Childhood mediastinal neurogenic neoplasm

disease
On this page

Also known as childhood mediastinal neurogenic tumorchildhood neurogenic neoplasm of mediastinumchildhood neurogenic neoplasm of the mediastinumchildhood neurogenic tumor of mediastinumchildhood neurogenic tumor of the mediastinumchildhood neurogenic tumour of mediastinumchildhood neurogenic tumour of the mediastinumpaediatric mediastinal neurogenic neoplasmpaediatric mediastinal neurogenic tumourpaediatric neurogenic neoplasm of mediastinumpaediatric neurogenic neoplasm of the mediastinumpaediatric neurogenic tumour of the mediastinumpediatric mediastinal neurogenic neoplasmpediatric mediastinal neurogenic tumorpediatric neurogenic neoplasm of mediastinumpediatric neurogenic neoplasm of the mediastinumpediatric neurogenic tumor of mediastinumpediatric neurogenic tumor of the mediastinum

Summary

Childhood mediastinal neurogenic neoplasm (MONDO:0003097) is a cancer. A subtype of mediastinal neural neoplasm — broader associated-gene and molecular evidence is on the parent page (see Disease family below).

At a glance

  • Classification: Cancer

Clinical features

No curated clinical features (Orphanet) for this disease.

Identifiers

Disease identifiers

FieldValue
Canonical namechildhood mediastinal neurogenic neoplasm
Mondo IDMONDO:0003097
DOIDDOID:4690
NCITC5429
UMLSC1332981
MedGen234134
Is cancer (heuristic)yes

Also known as: childhood mediastinal neurogenic neoplasm · childhood mediastinal neurogenic tumor · childhood neurogenic neoplasm of mediastinum · childhood neurogenic neoplasm of the mediastinum · childhood neurogenic tumor of mediastinum · childhood neurogenic tumor of the mediastinum · childhood neurogenic tumour of mediastinum · childhood neurogenic tumour of the mediastinum · paediatric mediastinal neurogenic neoplasm · paediatric mediastinal neurogenic tumour · paediatric neurogenic neoplasm of mediastinum · paediatric neurogenic neoplasm of the mediastinum · paediatric neurogenic tumour of the mediastinum · pediatric mediastinal neurogenic neoplasm · pediatric mediastinal neurogenic tumor · pediatric neurogenic neoplasm of mediastinum · pediatric neurogenic neoplasm of the mediastinum · pediatric neurogenic tumor of mediastinum · pediatric neurogenic tumor of the mediastinum

Disease family

This is a subtype of mediastinal neural neoplasm. Genetic, therapeutic, and trial evidence is largely curated at the broader-term level — see the parent page for the associated-gene cohort and molecular evidence.

Classification path: disease › human disease › disease by body system or component › nervous system disorderperipheral nervous system disorderperipheral nervous system neoplasmmediastinal neural neoplasmchildhood mediastinal neurogenic neoplasm

Related subtypes (4): mediastinum neuroblastoma, mediastinum neurofibroma, mediastinal schwannoma, malignant mediastinal neural neoplasm

Genetics & variants

GWAS landscape

No GWAS associations recorded — common-variant (GWAS) studies don’t cover this disease (typical for Mendelian / rare diseases). See the curated gene cohort and Mendelian overlap below.

Variant details and genetic-evidence tiers

No tiered GWAS variants or ClinVar records for this disease.

Genes & proteins

No associated-gene cohort resolved for this disease. Atlas builds the molecular and therapeutic sections — associated genes, protein families, druggability, pathways, interactions, and drug associations — by aggregating over a disease’s associated genes (resolved via GWAS / GenCC / ClinVar / CIViC), and none resolved here. This is expected for antibody-mediated, autoimmune, or otherwise non-gene-defined conditions; the curated evidence for this disease is its clinical features, GWAS susceptibility, and clinical trials (above).

Function

No pathway enrichment — requires an associated-gene cohort.

Therapeutics

No druggable-target or therapeutic data for this disease’s cohort.

Clinical trials & evidence

Clinical trials

Clinical trials: 0.

No linked Atlas pages yet — the cross-entity mesh grows as the corpus expands.