Head and neck neoplasm

disease
On this page

Also known as craniocervical region neoplasmcraniocervical region neoplasm (disease)craniocervical region tumorcraniocervical region tumourhead and neck neoplasm (excluding central nervous system)head and neck tumorhead and neck tumourneoplasm of craniocervical regionneoplasm of head and neckneoplasm of the head and necktumor of craniocervical regiontumor of head and necktumor of the head and necktumour of craniocervical regiontumour of head and necktumour of the head and neck

Summary

Head and neck neoplasm (MONDO:0005586) is a cancer (an umbrella term covering 37 Mondo subtypes) with 1 GWAS associations across 5 studies and 320 clinical trials. Top therapeutic interventions include cisplatin, afatinib, and docetaxel anhydrous. A subtype of neoplasm — broader associated-gene and molecular evidence is on the parent page (see Disease family below).

At a glance

  • Classification: Cancer
  • Umbrella term: 37 Mondo subtypes
  • GWAS associations: 1
  • Clinical trials: 320

Clinical features

No curated clinical features (Orphanet) for this disease.

Identifiers

Disease identifiers

FieldValue
Canonical namehead and neck neoplasm
Mondo IDMONDO:0005586
EFOEFO:0005950
NCITC3077
SNOMED CT255055008
UMLSC0018671
MedGen6728
Anatomy (UBERON)UBERON:0007811
Is cancer (heuristic)yes

Also known as: craniocervical region neoplasm · craniocervical region neoplasm (disease) · craniocervical region tumor · craniocervical region tumour · head and neck neoplasm · head and neck neoplasm (excluding central nervous system) · head and neck tumor · head and neck tumour · neoplasm of craniocervical region · neoplasm of head and neck · neoplasm of the head and neck · tumor of craniocervical region · tumor of head and neck · tumor of the head and neck · tumour of craniocervical region · tumour of head and neck · tumour of the head and neck

Data availability: 1 GWAS association (5 studies).

Disease family

This is a subtype of neoplasm. Genetic, therapeutic, and trial evidence is largely curated at the broader-term level — see the parent page for the associated-gene cohort and molecular evidence.

Classification path: disease › human disease › disease by etiologic mechanism › cancer or benign tumorneoplastic disease or syndromeneoplasmhead and neck neoplasm

Related subtypes (47): pre-malignant neoplasm, endocrine gland neoplasm, giant cell tumor, hematopoietic and lymphoid system neoplasm, skin neoplasm, mesenchymal cell neoplasm, epidural spinal canal neoplasm, skeletal muscle neoplasm, trophoblastic neoplasm, cancer, germ cell tumor, benign neoplasm, upper aerodigestive tract neoplasm, histiocytoma, embryonal neoplasm, epithelial neoplasm, reproductive system neoplasm, non-seminomatous lesion, odontogenic cyst, phosphaturic mesenchymal tumor, thyroglossal duct cyst, hamartoma, mesenchymoma, mesothelial neoplasm, peritoneal neoplasm, virus associated tumor, nail tumor, respiratory tract neoplasm, spindle cell neoplasm, mixed neoplasm, urinary system neoplasm, cystic neoplasm, childhood neoplasm, melanocytic neoplasm, digestive system neoplasm, nervous system neoplasm, neoplasm of thorax, connective tissue neoplasm, bronchial adenomas/carcinoids childhood, diffuse idiopathic pulmonary neuroendocrine cell hyperplasia, erythroplakia, retroperitoneal neoplasm, cardiovascular neoplasm, dermoid or epidermoid cyst of the central nervous system, connective and soft tissue neoplasm, NTRK fusion positive cancer, RET fusion positive cancer

