Pancreas disorder

disease
On this page

Also known as disease of pancreasdisease or disorder of pancreasdisease, pancreaticdiseases, pancreaticdisorder of pancreaspancreas diseasepancreas disease or disorderpancreatic diseasepancreatic disorder

Summary

Pancreas disorder (MONDO:0002356) is a disease (an umbrella term covering 14 Mondo subtypes) with 13 GWAS associations across 25 studies and 137 clinical trials. Top therapeutic interventions include alfentanil, cefoxitin, and dextrose. A subtype of digestive system disorder — broader associated-gene and molecular evidence is on the parent page (see Disease family below).

At a glance

  • Umbrella term: 14 Mondo subtypes
  • GWAS associations: 13
  • Clinical trials: 137

Clinical features

No curated clinical features (Orphanet) for this disease.

Identifiers

Disease identifiers

FieldValue
Canonical namepancreas disorder
Mondo IDMONDO:0002356
EFOEFO:0009605
MeSHD010182
DOIDDOID:26
ICD-10-CMK86.9
ICD-111726554290
NCITC26842
SNOMED CT3855007
UMLSC0030286
MedGen14583
Anatomy (UBERON)UBERON:0001264
Is cancer (heuristic)no

Also known as: disease of pancreas · disease or disorder of pancreas · disease, pancreatic · diseases, pancreatic · disorder of pancreas · pancreas disease · pancreas disease or disorder · pancreatic disease · pancreatic disorder

Data availability: 13 GWAS associations (25 studies).

Disease family

This is a subtype of digestive system disorder. Genetic, therapeutic, and trial evidence is largely curated at the broader-term level — see the parent page for the associated-gene cohort and molecular evidence.

Classification path: disease › human disease › disease by body system or component › digestive system disorderpancreas disorder

Related subtypes (30): benign digestive system neoplasm, autoimmune disorder of gastrointestinal tract, gastrointestinal mucositis, diarrheal disease, hepatobiliary disorder, digestive system cancer, peptic ulcer disease, stomach disorder, intestinal disorder, Meckel diverticulum, Cronkhite-Canada syndrome, diverticulosis, small-intestinal, diverticulosis of bowel, hernia, and retinal detachment, congenital enteropathy due to enteropeptidase deficiency, hereditary mixed polyposis syndrome, caudal duplication, Moyamoya disease with early-onset achalasia, hyperplastic polyposis syndrome, thoraco-abdominal enteric duplication, digestive duplication, juvenile polyposis syndrome, umbilical cord ulceration-intestinal atresia syndrome, growth retardation-mild developmental delay-chronic hepatitis syndrome, common mesentery, neoplasm of oropharynx, gastrointestinal polyp, digestive system neuroendocrine neoplasm, digestive system infectious disorder, upper digestive tract disorder, congenital peritoneal encapsulation

Subtypes (14): pancreatic steatorrhea, pancreatic mucinous ductal ectasia, exocrine pancreatic insufficiency, endocrine pancreas disorder, pancreatitis, annular pancreas, pancreatic triacylglycerol lipase deficiency, follicular cholangitis and pancreatitis, congenital pancreatic cyst, recurrent acute pancreatitis, accessory pancreas, pancreatic neoplasm, acinar cystic transformation of the pancreas, lymphoepithelial cyst of the pancreas

Genetics & variants

GWAS landscape

13 GWAS associations across 25 studies. Top hits map to 3 distinct genes (as reported by GWAS).

Top associations by p-value

rsIDp-valueGeneRisk alleleOdds ratio
chr6:326597039e-39A0.29
rs1139939603e-32CFTR?3
rs6795743e-15FUT2C0.09
rs1489117342e-12SPINK1 - SCGB3A2C0.39
rs28559723e-12PRSS1 - PRSS2C0.08
rs37412973e-10ZPR1?
chr10:1129985901e-09T0.14
chr13:1137347354e-09C3.84
chr20:631264771e-08C3.74
chr9:744324232e-08G2.48
chr4:1636243093e-08T1.45
chr11:1163835754e-08T0.13
chrX:646267385e-08C1.75

Top studies (by case count)

StudyLead authorYearCasesControlsTitle
GCST90478483Verma A202412,564431,876Diversity and scale: Genetic architecture of 2068 traits in the VA Million Veteran Program.
GCST90478482Verma A20244,616115,057Diversity and scale: Genetic architecture of 2068 traits in the VA Million Veteran Program.
GCST90480360Verma A20244,616115,057Diversity and scale: Genetic architecture of 2068 traits in the VA Million Veteran Program.
GCST90473182UK Biobank Whole-Genome Sequencing Consortium20254,573453,867Whole-genome sequencing of 490,640 UK Biobank participants.
GCST90667895UK Biobank Whole-Genome Sequencing Consortium20254,573453,867Whole-genome sequencing of 490,640 UK Biobank participants.
GCST90473885UK Biobank Whole-Genome Sequencing Consortium20253,632454,808Whole-genome sequencing of 490,640 UK Biobank participants.
GCST90436394Zhou W20182,690406,271Efficiently controlling for case-control imbalance and sample relatedness in large-scale genetic association studies.
GCST90651267Liu TY20252,151234,326Diversity and longitudinal records: Genetic architecture of disease associations and polygenic risk in the Taiwanese Han population.
GCST90079750Backman JD20211,620385,084Exome sequencing and analysis of 454,787 UK Biobank participants.
GCST90083736Backman JD20211,620385,084Exome sequencing and analysis of 454,787 UK Biobank participants.

