (an umbrella term covering 12 Mondo subtypes) with 1 GWAS associations across 3 studies and 115 clinical trials. Top therapeutic interventions include zoledronic acid anhydrous, ibandronic acid, and indocyanine green acid form. A subtype of musculoskeletal system cancer — broader associated-gene and molecular evidence is on the parent page (see Disease family below).

At a glance

  • Classification: Cancer
  • Umbrella term: 12 Mondo subtypes
  • GWAS associations: 1
  • Clinical trials: 115

Clinical features

No curated clinical features (Orphanet) for this disease.

Identifiers

Disease identifiers

FieldValue
Canonical namebone cancer
Mondo IDMONDO:0002129
EFOEFO:1000350
MeSHD001859
DOIDDOID:184
NCITC4016
SNOMED CT428281000
UMLSC0279530
MedGen79002
GARD0023070
Anatomy (UBERON)UBERON:0001474
Is cancer (heuristic)yes

Also known as: bone cancer · bone neoplasm · bone tumor · bone tumour · cancer of bone · cancer of skeletal element · cancer of the bone · malignant bone neoplasm · malignant bone tumor · malignant neoplasm of bone · malignant neoplasm of skeletal element · malignant neoplasm of the bone · malignant osseous neoplasm · malignant osseous tumor · malignant osseous tumour · malignant skeletal element neoplasm · malignant tumor of bone · malignant tumor of the bone · malignant tumour of bone · malignant tumour of the bone (+4 more)

Data availability: 1 GWAS association (3 studies).

Disease family

This is a subtype of musculoskeletal system cancer. Genetic, therapeutic, and trial evidence is largely curated at the broader-term level — see the parent page for the associated-gene cohort and molecular evidence.

Classification path: disease › human disease › disease by body system or component › musculoskeletal system disordermusculoskeletal system cancerbone cancer

Related subtypes (10): cartilage cancer, broad ligament malignant neoplasm, round ligament malignant neoplasm, laryngeal cartilage cancer, synovium cancer, uterine ligament cancer, tonsillar pillar cancer, gingival cancer, muscle cancer, ameloblastic carcinoma

Subtypes (12): bone chondrosarcoma, skull cancer, bone carcinoma, small cell osteogenic sarcoma, peripheral primitive neuroectodermal tumor of bone, sternum cancer, chest wall bone cancer, adult extraskeletal osteosarcoma, primary bone lymphoma, bone sarcoma, bone marrow cancer, cancer affecting bone of limb skeleton

Genetics & variants

GWAS landscape

1 GWAS associations across 3 studies. Top hits map to 3 distinct genes (as reported by GWAS).

Top associations by p-value

rsIDp-valueGeneRisk alleleOdds ratio
rs30251571e-07PLXDC1, RDM1P5, RDM1P5?

Top studies (by case count)

StudyLead authorYearCasesControlsTitle
GCST90481492Verma A2024588449,759Diversity and scale: Genetic architecture of 2068 traits in the VA Million Veteran Program.
GCST90651841Liu TY2025203236,808Diversity and longitudinal records: Genetic architecture of disease associations and polygenic risk in the Taiwanese Han population.
GCST90435592Zhou W2018128408,537Efficiently controlling for case-control imbalance and sample relatedness in large-scale genetic association studies.

Variant details and genetic-evidence tiers

Tier distribution (top 50 variants)

TierVariants
Tier 1: coding0
Tier 2: splice/UTR0
Tier 3: regulatory0
Tier 4: intronic/intergenic1

MAF distribution

BucketVariants
common (>=0.05)0
low_freq (0.01-0.05)0
rare (<0.01)0
unknown1

Functional consequences

ConsequenceCount
non_coding_transcript_exon_variant1

Top variants

rsIDChrPosAllelesMAFConsequenceGenep-valueTier
rs30251571739107577G>A,Tnon_coding_transcript_exon_variantPLXDC1, RDM1P5, RDM1P51e-07Tier 4: intronic/intergenic

Genes & proteins

No associated-gene cohort resolved for this disease. Atlas builds the molecular and therapeutic sections — associated genes, protein families, druggability, pathways, interactions, and drug associations — by aggregating over a disease’s associated genes (resolved via GWAS / GenCC / ClinVar / CIViC), and none resolved here. This is expected for antibody-mediated, autoimmune, or otherwise non-gene-defined conditions; the curated evidence for this disease is its clinical features, GWAS susceptibility, and clinical trials (above).

