Idiopathic membranous glomerulonephritis

disease
On this page

Also known as Extramembranous glomerulonephritisglomerulonephritis, membranousidiopathic membranous nephropathyMBNPmembranous GNmembranous nephropathy - Idiopathicmembranous nephropathy, susceptibility toMGN

Summary

Idiopathic membranous glomerulonephritis (MONDO:0013860) is a disease and 52 clinical trials. Top therapeutic interventions include mycophenolate mofetil, belimumab, and tacrolimus anhydrous. A subtype of membranous glomerulonephritis — broader associated-gene and molecular evidence is on the parent page (see Disease family below).

At a glance

  • Prevalence: Unknown (Worldwide) [Orphanet-validated]
  • Phenotypes (HPO): 1
  • Clinical trials: 52

Clinical features

Epidemiology

Prevalence records

2 prevalence record(s), Orphanet:

TypeClassValueGeographyValidation
Annual incidence1-9 / 1 000 0000.8103WorldwideValidated
Annual incidence1-9 / 1 000 0000.9194EuropeValidated

Signs & symptoms

Clinical features (HPO)

1 HPO clinical features (Orphanet curated; top 1 by frequency):

HPO IDTermFrequency
HP:0034002Anti-phospholipase A2 receptor antibody positivityFrequent (30-79%)

Identifiers

Disease identifiers

FieldValue
Canonical nameidiopathic membranous glomerulonephritis
Mondo IDMONDO:0013860
OMIM614692
Orphanet97560
NCITC123060
SNOMED CT722119002
UMLSC0086445
MedGen39226
GARD0009180
Is cancer (heuristic)no

Also known as: Extramembranous glomerulonephritis · glomerulonephritis, membranous · idiopathic membranous nephropathy · MBNP · membranous GN · membranous nephropathy - Idiopathic · membranous nephropathy, susceptibility to · MGN

Disease family

This is a subtype of membranous glomerulonephritis. Genetic, therapeutic, and trial evidence is largely curated at the broader-term level — see the parent page for the associated-gene cohort and molecular evidence.

Classification path: disease › human disease › disease by body system or component › urinary system disorderkidney disordernephritisglomerulonephritismembranous glomerulonephritisidiopathic membranous glomerulonephritis

Genetics & variants

GWAS landscape

No GWAS associations recorded — common-variant (GWAS) studies don’t cover this disease (typical for Mendelian / rare diseases). See the curated gene cohort and Mendelian overlap below.

Variant details and genetic-evidence tiers

No tiered GWAS variants or ClinVar records for this disease.

Genes & proteins

No associated-gene cohort resolved for this disease. Atlas builds the molecular and therapeutic sections — associated genes, protein families, druggability, pathways, interactions, and drug associations — by aggregating over a disease’s associated genes (resolved via GWAS / GenCC / ClinVar / CIViC), and none resolved here. This is expected for antibody-mediated, autoimmune, or otherwise non-gene-defined conditions; the curated evidence for this disease is its clinical features, GWAS susceptibility, and clinical trials (above).

Function

No pathway enrichment — requires an associated-gene cohort.

Therapeutics

No druggable-target or therapeutic data for this disease’s cohort.

Clinical trials & evidence

Clinical trials

Clinical trials: 52.

Phase distribution (across all retrieved trials)

PhaseTrials
Not specified25
PHASE39
PHASE46
PHASE26
PHASE2/PHASE33
PHASE1/PHASE21
PHASE11
EARLY_PHASE11

