Post-transplant lymphoproliferative disease

disease
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Also known as post-transplant lymphoproliferative disorderPTLD

Summary

Post-transplant lymphoproliferative disease (MONDO:0019088) is a disease and 64 clinical trials. Top therapeutic interventions include fludarabine phosphate, foscarnet, and cyclophosphamide anhydrous. A subtype of disease related to transplantation — broader associated-gene and molecular evidence is on the parent page (see Disease family below).

At a glance

  • Prevalence: 1-5 / 10 000 (Europe) [Orphanet-validated]
  • Phenotypes (HPO): 16
  • Clinical trials: 64

Clinical features

Epidemiology

Prevalence records

1 prevalence record(s), Orphanet:

TypeClassValueGeographyValidation
Point prevalence1-5 / 10 00026.2EuropeValidated

Signs & symptoms

Clinical features (HPO)

16 HPO clinical features (Orphanet curated; top 16 by frequency):

HPO IDTermFrequency
HP:0001608Abnormality of the voiceFrequent (30-79%)
HP:0001824Weight lossFrequent (30-79%)
HP:0001945FeverFrequent (30-79%)
HP:0002716LymphadenopathyFrequent (30-79%)
HP:0004396Poor appetiteFrequent (30-79%)
HP:0012378FatigueFrequent (30-79%)
HP:0025267SnoringFrequent (30-79%)
HP:0030166Night sweatsFrequent (30-79%)
HP:0033050PharyngalgiaFrequent (30-79%)
HP:0033834MalaiseFrequent (30-79%)
HP:0002014DiarrheaOccasional (5-29%)
HP:0002027Abdominal painOccasional (5-29%)
HP:0002239Gastrointestinal hemorrhageOccasional (5-29%)
HP:0003073HypoalbuminemiaOccasional (5-29%)
HP:0012115HepatitisOccasional (5-29%)
HP:0033608Pulmonary noduleOccasional (5-29%)

Identifiers

Disease identifiers

FieldValue
Canonical namepost-transplant lymphoproliferative disease
Mondo IDMONDO:0019088
Orphanet70568
ICD-10-CMD47.Z1
NCITC4727
SNOMED CT254290004
UMLSC0432487
MedGen98160
GARD0009553
MedDRA10051358
NORD1950
Is cancer (heuristic)no

Also known as: post-transplant lymphoproliferative disorder · PTLD

Data availability: 1 cell line.

Disease family

This is a subtype of disease related to transplantation. Genetic, therapeutic, and trial evidence is largely curated at the broader-term level — see the parent page for the associated-gene cohort and molecular evidence.

Classification path: disease › human disease › disease by etiologic mechanism › disease of primarily extrinsic mechanism › disease related to transplantationpost-transplant lymphoproliferative disease

Related subtypes (4): posttransplant acute limbic encephalitis, disease related to solid organ transplantation, disease related to hematopoietic stem cell transplant, transplant rejection

Genetics & variants

GWAS landscape

No GWAS associations recorded — common-variant (GWAS) studies don’t cover this disease (typical for Mendelian / rare diseases). See the curated gene cohort and Mendelian overlap below.

Variant details and genetic-evidence tiers

No tiered GWAS variants or ClinVar records for this disease.

Genes & proteins

No associated-gene cohort resolved for this disease. Atlas builds the molecular and therapeutic sections — associated genes, protein families, druggability, pathways, interactions, and drug associations — by aggregating over a disease’s associated genes (resolved via GWAS / GenCC / ClinVar / CIViC), and none resolved here. This is expected for antibody-mediated, autoimmune, or otherwise non-gene-defined conditions; the curated evidence for this disease is its clinical features, GWAS susceptibility, and clinical trials (above).

Function

No pathway enrichment — requires an associated-gene cohort.

Therapeutics

No druggable-target or therapeutic data for this disease’s cohort.

Clinical trials & evidence

Clinical trials

Clinical trials: 64.

