Necrotizing vasculitis

disease
On this page

Also known as systemic vasculitis

Summary

Necrotizing vasculitis (MONDO:0800113) is a disease and 17 clinical trials. Top therapeutic interventions include rituximab and varicella zoster virus envelope glycoprotein e. A subtype of vasculitis — broader associated-gene and molecular evidence is on the parent page (see Disease family below).

At a glance

  • Clinical trials: 17

Clinical features

No curated clinical features (Orphanet) for this disease.

Identifiers

Disease identifiers

FieldValue
Canonical namenecrotizing vasculitis
Mondo IDMONDO:0800113
NCITC70635
UMLSC1318520
MedGen230813
GARD0005106
Is cancer (heuristic)no

Also known as: systemic vasculitis

Disease family

This is a subtype of vasculitis. Genetic, therapeutic, and trial evidence is largely curated at the broader-term level — see the parent page for the associated-gene cohort and molecular evidence.

Classification path: disease › human disease › disease by body system or component › cardiovascular disordervascular disordervasculitisnecrotizing vasculitis

Related subtypes (17): choroiditis, Shwartzman phenomenon, central nervous system vasculitis, phlebitis, lymphangitis, aortitis, hypersensitivity vasculitis, retinal vasculitis, vasculitis, lymphocytic, nodular, Kawasaki disease, deficiency of adenosine deaminase 2, immune complex mediated vasculitis, secondary vasculitis, cutaneous vasculitis, livedoid vasculopathy, autoimmune vasculitis, arteritis

Subtypes (3): anti-neutrophil cytoplasmic antibody-associated vasculitis, immunoglobulin A vasculitis, disseminated visceral giant cell angiitis

Genetics & variants

GWAS landscape

No GWAS associations recorded — common-variant (GWAS) studies don’t cover this disease (typical for Mendelian / rare diseases). See the curated gene cohort and Mendelian overlap below.

Variant details and genetic-evidence tiers

No tiered GWAS variants or ClinVar records for this disease.

Genes & proteins

No associated-gene cohort resolved for this disease. Atlas builds the molecular and therapeutic sections — associated genes, protein families, druggability, pathways, interactions, and drug associations — by aggregating over a disease’s associated genes (resolved via GWAS / GenCC / ClinVar / CIViC), and none resolved here. This is expected for antibody-mediated, autoimmune, or otherwise non-gene-defined conditions; the curated evidence for this disease is its clinical features, GWAS susceptibility, and clinical trials (above).

Function

No pathway enrichment — requires an associated-gene cohort.

Therapeutics

No druggable-target or therapeutic data for this disease’s cohort.

Clinical trials & evidence

Clinical trials

Clinical trials: 17.

Phase distribution (across all retrieved trials)

PhaseTrials
Not specified10
PHASE43
PHASE22
PHASE31
PHASE2/PHASE31

Top trials by phase / activity

NCTPhaseStatusTitle
NCT06763783PHASE4ENROLLING_BY_INVITATIONVaccination Against Herpes Zoster in Patients With Inflammatory Rheumatic Diseases
NCT01151644PHASE4UNKNOWNSafety and Efficacy of Anti-Pandemic H1N1 Vaccination in Rheumatic Diseases
NCT03762824PHASE4COMPLETEDCombined Pneumococcal Conjugate and Polysaccharide Vaccination in Inflammatory Rheumatic Disease
NCT01257802PHASE3TERMINATEDGnRH-a for Ovarian Protection During CYC Therapy for Rheumatic Diseases
NCT05236491PHASE2/PHASE3UNKNOWNCOvid-19 Vaccine Booster in Immunocompromised Rheumatic Diseases
NCT02556866PHASE2TERMINATEDRituximab Plus Corticosteroids in Non-infectious Active Mixed Cryoglobulinemia Vasculitis
NCT03514979PHASE2UNKNOWNAcquired Immunodeficiency in ANCA Associated Vasculitis
NCT02593565Not specifiedRECRUITINGVasculitis Pregnancy Registry
NCT06642870Not specifiedRECRUITINGRare AutoImmune SElf-management Programme Development
NCT07037732Not specifiedRECRUITINGCirculating B-cell, Drug and Anti-drug Antibodies Monitoring in Patients Treated With Rituximab for Autoimmune Disorders
NCT01314547Not specifiedCOMPLETEDImpact of Environmental Factors on Disease Activity in Spondyloarthritis (SPA): Results of the Prospective Co-Env Cohort
NCT01599260Not specifiedTERMINATEDResistance Exercise in Rheumatic Disease
NCT02042092Not specifiedCOMPLETEDMagnetic Resonance Angiography vs Ultrasonography in Systemic Large vEssel vasculitiS
NCT02476292Not specifiedCOMPLETEDImpact of Vasculitis on Employment and Income
NCT03410290Not specifiedCOMPLETEDJourney of Patients With Vasculitis From First Symptom to Diagnosis
NCT03543527Not specifiedUNKNOWNStudy of Refractory and/or Relapsing TAkayasu aRTeritis
NCT05164822Not specifiedTERMINATEDEvolution of Neuropathies Associated With Necrotizing Vasculitis

Drugs tested across these trials (top 30)

MoleculeMax phaseTrials referencing
RITUXIMAB41
VARICELLA ZOSTER VIRUS ENVELOPE GLYCOPROTEIN E41