Occlusion precerebral artery

disease
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Summary

Occlusion precerebral artery (MONDO:0003718) is a disease with 35 GWAS associations across 17 studies. A subtype of cerebrovascular disorder — broader associated-gene and molecular evidence is on the parent page (see Disease family below).

At a glance

  • GWAS associations: 35

Clinical features

No curated clinical features (Orphanet) for this disease.

Identifiers

Disease identifiers

FieldValue
Canonical nameocclusion precerebral artery
Mondo IDMONDO:0003718
EFOEFO:0009677
DOIDDOID:5976
SNOMED CT28790007
UMLSC0265090
MedGen539069
Is cancer (heuristic)no

Data availability: 35 GWAS associations (17 studies).

Disease family

This is a subtype of cerebrovascular disorder. Genetic, therapeutic, and trial evidence is largely curated at the broader-term level — see the parent page for the associated-gene cohort and molecular evidence.

Classification path: disease › human disease › disease by body system or component › nervous system disordercentral nervous system disorderbrain disordercerebrovascular disorderocclusion precerebral artery

Related subtypes (23): cerebral arteritis, intracranial thrombosis, vascular dementia, stroke disorder, internal carotid artery stenosis, carotid artery disorder, brain ischemia, brain infarction, cerebral amyloid angiopathy, vascular brain injury, basal ganglia cerebrovascular disorder, intracranial arterial disease, intracranial vasospasm, subclavian steal syndrome, pseudotumor cerebri, cerebral sinovenous thrombosis, HTRA1-related autosomal dominant cerebral small vessel disease, familial porencephaly, microangiopathy and leukoencephalopathy, pontine, autosomal dominant, cathepsin a-related arteriopathy-strokes-leukoencephalopathy, precerebral artery stenosis, cerebral artery stenosis, APP-related brain and vascular amyloidosis

Subtypes (3): vertebral artery occlusion, basilar artery occlusion, carotid artery occlusion

Genetics & variants

GWAS landscape

35 GWAS associations across 17 studies. Top hits map to 12 distinct genes (as reported by GWAS).

Top associations by p-value

rsIDp-valueGeneRisk alleleOdds ratio
chr7:190527339e-69G0.22
rs21075952e-57HDAC9 - TWIST1G0.19
rs104558724e-56LPAA0.26
rs15373734e-51CDKN2B-AS1T0.13
rs132257231e-34LINC02577G0.13
chr16:754032897e-32C0.11
rs591557203e-28TMEM170AA0.1
chr11:1027186954e-25T0.12
chr4:1484008192e-24C0.13
rs75004481e-23CDH13A0.11
rs6467761e-22CELSR2 - PSRC1C0.1
rs127403741e-21CELSR2G0.11
rs5277259e-19IPO9-AS1, NAV1A0.08
rs18929719e-19RNU7-159P - MMP13G0.1
rs738558142e-18PRMT5P1 - EDNRAG0.11
rs116700564e-18ELLC0.13
chr18:200036256e-18C0.08
chr17:121873392e-13T0.08
rs5276092743e-13VITG2.78
chr19:111916776e-13T0.1
rs48004021e-12ATP7BP1 - RPS4XP18A0.07
rs1382941132e-12SMARCA4 - LDLRC0.1
chr16:730900394e-12G0.07
rs38270667e-12ZNF335C0.08
chr5:1082001142e-11C0.11
chr7:190319352e-11C0.31
rs74122e-11APOEC0.12
rs10658533e-11APOE - APOC1G0.11
rs780124381e-06SLC22A5 - CARINH?

Top studies (by case count)

StudyLead authorYearCasesControlsTitle
GCST90475986Verma A202426,524402,475Diversity and scale: Genetic architecture of 2068 traits in the VA Million Veteran Program.
GCST90652231Liu TY20254,055215,981Diversity and longitudinal records: Genetic architecture of disease associations and polygenic risk in the Taiwanese Han population.
GCST90477984Verma A20243,388113,694Diversity and scale: Genetic architecture of 2068 traits in the VA Million Veteran Program.
GCST90480193Verma A20243,388113,694Diversity and scale: Genetic architecture of 2068 traits in the VA Million Veteran Program.
GCST90475987Verma A20242,276446,000Diversity and scale: Genetic architecture of 2068 traits in the VA Million Veteran Program.
GCST90043999Jiang L20211,830454,518A generalized linear mixed model association tool for biobank-scale data.
GCST90477983Verma A20241,61456,314Diversity and scale: Genetic architecture of 2068 traits in the VA Million Veteran Program.
GCST90080038Backman JD20211,329386,456Exome sequencing and analysis of 454,787 UK Biobank participants.
GCST90084024Backman JD20211,329386,456Exome sequencing and analysis of 454,787 UK Biobank participants.
GCST90436139Zhou W20181,185399,017Efficiently controlling for case-control imbalance and sample relatedness in large-scale genetic association studies.

