Non-autoimmune hemolytic anemia

disease
On this page

Also known as Non-Autoimmune Hemolytic Anaemia

Summary

Non-autoimmune hemolytic anemia (MONDO:0021559) is a disease with 30 GWAS associations across 13 studies. A subtype of hemolytic anemia — broader associated-gene and molecular evidence is on the parent page (see Disease family below).

At a glance

  • GWAS associations: 30

Clinical features

No curated clinical features (Orphanet) for this disease.

Identifiers

Disease identifiers

FieldValue
Canonical namenon-autoimmune hemolytic anemia
Mondo IDMONDO:0021559
EFOEFO:0005558
NCITC34853
SNOMED CT191216004
UMLSC0028283
MedGen45122
GARD0025337
Is cancer (heuristic)no

Also known as: Non-Autoimmune Hemolytic Anaemia · Non-autoimmune hemolytic anaemia · non-autoimmune hemolytic anemia

Data availability: 30 GWAS associations (13 studies).

Disease family

This is a subtype of hemolytic anemia. Genetic, therapeutic, and trial evidence is largely curated at the broader-term level — see the parent page for the associated-gene cohort and molecular evidence.

Classification path: disease › human disease › disease by body system or component › hematologic disorderanemianormocytic anemiahemolytic anemianon-autoimmune hemolytic anemia

Related subtypes (10): familial hemolytic anemia, Heinz body anemia, lethal hemolytic anemia-genital anomalies syndrome, hemolytic disease of the newborn with Kell alloimmunization, hereditary elliptocytosis, Shiga toxin-associated hemolytic uremic syndrome, hereditary stomatocytosis, autoimmune hemolytic anemia, 6-phosphogluconate dehydrogenase deficiency, paroxysmal nocturnal hemoglobinuria

Genetics & variants

GWAS landscape

30 GWAS associations across 13 studies. Top hits map to 8 distinct genes (as reported by GWAS).

Top associations by p-value

rsIDp-valueGeneRisk alleleOdds ratio
chr11:52270023e-174A2.36
chr11:52256784e-31?3.29
chr16:1835271e-17A4.61
rs5407773455e-15SHH - Y_RNAA3.29
rs1391859142e-14WDR12G3.85
rs5324235451e-12DTWD2 - DMXL1-DTC3.96
rs5470422924e-12RPS3AP2 - PTX4C3.46
rs1390697155e-12ZBTB43A2.56
rs1927834179e-12EQTN - MOB3BG1.95
rs5286140569e-12IFTAP - RPL7AP56C4.02
rs1815125411e-11CNTLNC3.23
rs5765319901e-11SBF2-AS1, SBF2G3.27
rs5554600191e-11ADGRA2G1.89
rs1921245712e-11RNA5SP94 - MIR4432HGC3.35
rs1133729353e-11CD300A - CD300LBG3.63
rs761985783e-11NCR2 - FOXP4-AS1C2.09
rs1138129184e-11PRKCZC3.65
rs1806929294e-11COMMD8 - ATP10DG3.42
rs5540974624e-11LINC01448 - TCP1P1C2.91
rs75458499e-10CYP2J2?
chrX:1218565942e-09C3.34
chr16:57743291e-08G4.02
chr17:32296412e-08A4.13
chrX:842198322e-08G2.95
chr22:270555053e-08T4.5
chr8:770758513e-08T3.65
chr11:1125601113e-08A4.57
chr16:36220903e-08T4.51
chr13:623793395e-08A4.56
chr11:5226943inf?3.46

Top studies (by case count)

StudyLead authorYearCasesControlsTitle
GCST90473121UK Biobank Whole-Genome Sequencing Consortium2025847457,593Whole-genome sequencing of 490,640 UK Biobank participants.
GCST90667918UK Biobank Whole-Genome Sequencing Consortium2025847457,593Whole-genome sequencing of 490,640 UK Biobank participants.
GCST90473120UK Biobank Whole-Genome Sequencing Consortium20257228,493Whole-genome sequencing of 490,640 UK Biobank participants.
GCST90477453Verma A2024687449,900Diversity and scale: Genetic architecture of 2068 traits in the VA Million Veteran Program.
GCST90726705Kim HI202651643,510Exome sequencing and analysis of 44,028 British South Asians enriched for high autozygosity.
GCST90473127UK Biobank Whole-Genome Sequencing Consortium2025366458,074Whole-genome sequencing of 490,640 UK Biobank participants.
GCST90479967Verma A2024273121,331Diversity and scale: Genetic architecture of 2068 traits in the VA Million Veteran Program.
GCST90481654Verma A2024273121,331Diversity and scale: Genetic architecture of 2068 traits in the VA Million Veteran Program.
GCST90727234Kim HI202625143,775Exome sequencing and analysis of 44,028 British South Asians enriched for high autozygosity.
GCST90473122UK Biobank Whole-Genome Sequencing Consortium20252449,369Whole-genome sequencing of 490,640 UK Biobank participants.