Phase distribution (across all retrieved trials)

PhaseTrials
PHASE218
PHASE117
PHASE1/PHASE213
Not specified12
EARLY_PHASE12
PHASE41
PHASE31

Top trials by phase / activity

NCTPhaseStatusTitle
NCT01088724PHASE4COMPLETEDFludarabine, Cyclophosphamide, Doxorubicin and Rituximab for the Treatment of Post-transplant Lymphoproliferative Disease (PTLD)
NCT03386539PHASE3ACTIVE_NOT_RECRUITINGTacrolimus/Everolimus vs. Tacrolimus/MMF in Pediatric Heart Transplant Recipients Using the MATE Score
NCT05688241PHASE1/PHASE2NOT_YET_RECRUITINGEBV-Tscm Cytotoxic T Cells (CTLs) for EBV- Driven Lymphomas/ Diseases
NCT06040320PHASE1/PHASE2RECRUITINGPolatuzumab Vedotin (Pola) Plus Rituximab (R) in Patients With Post-transplant Lymphoproliferative Disorder (PTLD)
NCT07368634PHASE1/PHASE2RECRUITINGExploratory Study of EBV-TCR-T Cell Injection for EBV DNAemia After Allogeneic Hematopoietic Stem Cell Transplantation
NCT07438067PHASE1/PHASE2RECRUITINGEBV-AST Cell Therapy for EBV-Related Diseases After Stem Cell Transplantation
NCT07573436PHASE1/PHASE2NOT_YET_RECRUITINGLoncastuximab Tesirine and Rituximab as First-line Therapy in Patients With Post-transplant Lymphoproliferative Disorder (PLUTO)
NCT00006251PHASE1/PHASE2COMPLETEDFludarabine Phosphate, Low-Dose Total-Body Irradiation, and Donor Stem Cell Transplant Followed by Cyclosporine, Mycophenolate Mofetil, Donor Lymphocyte Infusion in Treating Patients With Hematopoietic Cancer
NCT00049504PHASE2COMPLETEDHaploidentical Donor Bone Marrow Transplant in Treating Patients With High-Risk Hematologic Cancer
NCT00064246PHASE1/PHASE2COMPLETEDYttrium Y 90 Ibritumomab Tiuxetan and Rituximab in Treating Patients With Post-Transplant Lymphoproliferative Disorder
NCT00078858PHASE1/PHASE2COMPLETEDMycophenolate Mofetil and Cyclosporine in Reducing Graft-Versus-Host Disease in Patients With Hematologic Malignancies or Metastatic Kidney Cancer Undergoing Donor Stem Cell Transplant
NCT00089011PHASE2COMPLETEDTacrolimus and Mycophenolate Mofetil in Preventing Graft-Versus-Host Disease in Patients Who Have Undergone Total-Body Irradiation With or Without Fludarabine Phosphate Followed by Donor Peripheral Blood Stem Cell Transplant for Hematologic Cancer
NCT00590447PHASE2COMPLETEDRisk Stratified Sequential Treatment for CD20-positive PTLD
NCT00867529PHASE2COMPLETEDRituximab in Treating Patients Undergoing Donor Peripheral Blood Stem Cell Transplant for Relapsed or Refractory B-cell Lymphoma
NCT00918333PHASE1/PHASE2COMPLETEDPanobinostat and Everolimus in Treating Patients With Recurrent Multiple Myeloma, Non-Hodgkin Lymphoma, or Hodgkin Lymphoma
NCT01058239PHASE2COMPLETEDBortezomib Plus Rituximab for EBV+ PTLD
NCT01075321PHASE1/PHASE2COMPLETEDEverolimus and Lenalidomide in Treating Patients With Relapsed or Refractory Non-Hodgkin or Hodgkin Lymphoma
NCT01177371PHASE2COMPLETEDHigh-Dose Busulfan and High-Dose Cyclophosphamide Followed By Donor Bone Marrow Transplant in Treating Patients With Leukemia, Myelodysplastic Syndrome, Multiple Myeloma, or Recurrent Hodgkin or Non-Hodgkin Lymphoma
NCT01261247PHASE2COMPLETEDPanobinostat in Treating Patients With Relapsed or Refractory Non-Hodgkin Lymphoma
NCT01427881PHASE2COMPLETEDCyclophosphamide for Prevention of Graft-Versus-Host Disease After Allogeneic Peripheral Blood Stem Cell Transplantation in Patients With Hematological Malignancies
