Postpoliomyelitis syndrome

disease
On this page

Also known as polio late effectsPost Polio Syndromepost-polio muscular atrophypost-polio sequelaepost-poliomyelitic syndromepostpolio sequelaepostpolio syndromepostpoliomyelitic syndromepostpoliomyelitis sequelae

Summary

Postpoliomyelitis syndrome (MONDO:0017416) is a disease and 20 clinical trials. Top therapeutic interventions include levocarnitine, modafinil, and piracetam. A subtype of poliomyelitis — broader associated-gene and molecular evidence is on the parent page (see Disease family below).

At a glance

  • Prevalence: Unknown (Worldwide) [Orphanet-validated]
  • Phenotypes (HPO): 17
  • Clinical trials: 20

Clinical features

Signs & symptoms

Clinical features (HPO)

17 HPO clinical features (Orphanet curated; top 17 by frequency):

HPO IDTermFrequency
HP:0001324Muscle weaknessVery frequent (80-99%)
HP:0012531PainVery frequent (80-99%)
HP:0002829ArthralgiaFrequent (30-79%)
HP:0003326MyalgiaFrequent (30-79%)
HP:0003551Difficulty climbing stairsFrequent (30-79%)
HP:0011446Abnormality of higher mental functionFrequent (30-79%)
HP:0012378FatigueFrequent (30-79%)
HP:0100786HypersomniaFrequent (30-79%)
HP:0001260DysarthriaOccasional (5-29%)
HP:0001367Abnormal joint morphologyOccasional (5-29%)
HP:0002015DysphagiaOccasional (5-29%)
HP:0002093Respiratory insufficiencyOccasional (5-29%)
HP:0002360Sleep abnormalityOccasional (5-29%)
HP:0002380FasciculationsOccasional (5-29%)
HP:0003202Skeletal muscle atrophyOccasional (5-29%)
HP:0003394Muscle spasmOccasional (5-29%)
HP:0002791HypoventilationVery rare (<1-4%)

Identifiers

Disease identifiers

FieldValue
Canonical namepostpoliomyelitis syndrome
Mondo IDMONDO:0017416
EFOEFO:0007454
MeSHD016262
Orphanet2942
DOIDDOID:4952
ICD-10-CMG14
ICD-112018885243
SNOMED CT31097004
UMLSC0080040
MedGen36363
GARD0004454
NORD1600
Is cancer (heuristic)no

Also known as: polio late effects · Post Polio Syndrome · post polio syndrome · post-polio muscular atrophy · post-polio sequelae · post-poliomyelitic syndrome · postpolio sequelae · postpolio syndrome · postpoliomyelitic syndrome · postpoliomyelitis sequelae · postpoliomyelitis syndrome

Disease family

This is a subtype of poliomyelitis. Genetic, therapeutic, and trial evidence is largely curated at the broader-term level — see the parent page for the associated-gene cohort and molecular evidence.

Classification path: disease › human disease › disease by body system or component › nervous system disordercentral nervous system disorderspinal cord disordermyelitispoliomyelitispostpoliomyelitis syndrome

Related subtypes (2): paralytic poliomyelitis, acute nonparalytic poliomyelitis

Genetics & variants

GWAS landscape

No GWAS associations recorded — common-variant (GWAS) studies don’t cover this disease (typical for Mendelian / rare diseases). See the curated gene cohort and Mendelian overlap below.

Variant details and genetic-evidence tiers

No tiered GWAS variants or ClinVar records for this disease.

Genes & proteins

No associated-gene cohort resolved for this disease. Atlas builds the molecular and therapeutic sections — associated genes, protein families, druggability, pathways, interactions, and drug associations — by aggregating over a disease’s associated genes (resolved via GWAS / GenCC / ClinVar / CIViC), and none resolved here. This is expected for antibody-mediated, autoimmune, or otherwise non-gene-defined conditions; the curated evidence for this disease is its clinical features, GWAS susceptibility, and clinical trials (above).

Function

No pathway enrichment — requires an associated-gene cohort.