Variant details and genetic-evidence tiers

Tier distribution (top 50 variants)

TierVariants
Tier 1: coding0
Tier 2: splice/UTR1
Tier 3: regulatory0
Tier 4: intronic/intergenic29

MAF distribution

BucketVariants
common (>=0.05)1
low_freq (0.01-0.05)0
rare (<0.01)16
unknown13

Functional consequences

ConsequenceCount
unknown13
intron_variant9
intergenic_variant6
synonymous_variant1
splice_polypyrimidine_tract_variant1

Top variants

rsIDChrPosAllelesMAFConsequenceGenep-valueTier
chr11:5226943Tier 4: intronic/intergenic
chr11:52270023e-174Tier 4: intronic/intergenic
chr11:52256784e-31Tier 4: intronic/intergenic
chr16:1835271e-17Tier 4: intronic/intergenic
rs5407773457156014699A>G0intron_variantSHH - Y_RNA5e-15Tier 4: intronic/intergenic
rs1391859142202902422G>A,C0intron_variantWDR122e-14Tier 4: intronic/intergenic
rs5324235455119001506C>T0.001intergenic_variantDTWD2 - DMXL1-DT1e-12Tier 4: intronic/intergenic
rs547042292161483584C>A,G,T0intergenic_variantRPS3AP2 - PTX44e-12Tier 4: intronic/intergenic
rs1390697159126818988A>T0.003intron_variantZBTB435e-12Tier 4: intronic/intergenic
rs192783417927298121G>A0.005intron_variantEQTN - MOB3B9e-12Tier 4: intronic/intergenic
rs5286140561137436741C>G0intergenic_variantIFTAP - RPL7AP569e-12Tier 4: intronic/intergenic
rs181512541917135713C>A,T0.001intron_variantCNTLN1e-11Tier 4: intronic/intergenic
rs576531990119800978G>C0intron_variantSBF2-AS1, SBF21e-11Tier 4: intronic/intergenic
rs555460019837824181G>A0.002intron_variantADGRA21e-11Tier 4: intronic/intergenic
rs192124571259826128C>G,T0.001intron_variantRNA5SP94 - MIR4432HG2e-11Tier 4: intronic/intergenic
rs1133729351774493857G>A0intergenic_variantCD300A - CD300LB3e-11Tier 4: intronic/intergenic
rs76198578641414845C>T0.001intergenic_variantNCR2 - FOXP4-AS13e-11Tier 4: intronic/intergenic
rs11381291812173976C>A,G,T0.001synonymous_variantPRKCZ4e-11Tier 4: intronic/intergenic
rs180692929447467501G>A0splice_polypyrimidine_tract_variantCOMMD8 - ATP10D4e-11Tier 2: splice/UTR
rs554097462742765625C>G,T0intergenic_variantLINC01448 - TCP1P14e-11Tier 4: intronic/intergenic
rs7545849159910442G>A0.05intron_variantCYP2J29e-10Tier 4: intronic/intergenic
chrX:1218565942e-09Tier 4: intronic/intergenic
chr16:57743291e-08Tier 4: intronic/intergenic
chr17:32296412e-08Tier 4: intronic/intergenic
chrX:842198322e-08Tier 4: intronic/intergenic
chr22:270555053e-08Tier 4: intronic/intergenic
chr8:770758513e-08Tier 4: intronic/intergenic
chr11:1125601113e-08Tier 4: intronic/intergenic
chr16:36220903e-08Tier 4: intronic/intergenic
chr13:623793395e-08Tier 4: intronic/intergenic

Genes & proteins

No associated-gene cohort resolved for this disease. Atlas builds the molecular and therapeutic sections — associated genes, protein families, druggability, pathways, interactions, and drug associations — by aggregating over a disease’s associated genes (resolved via GWAS / GenCC / ClinVar / CIViC), and none resolved here. This is expected for antibody-mediated, autoimmune, or otherwise non-gene-defined conditions; the curated evidence for this disease is its clinical features, GWAS susceptibility, and clinical trials (above).

Function

No pathway enrichment — requires an associated-gene cohort.

Therapeutics

Drugs indicated for this disease

4 approved. Disease-direct ChEMBL indications, not inferred from the associated-gene cohort below.

DrugDevelopment status
Cortisone AcetateApproved (phase 4)
DexamethasoneApproved (phase 4)
PrednisoloneApproved (phase 4)
PrednisoneApproved (phase 4)

Clinical trials & evidence

Clinical trials

Clinical trials: 0.

No linked Atlas pages yet — the cross-entity mesh grows as the corpus expands.