Psoriasis-related juvenile idiopathic arthritis

disease
On this page

Also known as JPsAjuvenile psoriatic arthritispsoriasis-related JIA

Summary

Psoriasis-related juvenile idiopathic arthritis (MONDO:0019436) is a disease and 11 clinical trials. Top therapeutic interventions include secukinumab, cravacitinib, and apremilast. A subtype of juvenile idiopathic arthritis — broader associated-gene and molecular evidence is on the parent page (see Disease family below).

At a glance

  • Prevalence: Unknown (Worldwide) [Orphanet-validated]
  • Phenotypes (HPO): 29
  • Clinical trials: 11

Clinical features

Signs & symptoms

Clinical features (HPO)

29 HPO clinical features (Orphanet curated; top 29 by frequency):

HPO IDTermFrequency
HP:0011118Abnormality of tumor necrosis factor secretionVery frequent (80-99%)
HP:0000989PruritusFrequent (30-79%)
HP:0001369ArthritisFrequent (30-79%)
HP:0001803Nail pitsFrequent (30-79%)
HP:0002829ArthralgiaFrequent (30-79%)
HP:0002960AutoimmunityFrequent (30-79%)
HP:0003493Antinuclear antibody positivityFrequent (30-79%)
HP:0003765Psoriasiform dermatitisFrequent (30-79%)
HP:0005764Polyarticular arthritisFrequent (30-79%)
HP:0031090Finger dactylitisFrequent (30-79%)
HP:0031091Toe dactylitisFrequent (30-79%)
HP:0040313OligoarthritisFrequent (30-79%)
HP:0100686EnthesitisFrequent (30-79%)
HP:0000554UveitisOccasional (5-29%)
HP:0000988Skin rashOccasional (5-29%)
HP:0001376Limitation of joint mobilityOccasional (5-29%)
HP:0002815Abnormality of the kneeOccasional (5-29%)
HP:0003019Abnormality of the wristOccasional (5-29%)
HP:0003043Abnormality of the shoulderOccasional (5-29%)
HP:0005197Generalized morning stiffnessOccasional (5-29%)
HP:0007663Reduced visual acuityOccasional (5-29%)
HP:0012122Anterior uveitisOccasional (5-29%)
HP:0025300Malar rashOccasional (5-29%)
HP:0025526Psoriasiform lesionOccasional (5-29%)
HP:0001094IridocyclitisVery rare (<1-4%)
HP:0001101IritisVery rare (<1-4%)
HP:0001806OnycholysisVery rare (<1-4%)
HP:0010754Abnormality of the temporomandibular jointVery rare (<1-4%)
HP:0012317Sacroiliac arthritisVery rare (<1-4%)

Identifiers

Disease identifiers

FieldValue
Canonical namepsoriasis-related juvenile idiopathic arthritis
Mondo IDMONDO:0019436
EFOEFO:0009733
Orphanet85436
ICD-111473955563
NCITC114361
SNOMED CT239802003
UMLSC3714758
MedGen811463
GARD0010970
Is cancer (heuristic)no

Also known as: JPsA · juvenile psoriatic arthritis · psoriasis-related JIA

Disease family

This is a subtype of juvenile idiopathic arthritis. Genetic, therapeutic, and trial evidence is largely curated at the broader-term level — see the parent page for the associated-gene cohort and molecular evidence.

Classification path: disease › human disease › disease by body system or component › connective tissue disorderrheumatic disorderjuvenile idiopathic arthritispsoriasis-related juvenile idiopathic arthritis

Related subtypes (5): polyarticular juvenile idiopathic arthritis, oligoarticular juvenile idiopathic arthritis, systemic-onset juvenile idiopathic arthritis, enthesitis-related juvenile idiopathic arthritis, unspecified juvenile idiopathic arthritis

Genetics & variants

GWAS landscape

No GWAS associations recorded — common-variant (GWAS) studies don’t cover this disease (typical for Mendelian / rare diseases). See the curated gene cohort and Mendelian overlap below.

