Enterochromaffin cell serotonin-producing pancreatic neuroendocrine tumor

disease
On this page

Also known as carcinoid neoplasm of pancreascarcinoid neoplasm of the pancreascarcinoid tumor of pancreascarcinoid tumor of the pancreascarcinoid tumour of pancreascarcinoid tumour of the pancreasEC cell, serotonin producing pancreatic NETEC cell, serotonin producing pancreatic neuroendocrine tumorEC cell, serotonin producing pancreatic neuroendocrine tumourpancreatic carcinoid tumorpancreatic carcinoid tumourpancreatic serotonin producing neoplasmpancreatic serotonin producing tumorpancreatic serotonin producing tumourserotonin-producing neuroendocrine tumour of pancreasserotonin-producing pancreatic NETserotonin-producing pancreatic neuroendocrine tumorserotonin-producing pancreatic neuroendocrine tumourserotonin-producing PNET

Summary

Enterochromaffin cell serotonin-producing pancreatic neuroendocrine tumor (MONDO:0024504) is a cancer and 3 clinical trials. Top therapeutic interventions include paltusotine. A subtype of pancreatic neuroendocrine tumor G1 — broader associated-gene and molecular evidence is on the parent page (see Disease family below).

At a glance

  • Classification: Cancer
  • Clinical trials: 3

Clinical features

No curated clinical features (Orphanet) for this disease.

Identifiers

Disease identifiers

FieldValue
Canonical nameenterochromaffin cell serotonin-producing pancreatic neuroendocrine tumor
Mondo IDMONDO:0024504
Orphanet506090
NCITC4446
UMLSC0345933
MedGen91057
GARD0022055
Is cancer (heuristic)yes

Also known as: carcinoid neoplasm of pancreas · carcinoid neoplasm of the pancreas · carcinoid tumor of pancreas · carcinoid tumor of the pancreas · carcinoid tumour of pancreas · carcinoid tumour of the pancreas · EC cell, serotonin producing pancreatic NET · EC cell, serotonin producing pancreatic neuroendocrine tumor · EC cell, serotonin producing pancreatic neuroendocrine tumour · enterochromaffin cell serotonin-producing pancreatic neuroendocrine tumor · pancreatic carcinoid tumor · pancreatic carcinoid tumour · pancreatic serotonin producing neoplasm · pancreatic serotonin producing tumor · pancreatic serotonin producing tumour · serotonin-producing neuroendocrine tumour of pancreas · serotonin-producing pancreatic NET · serotonin-producing pancreatic neuroendocrine tumor · serotonin-producing pancreatic neuroendocrine tumour · serotonin-producing PNET (+4 more)

Disease family

This is a subtype of pancreatic neuroendocrine tumor G1. Genetic, therapeutic, and trial evidence is largely curated at the broader-term level — see the parent page for the associated-gene cohort and molecular evidence.

Classification path: disease › human disease › disease by etiologic mechanism › cancer or benign tumorneoplastic disease or syndromeneoplasmendocrine gland neoplasmneuroendocrine neoplasmcarcinoid tumorpancreatic neuroendocrine tumor G1enterochromaffin cell serotonin-producing pancreatic neuroendocrine tumor

Genetics & variants

GWAS landscape

No GWAS associations recorded — common-variant (GWAS) studies don’t cover this disease (typical for Mendelian / rare diseases). See the curated gene cohort and Mendelian overlap below.

Variant details and genetic-evidence tiers

No tiered GWAS variants or ClinVar records for this disease.

Genes & proteins

No associated-gene cohort resolved for this disease. Atlas builds the molecular and therapeutic sections — associated genes, protein families, druggability, pathways, interactions, and drug associations — by aggregating over a disease’s associated genes (resolved via GWAS / GenCC / ClinVar / CIViC), and none resolved here. This is expected for antibody-mediated, autoimmune, or otherwise non-gene-defined conditions; the curated evidence for this disease is its clinical features, GWAS susceptibility, and clinical trials (above).

Function

No pathway enrichment — requires an associated-gene cohort.

Therapeutics

No druggable-target or therapeutic data for this disease’s cohort.

Clinical trials & evidence

Clinical trials

Clinical trials: 3.

Phase distribution (across all retrieved trials)

PhaseTrials
PHASE31
PHASE21
Not specified1

Top trials by phase / activity

NCTPhaseStatusTitle
NCT07087054PHASE3RECRUITINGCarcinoid Syndrome Efficacy Study Featuring an Oral Daily Paltusotine Regimen
NCT05361668PHASE2COMPLETEDStudy to Evaluate the Safety, PK, and Dose Response of Paltusotine in Subjects With Carcinoid Syndrome
NCT04907643Not specifiedRECRUITINGVirtual Reality for GI Cancer Pain to Improve Patient Reported Outcomes

Drugs tested across these trials (top 30)

MoleculeMax phaseTrials referencing
PALTUSOTINE32