Congenital tracheomalacia

disease
On this page

Also known as congenital major airway collapsetracheomalacia, congenitaltype 1 tracheomalacia

Summary

Congenital tracheomalacia (MONDO:0019804) is a disease. A subtype of tracheal disorder — broader associated-gene and molecular evidence is on the parent page (see Disease family below).

At a glance

  • Prevalence: Unknown (Europe)
  • Phenotypes (HPO): 45

Clinical features

Signs & symptoms

Clinical features (HPO)

45 HPO clinical features (Orphanet curated; top 45 by frequency):

HPO IDTermFrequency
HP:0002779TracheomalaciaVery frequent (80-99%)
HP:0004468Anomalous tracheal cartilageVery frequent (80-99%)
HP:0001601LaryngomalaciaFrequent (30-79%)
HP:0002093Respiratory insufficiencyFrequent (30-79%)
HP:0002788Recurrent upper respiratory tract infectionsFrequent (30-79%)
HP:0010307StridorFrequent (30-79%)
HP:0012735CoughFrequent (30-79%)
HP:0030828WheezingFrequent (30-79%)
HP:0032355Decreased peak expiratory flowFrequent (30-79%)
HP:0000961CyanosisOccasional (5-29%)
HP:0000973Cutis laxaOccasional (5-29%)
HP:0001508Failure to thriveOccasional (5-29%)
HP:0001609Hoarse voiceOccasional (5-29%)
HP:0001622Premature birthOccasional (5-29%)
HP:0001627Abnormal heart morphologyOccasional (5-29%)
HP:0001686Loss of voiceOccasional (5-29%)
HP:0002020Gastroesophageal refluxOccasional (5-29%)
HP:0002032Esophageal atresiaOccasional (5-29%)
HP:0002090PneumoniaOccasional (5-29%)
HP:0002094DyspneaOccasional (5-29%)
HP:0002107PneumothoraxOccasional (5-29%)
HP:0002575Tracheoesophageal fistulaOccasional (5-29%)
HP:0002643Neonatal respiratory distressOccasional (5-29%)
HP:0011968Feeding difficultiesOccasional (5-29%)
HP:0012758Neurodevelopmental delayOccasional (5-29%)
HP:0030864Intercostal retractionsOccasional (5-29%)
HP:0030966Abnormal pulmonary artery morphologyOccasional (5-29%)
HP:0031245Productive coughOccasional (5-29%)
HP:0032177Parenchymal consolidationOccasional (5-29%)
HP:0001629Ventricular septal defectVery rare (<1-4%)
HP:0001631Atrial septal defectVery rare (<1-4%)
HP:0001636Tetralogy of FallotVery rare (<1-4%)
HP:0001640CardiomegalyVery rare (<1-4%)
HP:0001643Patent ductus arteriosusVery rare (<1-4%)
HP:0001750Single ventricleVery rare (<1-4%)
HP:0002089Pulmonary hypoplasiaVery rare (<1-4%)
HP:0002092Pulmonary arterial hypertensionVery rare (<1-4%)
HP:0002097EmphysemaVery rare (<1-4%)
HP:0002104ApneaVery rare (<1-4%)
HP:0002110BronchiectasisVery rare (<1-4%)
HP:0002780BronchomalaciaVery rare (<1-4%)
HP:0002786TracheobronchomalaciaVery rare (<1-4%)
HP:0010773Partial anomalous pulmonary venous returnVery rare (<1-4%)
HP:0011590Double aortic archVery rare (<1-4%)
HP:0012020Right aortic archVery rare (<1-4%)

Identifiers

Disease identifiers

FieldValue
Canonical namecongenital tracheomalacia
Mondo IDMONDO:0019804
MeSHD055090
Orphanet95430
DOIDDOID:0060313
ICD-111616705280, 303133490
NCITC98634
SNOMED CT95467005
UMLSC0392109
MedGen140261
GARD0010515
MedDRA10010654
NORD2028
Is cancer (heuristic)no

Also known as: congenital major airway collapse · Congenital Tracheomalacia · congenital tracheomalacia · tracheomalacia, congenital · type 1 tracheomalacia

Data availability: 1 HPO phenotype.

Disease family

This is a subtype of tracheal disorder. Genetic, therapeutic, and trial evidence is largely curated at the broader-term level — see the parent page for the associated-gene cohort and molecular evidence.

Classification path: disease › human disease › disease by body system or component › respiratory system disorderlower respiratory tract disordertracheal disordercongenital tracheomalacia

Related subtypes (7): tracheal calcification, tracheal stenosis, chronic obstructive pulmonary disease, tracheitis, laryngotracheoesophageal cleft, isolated tracheo-esophageal fistula, trachea neoplasm

Genetics & variants

GWAS landscape

No GWAS associations recorded — common-variant (GWAS) studies don’t cover this disease (typical for Mendelian / rare diseases). See the curated gene cohort and Mendelian overlap below.

Variant details and genetic-evidence tiers

No tiered GWAS variants or ClinVar records for this disease.

Genes & proteins

No associated-gene cohort resolved for this disease. Atlas builds the molecular and therapeutic sections — associated genes, protein families, druggability, pathways, interactions, and drug associations — by aggregating over a disease’s associated genes (resolved via GWAS / GenCC / ClinVar / CIViC), and none resolved here. This is expected for antibody-mediated, autoimmune, or otherwise non-gene-defined conditions; the curated evidence for this disease is its clinical features, GWAS susceptibility, and clinical trials (above).

Function

No pathway enrichment — requires an associated-gene cohort.

Therapeutics

No druggable-target or therapeutic data for this disease’s cohort.

Clinical trials & evidence

Clinical trials

Clinical trials: 0.

No linked Atlas pages yet — the cross-entity mesh grows as the corpus expands.