Variant details and genetic-evidence tiers

No tiered GWAS variants or ClinVar records for this disease.

Genes & proteins

No associated-gene cohort resolved for this disease. Atlas builds the molecular and therapeutic sections — associated genes, protein families, druggability, pathways, interactions, and drug associations — by aggregating over a disease’s associated genes (resolved via GWAS / GenCC / ClinVar / CIViC), and none resolved here. This is expected for antibody-mediated, autoimmune, or otherwise non-gene-defined conditions; the curated evidence for this disease is its clinical features, GWAS susceptibility, and clinical trials (above).

Function

No pathway enrichment — requires an associated-gene cohort.

Therapeutics

Drugs indicated for this disease

1 approved, 1 in late-stage (phase 3) trials. Disease-direct ChEMBL indications, not inferred from the associated-gene cohort below.

DrugDevelopment status
AdalimumabApproved (phase 4)
RisankizumabPhase 3 (in late-stage trials)

Clinical trials & evidence

Clinical trials

Clinical trials: 11.

Phase distribution (across all retrieved trials)

PhaseTrials
PHASE37
PHASE12
Not specified2

Top trials by phase / activity

NCTPhaseStatusTitle
NCT04527380PHASE3ACTIVE_NOT_RECRUITINGA Study of Ixekizumab (LY2439821) in Children With Juvenile Idiopathic Arthritis Categories of Enthesitis-related Arthritis (Including Juvenile Onset Ankylosing Spondylitis) and Juvenile Psoriatic Arthritis
NCT05767047PHASE3RECRUITINGA Study of Apremilast in Children With Oral Ulcers Associated With Behçet’s Disease or Juvenile Psoriatic Arthritis
NCT06100744PHASE3RECRUITINGA Study to Assess Adverse Events, Change in Disease Activity, and How the Drug Moves Through the Body in Children With Juvenile Psoriatic Arthritis (jPsA) Receiving Subcutaneously Injected Risankizumab or Adalimumab
NCT06668181PHASE3RECRUITINGAn Open-label Study to Evaluate the Pharmacokinetics and Safety of Bimekizumab in Pediatric Study Participants With Active Juvenile Idiopathic Arthritis Subtypes Enthesitis-related Arthritis (Including Juvenile-onset Ankylosing Spondylitis) and Juvenile Psoriatic Arthritis
NCT06869551PHASE3RECRUITINGA Study to Evaluate the Drug Levels, Efficacy, and Safety of Deucravacitinib (BMS-986165) in Pediatric Participants With Juvenile Psoriatic Arthritis
NCT03031782PHASE3COMPLETEDSecukinumab Safety and Efficacy in Juvenile Psoriatic Arthritis (JPsA) and Enthesitis-related Arthritis (ERA)
NCT03769168PHASE3COMPLETEDAn Extension Study of Subcutaneous Secukinumab in Patients With Juvenile Psoriatic Arthritis (JPsA) and Enthesitis Related Arthritis (ERA)
NCT06751238PHASE1RECRUITINGStudy to Evaluate the Pharmacokinetics (PK), Safety and Tolerability up to 6 Years of Intravenous (i.v.) Secukinumab in Pediatric Participants With Juvenile Psoriatic Arthritis (JPsA).
NCT05252533PHASE1COMPLETEDA Study of Ustekinumab in Pediatric Participants (U-POPS) With Juvenile Psoriatic Arthritis or Psoriasis
NCT07190053Not specifiedNOT_YET_RECRUITINGLong Term Treatment Strategies and Effectiveness of Secukinumab in Patient With JIA Subtypes of JPsA and ERA: Study From German BIKER Registry.
NCT05545839Not specifiedCOMPLETEDTransition to Adulthood Through Coaching and Empowerment in Rheumatology

Drugs tested across these trials (top 30)

MoleculeMax phaseTrials referencing
SECUKINUMAB44
CRAVACITINIB43
APREMILAST41
BIMEKIZUMAB41
IXEKIZUMAB41
RISANKIZUMAB41
CHEMBL47516501