Disorder of orbital region

disease
On this page

Also known as disease of orbital regiondisease or disorder of orbital regiondisorder of eye regionorbital region diseaseorbital region disease or disorder

Summary

Disorder of orbital region (MONDO:0002022) is a disease with 9 GWAS associations across 13 studies. A subtype of disease by body system or component — broader associated-gene and molecular evidence is on the parent page (see Disease family below).

At a glance

  • GWAS associations: 9

Clinical features

No curated clinical features (Orphanet) for this disease.

Identifiers

Disease identifiers

FieldValue
Canonical namedisorder of orbital region
Mondo IDMONDO:0002022
DOIDDOID:1492
ICD-10-CMH00-H59
SNOMED CT371409005
UMLSC5886742
MedGen1863347
Anatomy (UBERON)UBERON:0004088
Is cancer (heuristic)no

Also known as: disease of orbital region · disease or disorder of orbital region · disorder of eye region · disorder of orbital region · orbital region disease · orbital region disease or disorder

Data availability: 9 GWAS associations (13 studies).

Disease family

An umbrella term covering 4 Mondo subtypes.

Classification path: disease › human disease › disease by body system or component › disorder of orbital region

Related subtypes (18): integumentary system disorder, musculoskeletal system disorder, urinary system disorder, syndromic disease, auditory system disorder, breast disorder, connective tissue disorder, digestive system disorder, cardiovascular disorder, reproductive system disorder, immune system disorder, nervous system disorder, respiratory system disorder, endocrine system disorder, hematologic disorder, mouth disorder, disorder of visual system, otorhinolaryngologic disease

Subtypes (4): eye adnexa disorder, eye disorder, orbit neoplasm, orbital dermoid cyst

Genetics & variants

GWAS landscape

9 GWAS associations across 13 studies. Top hits map to 1 distinct genes (as reported by GWAS).

Top associations by p-value

rsIDp-valueGeneRisk alleleOdds ratio
rs1444639999e-10RARB?
chr19:529086479e-09A2.64
chr7:1190631721e-08C2.19
chr2:1684842032e-08T2.29
chr7:454920172e-08A1.27
chr9:912869304e-08C3.03
chr2:555396595e-08C1.51

Top studies (by case count)

StudyLead authorYearCasesControlsTitle
GCST90473459UK Biobank Whole-Genome Sequencing Consortium20258,369450,071Whole-genome sequencing of 490,640 UK Biobank participants.
GCST90667927UK Biobank Whole-Genome Sequencing Consortium20258,369450,071Whole-genome sequencing of 490,640 UK Biobank participants.
GCST90473462UK Biobank Whole-Genome Sequencing Consortium20257,629450,811Whole-genome sequencing of 490,640 UK Biobank participants.
GCST90667939UK Biobank Whole-Genome Sequencing Consortium20257,629450,811Whole-genome sequencing of 490,640 UK Biobank participants.
GCST90473384UK Biobank Whole-Genome Sequencing Consortium20251,143457,297Whole-genome sequencing of 490,640 UK Biobank participants.
GCST90473465UK Biobank Whole-Genome Sequencing Consortium2025610457,830Whole-genome sequencing of 490,640 UK Biobank participants.
GCST90481936Verma A2024339450,267Diversity and scale: Genetic architecture of 2068 traits in the VA Million Veteran Program.
GCST90473460UK Biobank Whole-Genome Sequencing Consortium20253269,287Whole-genome sequencing of 490,640 UK Biobank participants.
GCST90473463UK Biobank Whole-Genome Sequencing Consortium20253079,306Whole-genome sequencing of 490,640 UK Biobank participants.
GCST90726843Kim HI202626743,759Exome sequencing and analysis of 44,028 British South Asians enriched for high autozygosity.

Variant details and genetic-evidence tiers

Tier distribution (top 50 variants)

TierVariants
Tier 1: coding0
Tier 2: splice/UTR0
Tier 3: regulatory0
Tier 4: intronic/intergenic7

MAF distribution

BucketVariants
common (>=0.05)1
low_freq (0.01-0.05)0
rare (<0.01)0
unknown6

Functional consequences

ConsequenceCount
unknown6
intron_variant1

Top variants

rsIDChrPosAllelesMAFConsequenceGenep-valueTier
rs144463999325234649T>TC0.05intron_variantRARB9e-10Tier 4: intronic/intergenic
chr19:529086479e-09Tier 4: intronic/intergenic
chr7:1190631721e-08Tier 4: intronic/intergenic
chr2:1684842032e-08Tier 4: intronic/intergenic
chr7:454920172e-08Tier 4: intronic/intergenic
chr9:912869304e-08Tier 4: intronic/intergenic
chr2:555396595e-08Tier 4: intronic/intergenic

Genes & proteins

No associated-gene cohort resolved for this disease. Atlas builds the molecular and therapeutic sections — associated genes, protein families, druggability, pathways, interactions, and drug associations — by aggregating over a disease’s associated genes (resolved via GWAS / GenCC / ClinVar / CIViC), and none resolved here. This is expected for antibody-mediated, autoimmune, or otherwise non-gene-defined conditions; the curated evidence for this disease is its clinical features, GWAS susceptibility, and clinical trials (above).

Function

No pathway enrichment — requires an associated-gene cohort.

Therapeutics

No druggable-target or therapeutic data for this disease’s cohort.

Clinical trials & evidence

Clinical trials

Clinical trials: 0.

No linked Atlas pages yet — the cross-entity mesh grows as the corpus expands.