Maternal uniparental disomy of chromosome 20

disease
On this page

Also known as maternal uniparental disomy of chromosome type 20maternal UPD(20)MBCSUPD(20)mat

Summary

Maternal uniparental disomy of chromosome 20 (MONDO:0019917) is a disease. A subtype of chromosome 20 disorder — broader associated-gene and molecular evidence is on the parent page (see Disease family below).

At a glance

  • Prevalence: <1 / 1 000 000 (Worldwide) [Orphanet-validated]
  • Phenotypes (HPO): 15

Clinical features

Epidemiology

Prevalence records

2 prevalence record(s), Orphanet:

TypeClassValueGeographyValidation
Cases/families12WorldwideValidated
Point prevalence<1 / 1 000 000WorldwideValidated

Signs & symptoms

Clinical features (HPO)

15 HPO clinical features (Orphanet curated; top 15 by frequency):

HPO IDTermFrequency
HP:0008872Feeding difficulties in infancyVery frequent (80-99%)
HP:0008897Postnatal growth retardationVery frequent (80-99%)
HP:0000325Triangular faceFrequent (30-79%)
HP:0001252HypotoniaFrequent (30-79%)
HP:0001263Global developmental delayFrequent (30-79%)
HP:0001511Intrauterine growth retardationFrequent (30-79%)
HP:0001518Small for gestational ageFrequent (30-79%)
HP:0001562OligohydramniosFrequent (30-79%)
HP:0004322Short statureFrequent (30-79%)
HP:0004325Decreased body weightFrequent (30-79%)
HP:0011220Prominent foreheadFrequent (30-79%)
HP:0030084ClinodactylyFrequent (30-79%)
HP:0034323Reduced circulating growth hormone concentrationFrequent (30-79%)
HP:0000347MicrognathiaOccasional (5-29%)
HP:0100555Asymmetric growthOccasional (5-29%)

Identifiers

Disease identifiers

FieldValue
Canonical namematernal uniparental disomy of chromosome 20
Mondo IDMONDO:0019917
OMIM617352
Orphanet96186
DOIDDOID:0111714
ICD-11700797720
SNOMED CT715735007
UMLSC4275029
MedGen909388
GARD0016849
Is cancer (heuristic)no

Also known as: maternal uniparental disomy of chromosome type 20 · maternal UPD(20) · MBCS · UPD(20)mat

Disease family

Classification path: disease › human disease › disease by etiologic mechanism › disease of genetic or genomic mechanism › chromosomal disorder › autosomal anomaly › chromosome 20 disorder › maternal uniparental disomy of chromosome 20

Related subtypes (5): ring chromosome 20, partial deletion of chromosome 20, partial trisomy of chromosome 20, paternal uniparental disomy of chromosome 20, chromosome 20 trisomy

Genetics & variants

GWAS landscape

No GWAS associations recorded — common-variant (GWAS) studies don’t cover this disease (typical for Mendelian / rare diseases). See the curated gene cohort and Mendelian overlap below.

Variant details and genetic-evidence tiers

No tiered GWAS variants or ClinVar records for this disease.

Genes & proteins

No associated-gene cohort resolved for this disease. Atlas builds the molecular and therapeutic sections — associated genes, protein families, druggability, pathways, interactions, and drug associations — by aggregating over a disease’s associated genes (resolved via GWAS / GenCC / ClinVar / CIViC), and none resolved here. This is expected for antibody-mediated, autoimmune, or otherwise non-gene-defined conditions; the curated evidence for this disease is its clinical features, GWAS susceptibility, and clinical trials (above).

Function

No pathway enrichment — requires an associated-gene cohort.

Therapeutics

No druggable-target or therapeutic data for this disease’s cohort.

Clinical trials & evidence

Clinical trials

Clinical trials: 0.

No linked Atlas pages yet — the cross-entity mesh grows as the corpus expands.