Malignant glandular tumor of peripheral nerve sheath

Summary

Malignant glandular tumor of peripheral nerve sheath (MONDO:0004559) is a cancer. A subtype of malignant peripheral nerve sheath tumor — broader associated-gene and molecular evidence is on the parent page (see Disease family below).

At a glance

• Classification: Cancer

Clinical features

No curated clinical features (Orphanet) for this disease.

Identifiers

Disease identifiers

Field	Value
Canonical name	malignant glandular tumor of peripheral nerve sheath
Mondo ID	MONDO:0004559
DOID	DOID:8420
NCIT	C6560
SNOMED CT	699659007
UMLS	C1333821
MedGen	232558
GARD	0024069
Is cancer (heuristic)	yes

Also known as: glandular malignant peripheral nerve sheath tumor · glandular malignant peripheral nerve sheath tumour · glandular MPNST · malignant glandular neoplasm of peripheral nerve sheath · malignant glandular neoplasm of the peripheral nerve sheath · malignant glandular peripheral nerve sheath neoplasm · malignant glandular peripheral nerve sheath tumor · malignant glandular peripheral nerve sheath tumour · malignant glandular schwannoma · malignant glandular tumor of peripheral nerve sheath · malignant glandular tumor of the peripheral nerve sheath · malignant glandular tumour of the peripheral nerve sheath

Disease family

This is a subtype of malignant peripheral nerve sheath tumor. Genetic, therapeutic, and trial evidence is largely curated at the broader-term level — see the parent page for the associated-gene cohort and molecular evidence.

Classification path: human disease › disease by etiologic mechanism › cancer or benign tumor › neoplastic disease or syndrome › neoplasm › cancer › nervous system cancer › central nervous system cancer › central nervous system sarcoma › malignant peripheral nerve sheath tumor › malignant glandular tumor of peripheral nerve sheath

Related subtypes (6): malignant cardiac peripheral nerve sheath neoplasm, malignant melanocytic neoplasm of the peripheral nerve sheath, childhood malignant schwannoma, epithelioid malignant peripheral nerve sheath tumor, adult malignant schwannoma, malignant triton tumor

Genetics & variants

GWAS landscape

No GWAS associations recorded — common-variant (GWAS) studies don’t cover this disease (typical for Mendelian / rare diseases). See the curated gene cohort and Mendelian overlap below.

Variant details and genetic-evidence tiers

No tiered GWAS variants or ClinVar records for this disease.

Genes & proteins

No associated-gene cohort resolved for this disease. Atlas builds the molecular and therapeutic sections — associated genes, protein families, druggability, pathways, interactions, and drug associations — by aggregating over a disease’s associated genes (resolved via GWAS / GenCC / ClinVar / CIViC), and none resolved here. This is expected for antibody-mediated, autoimmune, or otherwise non-gene-defined conditions; the curated evidence for this disease is its clinical features, GWAS susceptibility, and clinical trials (above).

Function

No pathway enrichment — requires an associated-gene cohort.

Therapeutics

No druggable-target or therapeutic data for this disease’s cohort.

Clinical trials & evidence

Clinical trials

Clinical trials: 0.