Rheumatic disorder

disease
On this page

Also known as disease, rheumaticdiseases, rheumaticenthesopathiesenthesopathyrheumatic diseaserheumatismrheumatologic disorder

Summary

Rheumatic disorder (MONDO:0005554) is a disease (an umbrella term covering 30 Mondo subtypes) with 10 GWAS associations across 17 studies and 172 clinical trials. Top therapeutic interventions include abatacept, azathioprine, and belimumab. A subtype of connective tissue disorder — broader associated-gene and molecular evidence is on the parent page (see Disease family below).

At a glance

  • Umbrella term: 30 Mondo subtypes
  • GWAS associations: 10
  • Clinical trials: 172

Clinical features

No curated clinical features (Orphanet) for this disease.

Identifiers

Disease identifiers

FieldValue
Canonical namerheumatic disorder
Mondo IDMONDO:0005554
EFOEFO:0005755
MeSHD012216
DOIDDOID:1575
NCITC27204
SNOMED CT396332003
UMLSC0009326
MedGen3157
Is cancer (heuristic)no

Also known as: disease, rheumatic · diseases, rheumatic · enthesopathies · enthesopathy · rheumatic disease · rheumatism · rheumatologic disorder

Data availability: 10 GWAS associations (17 studies).

Disease family

This is a subtype of connective tissue disorder. Genetic, therapeutic, and trial evidence is largely curated at the broader-term level — see the parent page for the associated-gene cohort and molecular evidence.

Classification path: disease › human disease › disease by body system or component › connective tissue disorderrheumatic disorder

Related subtypes (15): benign connective and soft tissue neoplasm, ochronosis disorder, enthesopathy, synovitis, collagenopathy, fasciitis, interstitial keratitis, periostitis, panniculitis, ainhum, overlapping connective tissue disease, interstitial cystitis, connective tissue neoplasm, hereditary disorder of connective tissue, disease of the tendon

Subtypes (30): palindromic rheumatism, rheumatic pulmonary valve disease, lupus erythematosus, mixed connective tissue disease, Reye syndrome, Wissler syndrome, acroosteolysis dominant type, chondrocalcinosis 2, Gorham-Stout disease, rheumatoid arthritis, camptodactyly-arthropathy-coxa vara-pericarditis syndrome, juvenile idiopathic arthritis, sweet syndrome, dermatomyositis, IL10-related early-onset inflammatory bowel disease, unexplained long-lasting fever/inflammatory syndrome, myalgia-eosinophilia syndrome associated with tryptophan, reactive arthritis, rheumatic fever, intermittent hydrarthrosis, fibroblastic rheumatism, interstitial granulomatous dermatitis with arthritis, scleroderma, idiopathic juvenile osteoporosis, polymyalgia rheumatica, autoinflammatory syndrome, progeria-associated arthropathy, LAMA5-related multisystemic syndrome, rheumatic disease of mitral valve, isolated sternocostoclavicular hyperostosis

Genetics & variants

GWAS landscape

10 GWAS associations across 17 studies. Top hits map to 7 distinct genes (as reported by GWAS).

Top associations by p-value

rsIDp-valueGeneRisk alleleOdds ratio
rs728018594e-14RBL2, AKTIPC4.84
rs1405192662e-13SDK2C3.46
rs1424025243e-12LINC02772 - FCRL5G4.73
rs1928870069e-12ROBO2P1 - RN7SL292PA3.61
rs1820476501e-11MDN1G4.8
rs5513133852e-11CBX4 - LINC01979G3.22
rs7806332133e-11ACADSB - HMX3C4.03
rs1815682344e-11WWOXA2.48
rs5723578105e-11FHIT - PTPRGT5.12
rs1855282791e-08CDSN, PSORS1C1?

Top studies (by case count)

StudyLead authorYearCasesControlsTitle
GCST90478966Verma A20241,732448,852Diversity and scale: Genetic architecture of 2068 traits in the VA Million Veteran Program.
GCST90651496Liu TY20251,546210,582Diversity and longitudinal records: Genetic architecture of disease associations and polygenic risk in the Taiwanese Han population.
GCST90079959Backman JD20211,144386,786Exome sequencing and analysis of 454,787 UK Biobank participants.
GCST90083945Backman JD20211,144386,786Exome sequencing and analysis of 454,787 UK Biobank participants.
GCST90080543Backman JD20211,093386,775Exome sequencing and analysis of 454,787 UK Biobank participants.
GCST90084529Backman JD20211,093386,775Exome sequencing and analysis of 454,787 UK Biobank participants.
GCST90436693Zhou W20181,010378,711Efficiently controlling for case-control imbalance and sample relatedness in large-scale genetic association studies.
GCST90079958Backman JD2021732387,198Exome sequencing and analysis of 454,787 UK Biobank participants.
GCST90083944Backman JD2021732387,198Exome sequencing and analysis of 454,787 UK Biobank participants.
GCST90080542Backman JD2021657387,273Exome sequencing and analysis of 454,787 UK Biobank participants.

