Childhood cerebral astrocytoma

disease
On this page

Also known as cerebral astrocytomacerebral astrocytoma, childhoodchildhood astrocytic tumor of telencephalonchildhood astrocytic tumour of telencephalonchildhood astrocytoma of cerebrumchildhood astrocytoma of the cerebrumpaediatric astrocytoma of cerebrumpaediatric astrocytoma of the cerebrumpaediatric cerebral astrocytomapediatric astrocytoma of cerebrumpediatric astrocytoma of the cerebrumpediatric cerebral astrocytomatelencephalon childhood astrocytic tumortelencephalon childhood astrocytic tumourtelencephalon juvenile astrocytoma

Summary

Childhood cerebral astrocytoma (MONDO:0004071) is a disease and 24 clinical trials. Top therapeutic interventions include bevacizumab, edotreotide gallium ga-68, and fluorodopa f 18. A subtype of childhood astrocytic tumor — broader associated-gene and molecular evidence is on the parent page (see Disease family below).

At a glance

  • Clinical trials: 24

Clinical features

No curated clinical features (Orphanet) for this disease.

Identifiers

Disease identifiers

FieldValue
Canonical namechildhood cerebral astrocytoma
Mondo IDMONDO:0004071
DOIDDOID:7007
NCITC4347
UMLSC0338070
MedGen137828
GARD0009302
Anatomy (UBERON)UBERON:0001893
Is cancer (heuristic)no

Also known as: cerebral astrocytoma · cerebral astrocytoma, childhood · childhood astrocytic tumor of telencephalon · childhood astrocytic tumour of telencephalon · childhood astrocytoma of cerebrum · childhood astrocytoma of the cerebrum · paediatric astrocytoma of cerebrum · paediatric astrocytoma of the cerebrum · paediatric cerebral astrocytoma · pediatric astrocytoma of cerebrum · pediatric astrocytoma of the cerebrum · pediatric cerebral astrocytoma · telencephalon childhood astrocytic tumor · telencephalon childhood astrocytic tumour · telencephalon juvenile astrocytoma

Disease family

This is a subtype of childhood astrocytic tumor. Genetic, therapeutic, and trial evidence is largely curated at the broader-term level — see the parent page for the associated-gene cohort and molecular evidence.

Classification path: disease › human disease › disease by etiologic mechanism › cancer or benign tumorneoplastic disease or syndromeneoplasmchildhood neoplasmchildhood astrocytic tumorchildhood cerebral astrocytoma

Related subtypes (3): childhood cerebellar astrocytic neoplasm, childhood brainstem astrocytoma, childhood pilocytic astrocytoma

Subtypes (1): childhood optic tract astrocytoma

Genetics & variants

GWAS landscape

No GWAS associations recorded — common-variant (GWAS) studies don’t cover this disease (typical for Mendelian / rare diseases). See the curated gene cohort and Mendelian overlap below.

Variant details and genetic-evidence tiers

No tiered GWAS variants or ClinVar records for this disease.

Genes & proteins

No associated-gene cohort resolved for this disease. Atlas builds the molecular and therapeutic sections — associated genes, protein families, druggability, pathways, interactions, and drug associations — by aggregating over a disease’s associated genes (resolved via GWAS / GenCC / ClinVar / CIViC), and none resolved here. This is expected for antibody-mediated, autoimmune, or otherwise non-gene-defined conditions; the curated evidence for this disease is its clinical features, GWAS susceptibility, and clinical trials (above).

Function

No pathway enrichment — requires an associated-gene cohort.

Therapeutics

No druggable-target or therapeutic data for this disease’s cohort.

Clinical trials & evidence

Clinical trials

Clinical trials: 24.