Subtypes (37): cranial nerve neoplasm, cavernous hemangioma of face, gasserian ganglion meningioma, nasal cavity neoplasm, palatal neoplasm, nasopharyngeal neoplasm, head and neck cancer, head and neck paraganglioma, nasal cavity and paranasal sinus lethal midline granuloma, familial thyroglossal duct cyst, laryngeal neuroendocrine neoplasm, laryngotracheal angioma, facial dermoid cyst, epignathus, nasal glial heterotopia, nasal ganglioglioma, malignant epithelial tumor of salivary glands, benign epithelial tumor of salivary glands, juvenile nasopharyngeal angiofibroma, recurrent respiratory papillomatosis, ocular adnexal lymphoma, gingival neoplasm, odontogenic neoplasm, eye neoplasm, ear neoplasm, tongue neoplasm, buccal mucosa neoplasm, lip neoplasm, tonsil neoplasm, neoplasm of neck, tumor of salivary gland, neoplasm of hypopharynx, neoplasm of oropharynx, neoplasm of floor of mouth, lipoma of face, skull neoplasm, nasal cavity and paranasal sinus neoplasm

Genetics & variants

GWAS landscape

1 GWAS associations across 5 studies. Top hits map to 1 distinct genes (as reported by GWAS).

Top associations by p-value

rsIDp-valueGeneRisk alleleOdds ratio
rs1381591562e-08RAPGEF5?

Top studies (by case count)

StudyLead authorYearCasesControlsTitle
GCST90481719Verma A20249,195426,115Diversity and scale: Genetic architecture of 2068 traits in the VA Million Veteran Program.
GCST90481718Verma A20243,000113,391Diversity and scale: Genetic architecture of 2068 traits in the VA Million Veteran Program.
GCST90481717Verma A20241,16356,794Diversity and scale: Genetic architecture of 2068 traits in the VA Million Veteran Program.
GCST90435852Zhou W2018907405,975Efficiently controlling for case-control imbalance and sample relatedness in large-scale genetic association studies.
GCST90651522Liu TY2025771235,272Diversity and longitudinal records: Genetic architecture of disease associations and polygenic risk in the Taiwanese Han population.

Variant details and genetic-evidence tiers

Tier distribution (top 50 variants)

TierVariants
Tier 1: coding0
Tier 2: splice/UTR0
Tier 3: regulatory0
Tier 4: intronic/intergenic1

MAF distribution

BucketVariants
common (>=0.05)0
low_freq (0.01-0.05)0
rare (<0.01)0
unknown1

Functional consequences

ConsequenceCount
intron_variant1

Top variants

rsIDChrPosAllelesMAFConsequenceGenep-valueTier
rs138159156722171893C>Tintron_variantRAPGEF52e-08Tier 4: intronic/intergenic

Genes & proteins

No associated-gene cohort resolved for this disease. Atlas builds the molecular and therapeutic sections — associated genes, protein families, druggability, pathways, interactions, and drug associations — by aggregating over a disease’s associated genes (resolved via GWAS / GenCC / ClinVar / CIViC), and none resolved here. This is expected for antibody-mediated, autoimmune, or otherwise non-gene-defined conditions; the curated evidence for this disease is its clinical features, GWAS susceptibility, and clinical trials (above).

Function

No pathway enrichment — requires an associated-gene cohort.

Therapeutics

Drugs indicated for this disease

3 approved, 6 in late-stage (phase 3) trials. Disease-direct ChEMBL indications, not inferred from the associated-gene cohort below.

DrugDevelopment status
CetuximabApproved (phase 4)
Docetaxel AnhydrousApproved (phase 4)
TemoporfinApproved (phase 4)
CarboplatinPhase 3 (in late-stage trials)
CisplatinPhase 3 (in late-stage trials)
DostarlimabPhase 3 (in late-stage trials)
FluorouracilPhase 3 (in late-stage trials)
LapatinibPhase 3 (in late-stage trials)
PembrolizumabPhase 3 (in late-stage trials)

Earlier-phase candidates (phase 2, investigational — efficacy not yet established): Atezolizumab, Belrestotug, Feladilimab.

Clinical trials & evidence

Clinical trials

Clinical trials: 320.