Function

No pathway enrichment — requires an associated-gene cohort.

Therapeutics

Drugs indicated for this disease

0 approved, 2 in late-stage (phase 3) trials. Disease-direct ChEMBL indications, not inferred from the associated-gene cohort below.

DrugDevelopment status
Sodium ChloridePhase 3 (in late-stage trials)
Tranexamic AcidPhase 3 (in late-stage trials)

Earlier-phase candidates (phase 2, investigational — efficacy not yet established): Carboplatin, Doxorubicin, Gemcitabine, Irinotecan, Lomustine, Paclitaxel.

Clinical trials & evidence

Clinical trials

Clinical trials: 115.

Phase distribution (across all retrieved trials)

PhaseTrials
Not specified74
PHASE210
PHASE110
PHASE38
PHASE1/PHASE26
EARLY_PHASE15
PHASE41
PHASE2/PHASE31

Top trials by phase / activity

NCTPhaseStatusTitle
NCT02905916PHASE4UNKNOWNThe Efficacy and Safety of PEG-rhG-CSF in Neutropenia After Chemotherapy
NCT05115331PHASE3ACTIVE_NOT_RECRUITINGPalliative UNConventional Hypofractionation Trial for Metastatic Bone Disease
NCT00099177PHASE3TERMINATEDA Study to Assess the Efficacy of Intravenous/Oral Bondronat (Ibandronate) in Patients With Metastatic Bone Disease Experiencing Moderate to Severe Pain
NCT00099203PHASE3TERMINATEDA Study to Assess the Efficacy of Intravenous Bondronat (Ibandronate) in Patients With Malignant and Painful Bone Disease
NCT00127387PHASE2/PHASE3TERMINATEDEnbrel Versus Placebo With Radiation Therapy to Combat Fatigue and Cachexia
NCT02153593PHASE3TERMINATEDPostoperative Bleeding Prevention in Massive Bone Tumour Resection
NCT03002454PHASE3TERMINATEDSodium Pertechnetate (99Tc) Injection Generator: 99mTc From Neutron-activation 99Mo v 99mTc From Fission 99Mo
NCT03389724PHASE3COMPLETEDPrevention of Chemotherapy Induced Cardiotoxicity in Children With Bone Tumors and Acute Myeloid Leukemia
NCT04410042PHASE3TERMINATEDTranexamic Acid Use to Reduce Blood Transfusion in Pediatric Cancer Patients Undergoing Limb Salvage Procedure
NCT04842071PHASE3UNKNOWN18F-sodium Fluoride (NaF) PET to Replace Bone Scintigraphy: Safety and Efficacy Assessment
NCT02880319PHASE2ACTIVE_NOT_RECRUITINGEvaluating Stereotactic Body Radiation Therapy for Oligometastatic Disease of the Bone
NCT03678883PHASE2ACTIVE_NOT_RECRUITING9-ING-41 in Patients With Advanced Cancers
NCT04974008PHASE2ACTIVE_NOT_RECRUITINGOsteosarcoma Maintenance Therapy With OST31-164
NCT07560410PHASE1/PHASE2NOT_YET_RECRUITINGTreatment of Truncated ALK-positive Bone Cancer Using Crizotinib (Xalkori) or Alectinib (Alecensa)
NCT00478270PHASE2WITHDRAWNA Study of Loading Doses of Intravenous Bondronat (Ibandronate) in Patients With Breast Cancer and Metastatic Bone Disease.
NCT01085565PHASE2COMPLETEDFocused Ultrasound Surgery in the Treatment of Pain Resulting From Metastatic Bone Tumors With the ExAblate 2100 Conformal Bone System
NCT01117246PHASE1/PHASE2COMPLETEDPilot Study for Palliation of Pain in Bone Metastases by MR-HIFU
NCT01313884PHASE2TERMINATEDCyclophosphamide, Doxorubicin, Vincristine w/ Irinotecan and Temozolomide in Ewings Sarcoma