Variant details and genetic-evidence tiers

Tier distribution (top 50 variants)

TierVariants
Tier 1: coding1
Tier 2: splice/UTR0
Tier 3: regulatory0
Tier 4: intronic/intergenic12

MAF distribution

BucketVariants
common (>=0.05)3
low_freq (0.01-0.05)0
rare (<0.01)1
unknown9

Functional consequences

ConsequenceCount
unknown8
intron_variant2
intergenic_variant2
inframe_insertion1

Top variants

rsIDChrPosAllelesMAFConsequenceGenep-valueTier
chr6:326597039e-39Tier 4: intronic/intergenic
rs1139939607117559591ATCT>A,ATCTTCT0.05inframe_insertionCFTR3e-32Tier 1: coding
rs6795741948702851C>A,G0.474intron_variantFUT23e-15Tier 4: intronic/intergenic
rs1489117345147838808C>A,T0.008intergenic_variantSPINK1 - SCGB3A22e-12Tier 4: intronic/intergenic
rs28559727142756070C>A,G,T0.459intergenic_variantPRSS1 - PRSS23e-12Tier 4: intronic/intergenic
rs374129711116786951C>Tintron_variantZPR13e-10Tier 4: intronic/intergenic
chr10:1129985901e-09Tier 4: intronic/intergenic
chr13:1137347354e-09Tier 4: intronic/intergenic
chr20:631264771e-08Tier 4: intronic/intergenic
chr9:744324232e-08Tier 4: intronic/intergenic
chr4:1636243093e-08Tier 4: intronic/intergenic
chr11:1163835754e-08Tier 4: intronic/intergenic
chrX:646267385e-08Tier 4: intronic/intergenic

Genes & proteins

No associated-gene cohort resolved for this disease. Atlas builds the molecular and therapeutic sections — associated genes, protein families, druggability, pathways, interactions, and drug associations — by aggregating over a disease’s associated genes (resolved via GWAS / GenCC / ClinVar / CIViC), and none resolved here. This is expected for antibody-mediated, autoimmune, or otherwise non-gene-defined conditions; the curated evidence for this disease is its clinical features, GWAS susceptibility, and clinical trials (above).

Function

No pathway enrichment — requires an associated-gene cohort.

Therapeutics

No druggable-target or therapeutic data for this disease’s cohort.

Clinical trials & evidence

Clinical trials

Clinical trials: 137.

Phase distribution (across all retrieved trials)

PhaseTrials
Not specified114
PHASE47
PHASE36
PHASE26
PHASE2/PHASE32
PHASE1/PHASE21
PHASE11

