Non-functioning pituitary adenoma

disease
On this page

Also known as functionless adenoma of pituitaryfunctionless adenoma of pituitary glandfunctionless adenoma of the pituitaryfunctionless adenoma of the pituitary glandfunctionless pituitary adenomafunctionless pituitary gland adenomaNFPAnon-functioning adenoma of pituitarynon-functioning adenoma of pituitary glandnon-functioning adenoma of the pituitarynon-functioning adenoma of the pituitary glandnon-functioning pituitary gland adenomanon-secretory adenoma of pituitarynon-secretory adenoma of pituitary glandnon-secretory adenoma of the pituitarynon-secretory adenoma of the pituitary glandnon-secretory pituitary adenomanon-secretory pituitary gland adenomanonfunctional pituitary gland adenoma

Summary

Non-functioning pituitary adenoma (MONDO:0019613) is a cancer and 5 clinical trials. Top therapeutic interventions include cabergoline, pasireotide, and sodium chloride. A subtype of non-functioning pituitary gland neoplasm — broader associated-gene and molecular evidence is on the parent page (see Disease family below).

At a glance

  • Classification: Cancer
  • Prevalence: 1-5 / 10 000 (Europe) [Orphanet-validated]
  • Phenotypes (HPO): 58
  • Clinical trials: 5

Clinical features

Epidemiology

Prevalence records

9 prevalence record(s), Orphanet:

TypeClassValueGeographyValidation
Annual incidence1-9 / 100 0001.05WorldwideValidated
Point prevalence1-5 / 10 000EuropeValidated
Annual incidence1-9 / 100 0004FinlandValidated
Annual incidence1-9 / 100 0001.1SwedenValidated
Point prevalence6-9 / 10 00094BelgiumValidated
Point prevalence6-9 / 10 00080.5SwitzerlandValidated
Point prevalence6-9 / 10 00077.6United KingdomValidated
Point prevalence6-9 / 10 00068FinlandValidated
Annual incidence1-9 / 100 0002.55EuropeNot yet validated

Signs & symptoms

Clinical features (HPO)

58 HPO clinical features (Orphanet curated; top 50 by frequency):

HPO IDTermFrequency
HP:0002893Pituitary adenomaVery frequent (80-99%)
HP:0000026Male hypogonadismFrequent (30-79%)
HP:0000044Hypogonadotropic hypogonadismFrequent (30-79%)
HP:0000134Female hypogonadismFrequent (30-79%)
HP:0000135HypogonadismFrequent (30-79%)
HP:0000140Abnormality of the menstrual cycleFrequent (30-79%)
HP:0000529Progressive visual lossFrequent (30-79%)
HP:0000802ImpotenceFrequent (30-79%)
HP:0000824Decreased response to growth hormone stimulation testFrequent (30-79%)
HP:0000830Anterior hypopituitarismFrequent (30-79%)
HP:0000837Increased circulating gonadotropin levelFrequent (30-79%)
HP:0000846Adrenal insufficiencyFrequent (30-79%)
HP:0000858Irregular menstruationFrequent (30-79%)
HP:0000868Decreased fertility in femalesFrequent (30-79%)
HP:0000980PallorFrequent (30-79%)
HP:0002013VomitingFrequent (30-79%)
HP:0002017Nausea and vomitingFrequent (30-79%)
HP:0002315HeadacheFrequent (30-79%)
HP:0002615HypotensionFrequent (30-79%)
HP:0002920Decreased circulating ACTH levelFrequent (30-79%)
HP:0003388Easy fatigabilityFrequent (30-79%)
HP:0008240Secondary growth hormone deficiencyFrequent (30-79%)
HP:0008245Pituitary hypothyroidismFrequent (30-79%)
HP:0008993Increased intraabdominal fatFrequent (30-79%)
HP:0010972Anemia of inadequate productionFrequent (30-79%)
HP:0011362Abnormal hair quantityFrequent (30-79%)
HP:0011734Central adrenal insufficiencyFrequent (30-79%)
HP:0011735Adrenocorticotropin deficient adrenal insufficiencyFrequent (30-79%)
HP:0011748Adrenocorticotropic hormone deficiencyFrequent (30-79%)
HP:0011804Abnormal muscle physiologyFrequent (30-79%)
HP:0012041Decreased fertility in malesFrequent (30-79%)
HP:0012378FatigueFrequent (30-79%)
HP:0012503Abnormality of the pituitary glandFrequent (30-79%)
HP:0030018Decreased female libidoFrequent (30-79%)
HP:0030521Bitemporal hemianopiaFrequent (30-79%)
HP:0040075HypopituitarismFrequent (30-79%)
HP:0100639Erectile dysfunctionFrequent (30-79%)
HP:0000508PtosisOccasional (5-29%)
HP:0000618BlindnessOccasional (5-29%)
HP:0000651DiplopiaOccasional (5-29%)
HP:0000863Central diabetes insipidusOccasional (5-29%)
HP:0000870Increased circulating prolactin concentrationOccasional (5-29%)
HP:0000871PanhypopituitarismOccasional (5-29%)
HP:0000873Diabetes insipidusOccasional (5-29%)
HP:0001117Sudden loss of visual acuityOccasional (5-29%)
HP:0001250SeizureOccasional (5-29%)
HP:0002050Macroorchidism, postpubertalOccasional (5-29%)
HP:0002321VertigoOccasional (5-29%)
HP:0006824Cranial nerve paralysisOccasional (5-29%)
HP:0006897Abducens palsyOccasional (5-29%)