NCT01434472PHASE2TERMINATEDHigh-Dose Y-90-Ibritumomab Tiuxetan Added to Reduced-Intensity Allogeneic Stem Cell Transplant Regimen for Relapsed or Refractory Aggressive B-Cell Lymphoma
NCT01529827PHASE2COMPLETEDFludarabine Phosphate, Melphalan, and Low-Dose Total-Body Irradiation Followed by Donor Peripheral Blood Stem Cell Transplant in Treating Patients With Hematologic Malignancies
NCT01652014PHASE2WITHDRAWNSingle or Double Donor Umbilical Cord Blood Transplant in Treating Patients With High-Risk Hematologic Malignancies
NCT01789255PHASE2COMPLETEDVorinostat, Tacrolimus, and Methotrexate in Preventing GVHD After Stem Cell Transplant in Patients With Hematological Malignancies
NCT01805037PHASE1/PHASE2TERMINATEDBrentuximab Vedotin + Rituximab as Frontline Therapy for Pts w/ CD30+ and/or EBV+ Lymphomas
NCT01839916PHASE2COMPLETEDDonor T Cells After Donor Stem Cell Transplant in Treating Patients With Hematologic Malignancies
NCT01964755PHASE2TERMINATEDChemotherapy for Relapsed Epstein Barr Virus Associated Lymphoma
NCT02580539PHASE1/PHASE2COMPLETEDA Study of the Safety and Efficacy of EBV Specific T-cell Lines
NCT02763254PHASE2TERMINATEDCellular Immunotherapy for Viral Induced Cancer - EBV Positive Lymphomas
NCT03086395PHASE2WITHDRAWNSingle Agent Obinutuzumab in Relapsed/Refractory Post-Transplant Lymphoproliferative Disorder (PTLD)
NCT04138875PHASE2WITHDRAWNA Risk Stratified Sequential Treatment With Rituximab, Brentuximab Vedotin and Bendamustine (RBvB)
NCT04337827PHASE2TERMINATEDRituximab and Acalabrutinib in Newly Diagnosed B Cell Post Transplant Lymphoproliferative Disorder
NCT04507477PHASE1/PHASE2UNKNOWNEx-vivo Delivery of Rituximab to Prevent PTLD in EBV Mismatch Lung Transplant Recipients: A Pilot Trial
NCT01815749PHASE1ACTIVE_NOT_RECRUITINGGenetically Modified T-cell Infusion Following Peripheral Blood Stem Cell Transplant in Treating Patients With Recurrent or High-Risk Non-Hodgkin Lymphoma
NCT02153580PHASE1ACTIVE_NOT_RECRUITINGCellular Immunotherapy Following Chemotherapy in Treating Patients With Recurrent Non-Hodgkin Lymphomas, Chronic Lymphocytic Leukemia, or B-Cell Prolymphocytic Leukemia
NCT06666153PHASE1NOT_YET_RECRUITINGClinical Study of Therapeutic Immunological Agent for EBV Lymphoproliferative Diseases
NCT07614282PHASE1NOT_YET_RECRUITINGRituximab for PTLD Prevention in Solid Organ Transplant Recipients With EBV DNAemia
NCT00036855PHASE1TERMINATEDRadiolabeled Monoclonal Antibody With or Without Peripheral Stem Cell Transplantation in Treating Children With Recurrent or Refractory Lymphoma
NCT00348985PHASE1COMPLETEDPXD101 and Bortezomib in Treating Patients With Advanced Solid Tumors or Lymphomas
NCT00354185PHASE1TERMINATEDPXD101 and 17-N-Allylamino-17-Demethoxygeldanamycin in Treating Patients With Metastatic or Unresectable Solid Tumors or Lymphoma

Drugs tested across these trials (top 30)

MoleculeMax phaseTrials referencing
FLUDARABINE PHOSPHATE412
FOSCARNET44
CYCLOPHOSPHAMIDE ANHYDROUS43
DOXORUBICIN43
YTTRIUM Y 90 IBRITUMOMAB TIUXETAN43
BELINOSTAT42
PANOBINOSTAT42
ACALABRUTINIB41
AZACITIDINE41
BENDAMUSTINE41
BRENTUXIMAB VEDOTIN41
GANCICLOVIR41
HYDROXYUREA41
LONCASTUXIMAB TESIRINE41
OBINUTUZUMAB41
POLATUZUMAB VEDOTIN41
RITUXIMAB41
VALGANCICLOVIR41
INDIUM IN 111 IBRITUMOMAB TIUXETAN32
FLUDARABINE31
QS-2131
TANESPIMYCIN31
AR-4221
BALTALEUCEL-T21
CHLORHEXIDINE PHOSPHANILATE11
CHEMBL34422702
CHEMBL29007701
CHEMBL474750601
CHEMBL518755401
CHEMBL527692501