Phase distribution (across all retrieved trials)

PhaseTrials
PHASE115
PHASE25
Not specified3
PHASE2/PHASE31

Top trials by phase / activity

NCTPhaseStatusTitle
NCT01236560PHASE2/PHASE3COMPLETEDVorinostat, Temozolomide, or Bevacizumab in Combination With Radiation Therapy Followed by Bevacizumab and Temozolomide in Young Patients With Newly Diagnosed High-Grade Glioma
NCT00004078PHASE2COMPLETEDIrinotecan in Treating Children With Refractory Solid Tumors
NCT00070525PHASE2COMPLETEDTipifarnib in Treating Young Patients With Recurrent or Progressive High-Grade Glioma, Medulloblastoma, Primitive Neuroectodermal Tumor, or Brain Stem Glioma
NCT00091182PHASE2COMPLETEDOxaliplatin in Treating Young Patients With Recurrent Solid Tumors That Have Not Responded to Previous Treatment
NCT00679354PHASE2COMPLETEDCilengitide in Treating Younger Patients With Recurrent or Progressive High-Grade Glioma That Has Not Responded to Standard Therapy
NCT01462695PHASE2COMPLETEDSunitinib Malate in Treating Younger Patients With Recurrent, Refractory, or Progressive Malignant Glioma or Ependymoma
NCT00012181PHASE1COMPLETEDFlavopiridol in Treating Children With Relapsed or Refractory Solid Tumors or Lymphomas
NCT00052780PHASE1COMPLETEDTemozolomide and O6-Benzylguanine in Treating Children With Recurrent Brain Tumors
NCT00053963PHASE1COMPLETEDFR901228 in Treating Children With Refractory or Recurrent Solid Tumors or Leukemia
NCT00063973PHASE1COMPLETEDCilengitide in Treating Children With Refractory Primary Brain Tumors
NCT00077454PHASE1COMPLETEDErlotinib and Temozolomide in Treating Young Patients With Recurrent or Refractory Solid Tumors
NCT00100880PHASE1COMPLETEDLenalidomide in Treating Young Patients With Recurrent, Progressive, or Refractory CNS Tumors
NCT00101270PHASE1COMPLETEDOxaliplatin and Irinotecan in Treating Young Patients With Refractory Solid Tumors or Lymphomas
NCT00326664PHASE1COMPLETEDAZD2171 in Treating Young Patients With Recurrent, Progressive, or Refractory Primary CNS Tumors
NCT00363272PHASE1COMPLETEDIspinesib in Treating Young Patients With Relapsed or Refractory Solid Tumors or Lymphoma
NCT00638898PHASE1COMPLETEDBusulfan, Melphalan, Topotecan Hydrochloride, and a Stem Cell Transplant in Treating Patients With Newly Diagnosed or Relapsed Solid Tumor
NCT00946335PHASE1COMPLETEDABT-888 and Temozolomide in Treating Young Patients With Recurrent or Refractory CNS Tumors
NCT00994500PHASE1COMPLETEDVorinostat and Bortezomib in Treating Young Patients With Refractory or Recurrent Solid Tumors, Including Central Nervous System Tumors and Lymphoma
NCT01076530PHASE1COMPLETEDVorinostat and Temozolomide in Treating Young Patients With Relapsed or Refractory Primary Brain Tumors or Spinal Cord Tumors
NCT01088763PHASE1TERMINATEDGamma-Secretase Inhibitor RO4929097 in Treating Young Patients With Relapsed or Refractory Solid Tumors, CNS Tumors, Lymphoma, or T-Cell Leukemia
NCT02255461PHASE1TERMINATEDPalbociclib Isethionate in Treating Younger Patients With Recurrent, Progressive, or Refractory Central Nervous System Tumors
NCT00919750Not specifiedCOMPLETEDCollecting and Storing Blood and Brain Tumor Tissue Samples From Children With Brain Tumors
NCT02175745Not specifiedTERMINATED18F-FDOPA PET/CT or PET/MRI in Measuring Tumors in Patients With Newly-Diagnosed or Recurrent Gliomas
NCT02194452Not specifiedWITHDRAWNEfficacy of 68Ga-DOTATOC Positron Emission Tomography (PET) CT in Children and Young Adults With Brain Tumors

Drugs tested across these trials (top 30)

MoleculeMax phaseTrials referencing
BEVACIZUMAB41
EDOTREOTIDE GALLIUM GA-6841
FLUORODOPA F 1841
PALBOCICLIB41
ROMIDEPSIN41
SUNITINIB MALATE41
TEMOZOLOMIDE41
VORINOSTAT41
ALVOCIDIB33
CILENGITIDE32
VELIPARIB32
6-O-BENZYLGUANINE31
CEDIRANIB MALEATE31
TIPIFARNIB31
ISPINESIB21
CHEMBL422879401
CHEMBL424819501
CHEMBL54188701
CHEMBL310927801
CHEMBL406646501
CHEMBL232652301