IgG4-related mesenteritis

Summary

IgG4-related mesenteritis (MONDO:0016544) is a disease and 1 clinical trial. A subtype of immunoglobulin G4-related sclerosing disease — broader associated-gene and molecular evidence is on the parent page (see Disease family below).

At a glance

• Prevalence: Unknown (Worldwide)
• Clinical trials: 1

Clinical features

No curated clinical features (Orphanet) for this disease.

Identifiers

Disease identifiers

Field	Value
Canonical name	IgG4-related mesenteritis
Mondo ID	MONDO:0016544
Orphanet	238593
ICD-11	1312565896
SNOMED CT	1092381000119100
UMLS	C0267770
MedGen	75639
GARD	0008169
Is cancer (heuristic)	no

Also known as: isolated mesenteric lipodystrophy · lipomatous mesenteritis · liposclerotic mesenteritis · mesenteric lipogranuloma · Mesenteric Panniculitis · mesenteric panniculitis · sclerosing mesenteritis

Disease family

This is a subtype of immunoglobulin G4-related sclerosing disease. Genetic, therapeutic, and trial evidence is largely curated at the broader-term level — see the parent page for the associated-gene cohort and molecular evidence.

Classification path: disease › human disease › disease by body system or component › immune system disorder › autoimmune disease › immunoglobulin G4-related sclerosing disease › IgG4-related mesenteritis

Related subtypes (13): autoimmune pancreatitis, IgG4-related sclerosing cholangitis, IgG4-related kidney disease, IgG4-related aortitis, IgG4-related pachymeningitis, IgG4-related submandibular gland disease, IgG4-related ophthalmic disorder, eosinophilic angiocentric fibrosis, primary cutaneous plasmacytosis, cutaneous pseudolymphoma, IgG4-related retroperitoneal fibrosis, IgG4-related mediastinitis, IgG4-related thyroid disease

Genetics & variants

GWAS landscape

No GWAS associations recorded — common-variant (GWAS) studies don’t cover this disease (typical for Mendelian / rare diseases). See the curated gene cohort and Mendelian overlap below.

Variant details and genetic-evidence tiers

No tiered GWAS variants or ClinVar records for this disease.

Genes & proteins

No associated-gene cohort resolved for this disease. Atlas builds the molecular and therapeutic sections — associated genes, protein families, druggability, pathways, interactions, and drug associations — by aggregating over a disease’s associated genes (resolved via GWAS / GenCC / ClinVar / CIViC), and none resolved here. This is expected for antibody-mediated, autoimmune, or otherwise non-gene-defined conditions; the curated evidence for this disease is its clinical features, GWAS susceptibility, and clinical trials (above).

Function

No pathway enrichment — requires an associated-gene cohort.

Therapeutics

No druggable-target or therapeutic data for this disease’s cohort.

Clinical trials & evidence

Clinical trials

Clinical trials: 1.

Phase distribution (across all retrieved trials)

Phase	Trials
Not specified	1

Top trials by phase / activity

NCT	Phase	Status	Title
NCT03316001	Not specified	COMPLETED	Mesenteric Panniculitis : Review of Consecutive Abdominal MDCT Examinations With a Matched-pair Analysis