Posttransplant acute limbic encephalitis

disease
On this page

Also known as PALE

Summary

Posttransplant acute limbic encephalitis (MONDO:0015595) is a disease. A subtype of limbic encephalitis — broader associated-gene and molecular evidence is on the parent page (see Disease family below).

At a glance

  • Prevalence: Unknown (Worldwide)
  • Phenotypes (HPO): 23

Clinical features

Signs & symptoms

Clinical features (HPO)

23 HPO clinical features (Orphanet curated; top 23 by frequency):

HPO IDTermFrequency
HP:0001250SeizureFrequent (30-79%)
HP:0002354Memory impairmentFrequent (30-79%)
HP:0002902HyponatremiaFrequent (30-79%)
HP:0002922Increased CSF protein concentrationFrequent (30-79%)
HP:0011185EEG with focal epileptiform dischargesFrequent (30-79%)
HP:0012756CSF polymorphonuclear pleocytosisFrequent (30-79%)
HP:0020071ViremiaFrequent (30-79%)
HP:0031885HyperglycorrhachiaFrequent (30-79%)
HP:0100806SepsisFrequent (30-79%)
HP:0200149CSF lymphocytic pleiocytosisFrequent (30-79%)
HP:0000708Atypical behaviorOccasional (5-29%)
HP:0000709PsychosisOccasional (5-29%)
HP:0000716DepressionOccasional (5-29%)
HP:0000739AnxietyOccasional (5-29%)
HP:0001251AtaxiaOccasional (5-29%)
HP:0001289ConfusionOccasional (5-29%)
HP:0001332DystoniaOccasional (5-29%)
HP:0001336MyoclonusOccasional (5-29%)
HP:0011203EEG with abnormally slow frequenciesOccasional (5-29%)
HP:0012332Abnormal autonomic nervous system physiologyOccasional (5-29%)
HP:0025100Abnormal hippocampus morphologyOccasional (5-29%)
HP:0100022Abnormality of movementOccasional (5-29%)
HP:0100543Cognitive impairmentOccasional (5-29%)

Identifiers

Disease identifiers

FieldValue
Canonical nameposttransplant acute limbic encephalitis
Mondo IDMONDO:0015595
Orphanet163921
UMLSC4750744
MedGen1657779
GARD0020051
Is cancer (heuristic)no

Also known as: PALE · pale

Disease family

This is a subtype of limbic encephalitis. Genetic, therapeutic, and trial evidence is largely curated at the broader-term level — see the parent page for the associated-gene cohort and molecular evidence.

Classification path: disease › human disease › disease by body system or component › nervous system disordercentral nervous system disorderencephalomyelitisencephalitislimbic encephalitisposttransplant acute limbic encephalitis

Related subtypes (5): paraneoplastic limbic encephalitis, non-herpetic acute limbic encephalitis, limbic encephalitis with caspr2 antibodies, limbic encephalitis with DPP6 antibodies, autoimmune limbic encephalitis

Genetics & variants

GWAS landscape

No GWAS associations recorded — common-variant (GWAS) studies don’t cover this disease (typical for Mendelian / rare diseases). See the curated gene cohort and Mendelian overlap below.

Variant details and genetic-evidence tiers

No tiered GWAS variants or ClinVar records for this disease.

Genes & proteins

No associated-gene cohort resolved for this disease. Atlas builds the molecular and therapeutic sections — associated genes, protein families, druggability, pathways, interactions, and drug associations — by aggregating over a disease’s associated genes (resolved via GWAS / GenCC / ClinVar / CIViC), and none resolved here. This is expected for antibody-mediated, autoimmune, or otherwise non-gene-defined conditions; the curated evidence for this disease is its clinical features, GWAS susceptibility, and clinical trials (above).

Function

No pathway enrichment — requires an associated-gene cohort.

Therapeutics

No druggable-target or therapeutic data for this disease’s cohort.

Clinical trials & evidence

Clinical trials

Clinical trials: 0.

No linked Atlas pages yet — the cross-entity mesh grows as the corpus expands.