Therapeutics

Drugs indicated for this disease

0 approved, 6 in late-stage (phase 3) trials. Disease-direct ChEMBL indications, not inferred from the associated-gene cohort below.

DrugDevelopment status
Human Immunoglobulin GPhase 3 (in late-stage trials)
L-CitrullinePhase 3 (in late-stage trials)
LevocarnitinePhase 3 (in late-stage trials)
ModafinilPhase 3 (in late-stage trials)
PiracetamPhase 3 (in late-stage trials)
Sodium ChloridePhase 3 (in late-stage trials)

Earlier-phase candidates (phase 2, investigational — efficacy not yet established): Poliovirus Vaccine Inactivated.

Clinical trials & evidence

Clinical trials

Clinical trials: 20.

Phase distribution (across all retrieved trials)

PhaseTrials
Not specified14
PHASE34
PHASE2/PHASE32

Top trials by phase / activity

NCTPhaseStatusTitle
NCT00067496PHASE3TERMINATEDModafinil to Treat Fatigue in Post-Polio Syndrome
NCT00231439PHASE2/PHASE3COMPLETEDPost-Poliosyndrome Treated With Intravenous Immunoglobulin (IvIg)
NCT01537575PHASE3COMPLETEDIntravenous Immunoglobulins for Post-Polio Syndrome
NCT01549847PHASE3WITHDRAWNA Randomized, Double Blind, Placebo Controlled Trial L-carnitine and Piracetam in the Treatment of Weakness, Muscle Fatigue and Muscle Pain in the Postpoliomyelitis Syndrome
NCT02176863PHASE2/PHASE3TERMINATEDStudy of the Efficacy and Safety of Immune Globulin Intravenous (Human) Flebogamma® 5% Dual Inactivation and Filtration (DIF) in Participants With Post-polio Syndrome
NCT02801071PHASE3COMPLETEDL-Citrulline in Patients With Post-Polio Syndrome
NCT02089880Not specifiedACTIVE_NOT_RECRUITINGComparing Functional Outcomes in Individuals Using Micro-processor Controlled Orthosis Versus Stance Control Orthosis
NCT05644522Not specifiedRECRUITINGNomad P-KAFO Study
NCT05663008Not specifiedRECRUITINGImpairments of Neuro-muscular Communication in Motor-Neuron Disease: A Bio-Marker for Early and Personalised Diagnosis
NCT07478172Not specifiedRECRUITINGEffects of Whole-body Electrical Muscle Stimulation Exercise on Adults With Neuromuscular Disease
NCT00001185Not specifiedCOMPLETEDStudy of Post-Polio Syndrome
NCT00004553Not specifiedCOMPLETEDElectromyography to Diagnose Neuromuscular Disorders
NCT01271530Not specifiedCOMPLETEDArm Cycling to Improve Fitness in Polio Survivors
NCT01402570Not specifiedCOMPLETEDGlutathione and Health With Post-Polio Syndrome
NCT02815878Not specifiedCOMPLETEDEnhance Wellness for Individuals With Long-Term Physical Disabilities
NCT03064711Not specifiedCOMPLETEDActivity and Fatigue of the Respiratory Muscles and Pulmonary Characteristics in Post-Polio Patients
NCT03561623Not specifiedUNKNOWNSpinal Cord Gray Matter Imaging in Post Polio Syndrome
NCT04387864Not specifiedCOMPLETEDWhole Body Vibration on Muscle Strength in Patients With Postpolio Syndrome
NCT06320444Not specifiedUNKNOWNNon-invasive Spinal, Cortical, and Sensorimotor Biomarkers in Motor Neurone Disease
NCT06926270Not specifiedCOMPLETEDEffectiveness of Transcranial Magnetic Stimulation Treatment in Patients Diagnosed With Postpolio Syndrome

Drugs tested across these trials (top 30)

MoleculeMax phaseTrials referencing
LEVOCARNITINE41
MODAFINIL41
PIRACETAM41
GLUTATHIONE31
CHEMBL4690901