Phase distribution (across all retrieved trials)

PhaseTrials
Not specified154
PHASE272
PHASE132
PHASE324
PHASE1/PHASE222
PHASE48
PHASE2/PHASE35
EARLY_PHASE13

Top trials by phase / activity

NCTPhaseStatusTitle
NCT07158164PHASE4RECRUITINGDPYD Pharmacogenomics and Fluoropyrimidine (FP) Dose-Adjustment
NCT00138827PHASE4COMPLETEDMouth Care Regimes During Radiotherapy
NCT00772681PHASE4COMPLETEDEfficacy of Chemoradiotherapy After Neoadjuvant Cisplatin and Docetaxel in the Nasopharynx Carcinoma
NCT00813631PHASE4UNKNOWNThe Effect on an Ionic Silver Dressing in Head and Neck Patients With Malignant Fungating Wound
NCT02015650PHASE4TERMINATEDCetuximab Compared to Mitomycin-C and 5-Fluorouracil for Locally Advanced Squamous Cell Carcinomas of the Head and Neck
NCT02241876PHASE4UNKNOWNTHE USE OF N-ACETYLCYSTEINE ATTENUATING CISPLATIN-INDUCED TOXICITIES BY OXIDATIVE STRESS
NCT02597582PHASE4COMPLETEDLigaSure Small Jaw® Versus Conventional Neck Dissection in Head and Neck Cancer Patients
NCT02622880PHASE4COMPLETEDComparison of Two Immunomodulatory Formulas on the Number of Postoperative Infections in Head & Neck Cancer Patients
NCT03765918PHASE3ACTIVE_NOT_RECRUITINGStudy of Pembrolizumab Given Prior to Surgery and in Combination With Radiotherapy Given Post-surgery for Advanced Head and Neck Squamous Cell Carcinoma (MK-3475-689)
NCT03840421PHASE3ACTIVE_NOT_RECRUITINGGP Vs PF As Induction Chemotherapy Combined with CCRT for Locoregionally Advanced Nasopharyngeal Carcinoma
NCT05187091PHASE3RECRUITINGThe SWOAR Trial Sparing of Swallowing and Aspiration Related Organs at Risk & Submandibular Gland With Intensity Modulated Radiotherapy Versus Standard IMRT in Head and Neck Squamous Cell Carcinomas
NCT06706401PHASE3RECRUITINGLymphocyte-Sparing And Radio-Immunotherapy in Head and Neck Carcinoma
NCT06737822PHASE3RECRUITINGUpfront Surgery Vs Induction Chemotherapy Followed By Surgery In Oral Cancers:
NCT06998069PHASE3RECRUITINGHead and Neck Cancer Study Project in the Geriatric Population
NCT00050388PHASE3COMPLETEDPhase II Trial of Allovectin-7® for Head and Neck Cancer
NCT00094081PHASE3COMPLETEDConcomitant Radiation and Cisplatin With and Without Tirapazamine in Treatment of Advanced Head and Neck Cancer
NCT00123097PHASE3COMPLETEDClinical Trial of New Elastomer for Maxillofacial Prosthetics
NCT00147862PHASE3COMPLETEDDoes Tranexamic Acid Administration Reduce Blood Loss During Head and Neck Surgery?
NCT00248235PHASE2/PHASE3COMPLETEDResistance Exercise Training for the Shoulder and Neck Following Surgery for Head and Neck Cancer
NCT00261703PHASE2/PHASE3COMPLETEDDocetaxel in Head and Neck Cancer
NCT00308880PHASE3UNKNOWNTranexamic Acid and Head and Neck Surgery Patients
NCT00363441PHASE2/PHASE3WITHDRAWNA Study of Conventional 3D Radiation vs. Intensity-Modulated Radiation in Squamous Cell Cancer of the Head and Neck
NCT00401323PHASE2/PHASE3COMPLETEDTaxotere (Docetaxel) in 1st Line Treatment of Recurrent/Metastatic Head and Neck Squamous Cell Carcinoma