Top trials by phase / activity

NCTPhaseStatusTitle
NCT07024199PHASE4RECRUITINGComparison of the Effectiveness of Paracetamol With Ibuprofen or Paracetamol With Metamizole in Treating Pain in Acute Pancreatitis in Children
NCT00526331PHASE4COMPLETEDEvaluation of Arterial Pressure Based Cardiac Output for Goal-Directed Perioperative Therapy
NCT00661648PHASE4UNKNOWNEffect of an Artificial Pancreas in Patients Undergoing Pancreatic Resection
NCT01350037PHASE4COMPLETEDAlfentanil Versus Remifentanil in Patient-controlled Sedation During Endoscopic Retrograde Cholangiopancreatography (ERCP)
NCT02092519PHASE4COMPLETEDRCT: Difference in Diagnostic Yield Between EUSFNA Needles With and Without a Side Port in Pancreatic Masses
NCT03198871PHASE4COMPLETEDIV Acetaminophen for Post-Operative Pain Management in Enhanced Recovery After Surgery (ERAS) Population
NCT05832047PHASE4COMPLETEDAggressive Hydration With Lactated Ringer’s Solution Versus Plasma Solution for the Prevention of Post ERCP Pancreatitis
NCT06861010PHASE3RECRUITINGEvaluating the Safety and Efficacy of Ondansetron in the Prevention of Post Endoscopic Retrograde Cholangiopancreatography Pancreatitis
NCT00731198PHASE3COMPLETEDDrotaverine Hydrochloride Versus Hyoscine-N-butylbromide for Duodenal Antimotility During Endoscopic Retrograde Cholangiopancreatography (ERCP)
NCT00975702PHASE3COMPLETEDRemote Ischemic Preconditioning In Abdominal Organ Transplantation
NCT01087801PHASE3COMPLETEDA Study of Synthetic Human Secretin (ChiRhoStim®) Administered Intravenously to Stimulate Exocrine Pancreas Fluid Secretion for Collection Via Endoscope and Laboratory Analysis of DNA Markers
NCT01964430PHASE3COMPLETEDNab-paclitaxel and Gemcitabine vs Gemcitabine Alone as Adjuvant Therapy for Patients With Resected Pancreatic Cancer (the Apact Study)
NCT03269994PHASE3COMPLETEDDoes Cefoxitin or Piperacillin-Tazobactam Prevent Postoperative Surgical Site Infections After Pancreatoduodenectomy?
NCT04021264PHASE2/PHASE3WITHDRAWNThe Impact of an Epidural Anesthetic on the Consumption of Sevoflurane in Major Abdominal Surgery
NCT04329039PHASE2/PHASE3SUSPENDEDSomatostatin Analogues With Perioperative Antibiotics Versus Prolonged Antibiotics
NCT07559175PHASE2NOT_YET_RECRUITINGA Study to Evaluate Safety and Explore Efficacy of New Lipase NHS7108 in Adult Participants With Exocrine Pancreatic Insufficiency.
NCT00040131PHASE2TERMINATEDSafety and Efficacy Study of IL-10 (Tenovil TM) in the Prevention of Post-ERCP Acute Pancreatitis (Study P02580)(TERMINATED)
NCT00902291PHASE2COMPLETEDA Study of AGS-1C4D4 Given in Combination With Gemcitabine in Subjects With Metastatic Pancreatic Cancer
NCT01608711PHASE2COMPLETEDA Study of AGS-1C4D4 in Pancreatic Cancer Subjects Previously Treated in Protocol 2008002
NCT03410914PHASE2COMPLETEDIntra-operative Application of HEMOPATCH to the Pancreatic Stump to Prevent Post-operative Pancreatic Fistula Following Distal Pancreatectomy
NCT03535727PHASE1/PHASE2COMPLETEDA Study of Gemcitabine, Nab-paclitaxel, Capecitabine, Cisplatin, and Irinotecan in Metastatic Pancreatic Cancer
NCT03717298PHASE2COMPLETEDEvaluation of Ocoxin-Viusid® in Advanced Pancreatic Adenocarcinoma
NCT01832116PHASE1COMPLETED89Zr-MMOT PET Imaging in Pancreatic and Ovarian Cancer Patients
NCT00830557Not specifiedRECRUITINGCollecting Medical Information and Tissue Samples From Patients With Pancreatic Cancer or Other Pancreatic Disorders
NCT02471170Not specifiedENROLLING_BY_INVITATIONProtocol to Permit the Acquisition of Circulating Tumor Material in Pancreatic Diseases
NCT03260842Not specifiedRECRUITINGBio-Repository of High Risk Cohorts for the Early Detection of Pancreas Cancer
NCT03334708Not specifiedRECRUITINGA Study of Blood Based Biomarkers for Pancreas Adenocarcinoma
NCT03807687Not specifiedRECRUITINGRegistry of Pancreatic Disease
NCT04259580Not specifiedRECRUITINGCalgary Registry for Advanced and Therapeutic Endoscopy
NCT04291651Not specifiedRECRUITINGUCSF PANC Cyst Registry
NCT04493632Not specifiedRECRUITINGOSPREY is a Post-market, Global, Multicentre, Observational, Prospective Registry.
NCT04556019Not specifiedRECRUITINGResults of Surgical Treatment of the Hepatobiliopancreatic Surgical Unit
NCT04760847Not specifiedNOT_YET_RECRUITINGIntermittent Fasting for Pancreatitis
NCT04949282Not specifiedRECRUITINGSpanish Series of Patients Treated With the Radionuclide Lutetium177
NCT05014347Not specifiedACTIVE_NOT_RECRUITINGPatient Reported Experience in Endoscopic Ultrasound
NCT05155878Not specifiedRECRUITINGPrognostic Factors in Periampullary Tumors and Cysts
NCT05193162Not specifiedRECRUITINGRetrospective Study on Microbial Diversity in Paraffin Tissue of Pancreatic Diseases
NCT05356039Not specifiedRECRUITINGSurvival, Quality of Life and Resectability in Locally Advanced Pancreatic Cancer
NCT05474417Not specifiedRECRUITINGThe Effects of the CF Carrier State on the Kidneys and Pancreas
NCT05714111Not specifiedRECRUITINGRadiology Registry on Pancreatic Malignancies

Drugs tested across these trials (top 30)

MoleculeMax phaseTrials referencing
ALFENTANIL41
CEFOXITIN41
DEXTROSE41
FIBRINOGEN I 12541
PANCRELIPASE41
PIPERACILLIN41
REMIFENTANIL41
SECRETIN SYNTHETIC HUMAN41
SOMATOSTATIN31
MK-472122
ALBACONAZOLE21
INTERLEUKIN-1021
CHEMBL548304001
CHEMBL42370701
SCEPTRIN01