NCT01336803PHASE2COMPLETEDDifferentiation of Bone Sarcomas and Osteomyelitis With Ferumoxytol-Enhanced MRI
NCT01553539PHASE2COMPLETEDTherapeutic Angiotensin-(1-7) in Treating Patients With Metastatic Sarcoma That Cannot Be Removed By Surgery
NCT01693770PHASE1/PHASE2UNKNOWNPrimary Pain Palliation in Bone Metastases Treated With Magnetic Resonance-guided Focused Ultrasound
NCT02862288PHASE1/PHASE2COMPLETEDPreliminary Study of Microwave Tumoral Ablation Performances for the Treatment of Pulmonary, Renal and Bone Neoplasia.
NCT03468075PHASE2TERMINATEDGemcitabine Plus Ascorbate for Sarcoma in Adults
NCT04310410PHASE1/PHASE2COMPLETEDFeasibility of Combined Focused Ultrasound and Radiotherapy Treatment in Patients With Painful Bone Metastasis
NCT05241132PHASE2UNKNOWNTislelizumab Combined With Chemotherapy in the Treatment of Bone Metastases of Unknown Primary
NCT06562673PHASE1/PHASE2COMPLETEDIntra-arterial Cisplatin Plus Rh-endostatin Combined With Systematic Chemotherapy in Osteosarcoma
NCT07197645PHASE1RECRUITINGSamarium Optimized for Long-lasting Analgesia in Cancerous End-stage Bone Pain
NCT00019630PHASE1COMPLETEDLiposomal Doxorubicin in Treating Children With Refractory Solid Tumors
NCT00020267PHASE1COMPLETEDVaccine Therapy in Treating Patients With Metastatic Cancer
NCT00960063PHASE1TERMINATEDA Study of Robatumumab (SCH 717454, MK-7454) in Combination With Different Treatment Regimens in Pediatric Participants With Advanced Solid Tumors (P05883, MK-7454-006)
NCT02398058PHASE1COMPLETEDTrabectedin Plus Olaparib in Metastatic or Advanced Sarcomas (TOMAS)
NCT03420963PHASE1TERMINATEDDonor Natural Killer Cells, Cyclophosphamide, and Etoposide in Treating Children and Young Adults With Relapsed or Refractory Solid Tumors
NCT03525392PHASE1TERMINATEDStudy to Evaluate the Safety and Activity (Including Distribution) of 177Lu-3BP-227 in Subjects With Solid Tumours Expressing Neurotensin Receptor Type 1.
NCT04178044PHASE1UNKNOWNPhase Ⅰ Clinical Study Protocol of GB223 Monoclonal Antibody Injection
NCT04798326PHASE1COMPLETEDComparing of the Pharmacokinetic, Pharmacodynamic, Safety and Immunogenicity of MW032 and Xgeva® in Healthy Adults
NCT06008483PHASE1UNKNOWNA Dose Finding Study to Treat Bone Tumor(s)
NCT04634227EARLY_PHASE1ACTIVE_NOT_RECRUITINGGemcitabine Plus Ascorbate for Sarcoma in Adults (Pilot)
NCT06171282EARLY_PHASE1RECRUITINGA Clinical Study on Oncolytic Virus Injection (R130) for the Treatment of Advanced Bone and Soft Tissue Tumors
NCT05075889EARLY_PHASE1COMPLETEDUtility of ICG in Benign Bone Tumors
NCT05851456EARLY_PHASE1UNKNOWNA Clinical Study on Oncolytic Virus Injection (R130) for the Treatment of Relapsed/Refractory Bone and Soft Tissue Tumors

Drugs tested across these trials (top 30)

MoleculeMax phaseTrials referencing
ZOLEDRONIC ACID ANHYDROUS46
IBANDRONIC ACID43
INDOCYANINE GREEN ACID FORM42
ALECTINIB41
FERUMOXYTOL41
GUANABENZ ACETATE41
LOMUSTINE41
SODIUM FLUORIDE F 1841
TRABECTEDIN41
FIBRIN31
FLUORIDE ION31
ELRAGLUSIB21
ROBATUMUMAB21
TALFIRASTIDE21
DOTMP SM-15311
FLUORIDE01