Malignant cardiac peripheral nerve sheath neoplasm
disease diseaseOn this page
Also known as Cardiac malignant peripheral nerve sheath tumorCardiac malignant peripheral nerve sheath tumourCardiac MPNSTCARDIAC schwannoma, malignantheart malignant peripheral nerve sheath tumorheart malignant peripheral nerve sheath tumourheart MPNSTmalignant Cardiac neurilemmomamalignant Cardiac peripheral nerve sheath tumormalignant Cardiac peripheral nerve sheath tumourmalignant Cardiac schwannomamalignant heart neurilemmomamalignant heart peripheral nerve sheath neoplasmmalignant heart peripheral nerve sheath tumormalignant heart peripheral nerve sheath tumourmalignant heart schwannomamalignant neurilemmoma of heartmalignant neurilemmoma of the heartmalignant peripheral nerve sheath neoplasm of heart
Summary
Malignant cardiac peripheral nerve sheath neoplasm (MONDO:0001990) is a cancer. A subtype of heart sarcoma — broader associated-gene and molecular evidence is on the parent page (see Disease family below).
At a glance
- Classification: Cancer
Clinical features
No curated clinical features (Orphanet) for this disease.
Identifiers
Disease identifiers
| Field | Value |
|---|---|
| Canonical name | malignant cardiac peripheral nerve sheath neoplasm |
| Mondo ID | MONDO:0001990 |
| DOID | DOID:14534 |
| NCIT | C5367 |
| UMLS | C1334569 |
| MedGen | 233146 |
| GARD | 0023052 |
| Is cancer (heuristic) | yes |
Also known as: Cardiac malignant peripheral nerve sheath tumor · Cardiac malignant peripheral nerve sheath tumour · Cardiac MPNST · CARDIAC schwannoma, malignant · heart malignant peripheral nerve sheath tumor · heart malignant peripheral nerve sheath tumour · heart MPNST · malignant Cardiac neurilemmoma · malignant Cardiac peripheral nerve sheath neoplasm · malignant Cardiac peripheral nerve sheath tumor · malignant Cardiac peripheral nerve sheath tumour · malignant Cardiac schwannoma · malignant heart neurilemmoma · malignant heart peripheral nerve sheath neoplasm · malignant heart peripheral nerve sheath tumor · malignant heart peripheral nerve sheath tumour · malignant heart schwannoma · malignant neurilemmoma of heart · malignant neurilemmoma of the heart · malignant peripheral nerve sheath neoplasm of heart (+9 more)
Disease family
This is a subtype of heart sarcoma. Genetic, therapeutic, and trial evidence is largely curated at the broader-term level — see the parent page for the associated-gene cohort and molecular evidence.
Classification path: disease › human disease › disease by etiologic mechanism › cancer or benign tumor › neoplastic disease or syndrome › neoplasm › cancer › cardiovascular cancer › heart cancer › heart sarcoma › malignant cardiac peripheral nerve sheath neoplasm
Related subtypes (2): heart leiomyosarcoma, heart fibrosarcoma
Genetics & variants
GWAS landscape
No GWAS associations recorded — common-variant (GWAS) studies don’t cover this disease (typical for Mendelian / rare diseases). See the curated gene cohort and Mendelian overlap below.
Variant details and genetic-evidence tiers
No tiered GWAS variants or ClinVar records for this disease.
Genes & proteins
No associated-gene cohort resolved for this disease. Atlas builds the molecular and therapeutic sections — associated genes, protein families, druggability, pathways, interactions, and drug associations — by aggregating over a disease’s associated genes (resolved via GWAS / GenCC / ClinVar / CIViC), and none resolved here. This is expected for antibody-mediated, autoimmune, or otherwise non-gene-defined conditions; the curated evidence for this disease is its clinical features, GWAS susceptibility, and clinical trials (above).
Function
No pathway enrichment — requires an associated-gene cohort.
Therapeutics
No druggable-target or therapeutic data for this disease’s cohort.
Clinical trials & evidence
Clinical trials
Clinical trials: 0.
Related Atlas pages
No linked Atlas pages yet — the cross-entity mesh grows as the corpus expands.