Identifiers

Disease identifiers

FieldValue
Canonical namenon-functioning pituitary adenoma
Mondo IDMONDO:0019613
EFOEFO:0008516
Orphanet91349
DOIDDOID:5715
ICD-111197752358
NCITC4348
SNOMED CT254962005
GARD0019159
Anatomy (UBERON)UBERON:0000007
Is cancer (heuristic)yes

Also known as: functionless adenoma of pituitary · functionless adenoma of pituitary gland · functionless adenoma of the pituitary · functionless adenoma of the pituitary gland · functionless pituitary adenoma · functionless pituitary gland adenoma · NFPA · non-functioning adenoma of pituitary · non-functioning adenoma of pituitary gland · non-functioning adenoma of the pituitary · non-functioning adenoma of the pituitary gland · non-functioning pituitary adenoma · non-functioning pituitary gland adenoma · non-secretory adenoma of pituitary · non-secretory adenoma of pituitary gland · non-secretory adenoma of the pituitary · non-secretory adenoma of the pituitary gland · non-secretory pituitary adenoma · non-secretory pituitary gland adenoma · nonfunctional pituitary gland adenoma (+1 more)

Data availability: 1 cell line.

Disease family

This is a subtype of non-functioning pituitary gland neoplasm. Genetic, therapeutic, and trial evidence is largely curated at the broader-term level — see the parent page for the associated-gene cohort and molecular evidence.

Classification path: disease › human disease › disease by etiologic mechanism › cancer or benign tumorneoplastic disease or syndromeneoplasmendocrine gland neoplasmpituitary tumornon-functioning pituitary gland neoplasmnon-functioning pituitary adenoma

Subtypes (2): silent pituitary adenoma, null pituitary adenoma

Genetics & variants

GWAS landscape

No GWAS associations recorded — common-variant (GWAS) studies don’t cover this disease (typical for Mendelian / rare diseases). See the curated gene cohort and Mendelian overlap below.

Variant details and genetic-evidence tiers

No tiered GWAS variants or ClinVar records for this disease.

Genes & proteins

No associated-gene cohort resolved for this disease. Atlas builds the molecular and therapeutic sections — associated genes, protein families, druggability, pathways, interactions, and drug associations — by aggregating over a disease’s associated genes (resolved via GWAS / GenCC / ClinVar / CIViC), and none resolved here. This is expected for antibody-mediated, autoimmune, or otherwise non-gene-defined conditions; the curated evidence for this disease is its clinical features, GWAS susceptibility, and clinical trials (above).

Function

No pathway enrichment — requires an associated-gene cohort.

Therapeutics

No druggable-target or therapeutic data for this disease’s cohort.

Clinical trials & evidence

Clinical trials

Clinical trials: 5.

Phase distribution (across all retrieved trials)

PhaseTrials
PHASE22
Not specified2
PHASE2/PHASE31

Top trials by phase / activity

NCTPhaseStatusTitle
NCT01620138PHASE2/PHASE3COMPLETEDResponse to Cabergoline and Pasireotide in Non-functioning Pituitary Adenomas and Resistant Prolactinomas
NCT01283542PHASE2COMPLETEDEvaluate the Efficacy and Safety of Pasireotide LAR (Long Acting Release) on the Treatment of Patients With Clinically Non-Functioning Pituitary Adenoma.
NCT05005715PHASE2UNKNOWNEffect of Dexmedetomidine on Quality of Recovery in Non-functioning Pituitary Adenoma Patients Undergoing Endoscopic Transsphenoidal Surgery
NCT06163261Not specifiedRECRUITINGIndividualized Physical Activity or Patients With Non Functioning Pituitary Adenoma
NCT04218721Not specifiedCOMPLETEDImplementing eHealth Interventions Into Regular Clinical Practice

Drugs tested across these trials (top 30)

MoleculeMax phaseTrials referencing
CABERGOLINE41
PASIREOTIDE41
SODIUM CHLORIDE41
CHEMBL459310501
CHEMBL519247001