NCT00412776PHASE2/PHASE3TERMINATEDStudy of Proxinium Plus Best Supportive Care Versus Best Supportive Care for Patients With Advanced Head and Neck Cancer
NCT00415194PHASE3COMPLETEDA Study for Patients With Head and Neck Cancer
NCT00995293PHASE3COMPLETEDTaxotere (Docetaxel) New Indication: Squamous Cell Carcinoma of the Head and Neck (SCCHN) Treatment Registration Trial
NCT01345669PHASE3TERMINATEDLUX-Head&Neck 2: A Phase III Trial of Afatinib (BIBW 2992) Versus Placebo for the Treatment of Head and Neck Squamous Cell Cancer After Treatment With Chemo-radiotherapy
NCT01345682PHASE3COMPLETEDLUX-Head&Neck 1: A Phase III Trial of Afatinib (BIBW2992) Versus Methotrexate for the Treatment of Recurrent and/or Metastatic (R/M) Head and Neck Squamous Cell Cancer After Platinum Based Chemotherapy
NCT01856478PHASE3COMPLETEDLUX-Head&Neck 3: Afatinib (BIBW2992) Versus Methotrexate for the Treatment of Recurrent and/or Metastatic Head and Neck Squamous Cell Cancer After Platinum Based Chemotherapy
NCT02131155PHASE3TERMINATEDLUX-Head & Neck 4: Afatinib (BIBW 2992) Versus Placebo for the Treatment of Head and Neck Squamous Cell Cancer After Treatment With Chemo-radiotherapy
NCT02183246PHASE3TERMINATEDPorfiromycin Used as an Adjuvant to Radiation Therapy in Postoperative Head and Neck Cancer Patients
NCT02442375PHASE3COMPLETEDUniform FDG-PET Guided Gradient Dose Prescription to Reduce Late Radiation Toxicity
NCT02630264PHASE3UNKNOWNE10A for the Treatment of Squamous Cell Carcinoma of the Head and Neck
NCT02918955PHASE3COMPLETEDDefinitive Chemo-Radiotherapy for Regionally Advanced Head and Neck Cancer With or Without Up-front Neck Dissection
NCT03040999PHASE3COMPLETEDStudy of Pembrolizumab (MK-3475) or Placebo With Chemoradiation in Participants With Locally Advanced Head and Neck Squamous Cell Carcinoma (MK-3475-412/KEYNOTE-412)
NCT03837808PHASE3UNKNOWNRadiotherapy Plus Concurrent Nimotuzumab or Cisplatin in Stage II-III Nasopharyngeal Carcinoma
NCT04222972PHASE3TERMINATEDA Study of Pralsetinib Versus Standard of Care for First-Line Treatment of Advanced Non-Small Cell Lung Cancer (NSCLC)
NCT02568267PHASE2ACTIVE_NOT_RECRUITINGBasket Study of Entrectinib (RXDX-101) for the Treatment of Patients With Solid Tumors Harboring NTRK 1/2/3 (Trk A/B/C), ROS1, or ALK Gene Rearrangements (Fusions)
NCT03691714PHASE2ACTIVE_NOT_RECRUITINGDurvalumab (MEDI4736) With Cetuximab in Previously Treated Recurrent or Metastatic Head and Neck Squamous Cell Carcinoma
NCT05260671PHASE2RECRUITINGPenpulimab in Combination With Cetuximab as First-line Treatment in R/M SCCHN

Drugs tested across these trials (top 30)

MoleculeMax phaseTrials referencing
CISPLATIN430
AFATINIB46
DOCETAXEL ANHYDROUS46
FLUOROURACIL42
PEMBROLIZUMAB42
PEMETREXED42
PRALSETINIB42
ACETYLCYSTEINE41
CAPECITABINE41
CETUXIMAB41
CYANOCOBALAMIN41
DACOMITINIB ANHYDROUS41
FOSTAMATINIB DISODIUM41
MITOMYCIN41
TRETINOIN41
OPORTUZUMAB MONATOX32
PORFIROMYCIN32
NIMOTUZUMAB31
TIRAPAZAMINE31
ZALUTUMUMAB31
GOLNERMINOGENE PRADENOVEC22
H11 SCFV22
LAPACHONE21
CHEMBL234795805
CHEMBL428367305
CHEMBL475911205
CHEMBL485467004
CHEMBL151089902
CHEMBL429759702
CHEMBL543550001