Variant details and genetic-evidence tiers

Tier distribution (top 50 variants)

TierVariants
Tier 1: coding1
Tier 2: splice/UTR1
Tier 3: regulatory3
Tier 4: intronic/intergenic24

MAF distribution

BucketVariants
common (>=0.05)27
low_freq (0.01-0.05)0
rare (<0.01)1
unknown1

Functional consequences

ConsequenceCount
unknown10
intron_variant9
intergenic_variant4
regulatory_region_variant3
3_prime_UTR_variant1
missense_variant1
non_coding_transcript_exon_variant1

Top variants

rsIDChrPosAllelesMAFConsequenceGenep-valueTier
chr7:190527330.169e-69Tier 4: intronic/intergenic
rs2107595719009765G>A,C,T0.18regulatory_region_variantHDAC9 - TWIST12e-57Tier 3: regulatory
rs104558726160589086A>G0.069intron_variantLPA4e-56Tier 4: intronic/intergenic
rs1537373922103342T>A,G0.499intron_variantCDKN2B-AS14e-51Tier 4: intronic/intergenic
rs132257237106776021G>A,C0.204intron_variantLINC025771e-34Tier 4: intronic/intergenic
chr16:754032890.4267e-32Tier 4: intronic/intergenic
rs591557201675449908A>C,G,T0.455intron_variantTMEM170A3e-28Tier 4: intronic/intergenic
chr11:1027186950.1834e-25Tier 4: intronic/intergenic
chr4:1484008190.1422e-24Tier 4: intronic/intergenic
rs75004481683012185A>G0.248intron_variantCDH131e-23Tier 4: intronic/intergenic
rs6467761109275908C>A,G,T0.22regulatory_region_variantCELSR2 - PSRC11e-22Tier 3: regulatory
rs127403741109274968G>T0.2253_prime_UTR_variantCELSR21e-21Tier 2: splice/UTR
rs5277251201783301A>C,T0.391intron_variantIPO9-AS1, NAV19e-19Tier 4: intronic/intergenic
rs189297111102924877G>A0.189regulatory_region_variantRNU7-159P - MMP139e-19Tier 3: regulatory
rs738558144147476599G>T0.147intergenic_variantPRMT5P1 - EDNRA2e-18Tier 4: intronic/intergenic
rs116700561918479133C>G,T0.083intron_variantELL4e-18Tier 4: intronic/intergenic
chr18:200036250.4186e-18Tier 4: intronic/intergenic
chr17:121873390.2432e-13Tier 4: intronic/intergenic
rs527609274236771243G>A0intron_variantVIT3e-13Tier 4: intronic/intergenic
chr19:111916770.1216e-13Tier 4: intronic/intergenic
rs48004021822423703A>G,T0.429intergenic_variantATP7BP1 - RPS4XP181e-12Tier 4: intronic/intergenic
rs1382941131911081053C>T0.12intergenic_variantSMARCA4 - LDLR2e-12Tier 4: intronic/intergenic
chr16:730900390.3014e-12Tier 4: intronic/intergenic
rs38270662045957384C>T0.155intron_variantZNF3357e-12Tier 4: intronic/intergenic
chr5:1082001140.0822e-11Tier 4: intronic/intergenic
chr7:190319350.0982e-11Tier 4: intronic/intergenic
rs74121944908822C>T0.082missense_variantAPOE2e-11Tier 1: coding
rs10658531944909976G>A,C,T0.081non_coding_transcript_exon_variantAPOE - APOC13e-11Tier 4: intronic/intergenic
rs780124385132396287G>Aintergenic_variantSLC22A5 - CARINH1e-06Tier 4: intronic/intergenic

Genes & proteins

No associated-gene cohort resolved for this disease. Atlas builds the molecular and therapeutic sections — associated genes, protein families, druggability, pathways, interactions, and drug associations — by aggregating over a disease’s associated genes (resolved via GWAS / GenCC / ClinVar / CIViC), and none resolved here. This is expected for antibody-mediated, autoimmune, or otherwise non-gene-defined conditions; the curated evidence for this disease is its clinical features, GWAS susceptibility, and clinical trials (above).

Function

No pathway enrichment — requires an associated-gene cohort.

Therapeutics

No druggable-target or therapeutic data for this disease’s cohort.

Clinical trials & evidence

Clinical trials

Clinical trials: 0.

No linked Atlas pages yet — the cross-entity mesh grows as the corpus expands.