Top trials by phase / activity

NCTPhaseStatusTitle
NCT05839314PHASE4RECRUITINGEffect of Huaier Granule on the Treatment of Idiopathic Membranous Nephropathy
NCT07404436PHASE4RECRUITINGRivaroxaban in Idiopathic Membranous Nephropathy
NCT00843856PHASE4COMPLETEDMycophenolate Mofetil and Tacrolimus Versus Tacrolimus for the Treatment of Idiopathic Membranous Glomerulonephritis
NCT01129557PHASE4TERMINATEDAldosterone Breakthrough During Diovan, Tekturna, and Combination Therapy in Patients With Proteinuric Kidney Disease
NCT01386554PHASE4COMPLETEDActhar for Treatment of Proteinuria in Membranous Nephropathy Patients
NCT03170323PHASE4UNKNOWNMycophenolate Mofetil Plus Steroid in the Treatment Of Patients With Progressive Idiopathic Membranous Nephropathy
NCT04745728PHASE3RECRUITINGDifferent Immunosuppressive Treatment in iMN
NCT05914155PHASE3RECRUITINGClinical Study of Rituximab for the Treatment for Idiopathic Membranous Nephropathy with Nephrotic Syndrome
NCT00135954PHASE3COMPLETEDTreatment of Patients With Idiopathic Membranous Nephropathy
NCT00135967PHASE2/PHASE3COMPLETEDMycophenolate Mofetil in Membranous Nephropathy
NCT00362531PHASE2/PHASE3COMPLETEDTacrolimus Combined With Prednisone Treatment of Idiopathic Membranous Nephropathy and Nephrotic Syndrome
NCT00404794PHASE3COMPLETEDA Study to Compare Mycophenolate Mofetil and Tacrolimus in the Treatment of Membranous Lupus Nephritis
NCT00404833PHASE3COMPLETEDMycophenolate Mofetil in Membranous Nephropathy and Focal Segmental
NCT01180036PHASE2/PHASE3COMPLETEDMEmbranous Nephropathy Trial Of Rituximab
NCT01282073PHASE3COMPLETEDMycophenolate Mofetil in Patients With Progressive Idiopathic Membranous Nephropathy
NCT01508468PHASE3COMPLETEDEvaluate Rituximab Treatment for Idiopathic Membranous Nephropathy
NCT03018535PHASE3UNKNOWNRituximab Versus Steroids and Cyclophosphamide in the Treatment of Idiopathic Membranous Nephropathy
NCT04743739PHASE3TERMINATEDRituximab Combined With Cyclosporine Versus Rituximab Alone in the Treatment of iMN
NCT00694863PHASE2COMPLETEDTreatment With Synthetic ACTH in High Risk Patients With Membranous Nephropathy
NCT01610492PHASE2COMPLETEDA Study of Belimumab in Idiopathic Membranous Glomerulonephropathy
NCT01762852PHASE2WITHDRAWNEfficacy and Safety Study of Intravenous Belimumab Versus Placebo in Subjects With Idiopathic Membranous Nephropathy
NCT02173106PHASE2UNKNOWNA Controlled Study of Steroids Plus Cyclosporin Therapy for Patients of Idiopathic Membranous Nephropathy
NCT03804359PHASE2COMPLETEDPersonalized Medicine for Membranous Nephropathy
NCT04145440PHASE1/PHASE2COMPLETEDTrial to Assess Safety and Efficacy of MOR202 in Anti-PLA2R + Membranous Nephropathy (aMN)
NCT04154787PHASE2TERMINATEDEfficacy and Safety of LNP023 Compared With Rituximab in Subjects With Idiopathic Membranous Nephropathy
NCT00805753PHASE1COMPLETEDDose-Finding Pilot Study of ACTH in Patients With Idiopathic Membranous Nephropathy
NCT07423572EARLY_PHASE1NOT_YET_RECRUITINGClinical Study of Anti-CD19/BCMA Universal Chimeric Antigen Receptor T Cells (UCAR-T) in the Treatment of Refractory Idiopathic Membranous Nephropathy (IMN)
NCT00199628Not specifiedCOMPLETEDResearch Network for Neonatal Diseases Induced by Tissular Fetomaternal Alloimmunization
NCT00302523Not specifiedCOMPLETEDTacrolimus Treatment of Patients With Idiopathic Membranous Nephropathy
NCT01093781Not specifiedWITHDRAWNAliskiren in Patients With Idiopathic Membranous Nephropathy
NCT01161459Not specifiedCOMPLETEDTreatment of Idiopathic Membranous Nephropathy With Tripterygium Wilfordii Plus Steroid vs Tacrolimus Plus Steroid
NCT01799460Not specifiedUNKNOWNStudy on Single-nucleotide-polymorphism in Idiopathic Membranous Nephropathy
NCT01845688Not specifiedCOMPLETEDClinical Study of QingReMoShen Granule to Treat Idiopathic Membranous Nephropathy
NCT02610595Not specifiedUNKNOWNStudy on the Therapeutic Effect of TCM Treatment for MDR MN
NCT03466801Not specifiedTERMINATEDThe Efficacy of Prednisone and Combination Therapy With Methylprednisolone and Cyclophosphamide on IMN in Stage I.
NCT03475602Not specifiedTERMINATEDMembranous Nephropathy-associated Serological Antibody Predict the Prognosis of Idiopathic Membranous Nephropathy
NCT03549663Not specifiedUNKNOWNTacrolimus Monotherapy for Idiopathic Membranous Nephropathy (IMN)
NCT03864250Not specifiedUNKNOWNTacrolimus Monotherapy for Idiopathic Membranous Nephropathy
NCT03880643Not specifiedCOMPLETEDRituximab in Refractory Primary Membranous Nephropathy
NCT04498962Not specifiedUNKNOWNThe Effect of Danzhu Fuyuan Granule as Adjunctive Therapy for Chronic Stable Angina, Vascular Dementia and Idiopathic Membranous Nephropathy: A Bayesian Basket Trial

Drugs tested across these trials (top 30)

MoleculeMax phaseTrials referencing
MYCOPHENOLATE MOFETIL45
BELIMUMAB42
TACROLIMUS ANHYDROUS42
ALISKIREN41
ANGIOTENSIN II41
CHLORAMBUCIL41
CORTICOTROPIN41
COSYNTROPIN41
CYCLOSPORINE41
IPTACOPAN41
RIVAROXABAN41
VALSARTAN41
WARFARIN SODIUM41
FELZARTAMAB31
CHEMBL456492301
CHEMBL11562201
CHEMBL40635201