Variant details and genetic-evidence tiers

Tier distribution (top 50 variants)

TierVariants
Tier 1: coding0
Tier 2: splice/UTR1
Tier 3: regulatory0
Tier 4: intronic/intergenic9

MAF distribution

BucketVariants
common (>=0.05)0
low_freq (0.01-0.05)0
rare (<0.01)9
unknown1

Functional consequences

ConsequenceCount
intron_variant7
intergenic_variant2
3_prime_UTR_variant1

Top variants

rsIDChrPosAllelesMAFConsequenceGenep-valueTier
rs728018591653490742C>G0.0013_prime_UTR_variantRBL2, AKTIP4e-14Tier 2: splice/UTR
rs1405192661773484110C>T0.001intron_variantSDK22e-13Tier 4: intronic/intergenic
rs1424025241157332951G>A0.001intergenic_variantLINC02772 - FCRL53e-12Tier 4: intronic/intergenic
rs192887006751705755A>G0.002intron_variantROBO2P1 - RN7SL292P9e-12Tier 4: intronic/intergenic
rs182047650689808945G>A,T0.001intron_variantMDN11e-11Tier 4: intronic/intergenic
rs5513133851779850109G>A0intron_variantCBX4 - LINC019792e-11Tier 4: intronic/intergenic
rs78063321310123106494C>G,T0intergenic_variantACADSB - HMX33e-11Tier 4: intronic/intergenic
rs1815682341678922369A>G0.001intron_variantWWOX4e-11Tier 4: intronic/intergenic
rs572357810361311665T>A0intron_variantFHIT - PTPRG5e-11Tier 4: intronic/intergenic
rs185528279631119172A>Gintron_variantCDSN, PSORS1C11e-08Tier 4: intronic/intergenic

Genes & proteins

No associated-gene cohort resolved for this disease. Atlas builds the molecular and therapeutic sections — associated genes, protein families, druggability, pathways, interactions, and drug associations — by aggregating over a disease’s associated genes (resolved via GWAS / GenCC / ClinVar / CIViC), and none resolved here. This is expected for antibody-mediated, autoimmune, or otherwise non-gene-defined conditions; the curated evidence for this disease is its clinical features, GWAS susceptibility, and clinical trials (above).

Function

No pathway enrichment — requires an associated-gene cohort.

Therapeutics

Drugs indicated for this disease

47 approved, 5 in late-stage (phase 3) trials. Disease-direct ChEMBL indications, not inferred from the associated-gene cohort below.

DrugDevelopment status
AcemetacinApproved (phase 4)
AlclofenacApproved (phase 4)
AuranofinApproved (phase 4)
AurothioglucoseApproved (phase 4)
BenoxaprofenApproved (phase 4)
BenzydamineApproved (phase 4)
BufexamacApproved (phase 4)
CaptoprilApproved (phase 4)
CelecoxibApproved (phase 4)
DexibuprofenApproved (phase 4)
DexketoprofenApproved (phase 4)
DiacereinApproved (phase 4)
DiclofenacApproved (phase 4)
EtodolacApproved (phase 4)
EtoricoxibApproved (phase 4)
FenoprofenApproved (phase 4)
FeprazoneApproved (phase 4)
FlurbiprofenApproved (phase 4)
GlucosamineApproved (phase 4)
IbuprofenApproved (phase 4)
IndomethacinApproved (phase 4)
IndoprofenApproved (phase 4)
KetoprofenApproved (phase 4)
KetorolacApproved (phase 4)
LornoxicamApproved (phase 4)
LoxoprofenApproved (phase 4)
LumiracoxibApproved (phase 4)
Meclofenamic AcidApproved (phase 4)
Mefenamic AcidApproved (phase 4)
MeloxicamApproved (phase 4)
NabumetoneApproved (phase 4)
NaproxenApproved (phase 4)
NimesulideApproved (phase 4)
OrgoteinApproved (phase 4)
OxaprozinApproved (phase 4)
ParecoxibApproved (phase 4)
PenicillamineApproved (phase 4)
PhenylbutazoneApproved (phase 4)
PiroxicamApproved (phase 4)
PirprofenApproved (phase 4)
RofecoxibApproved (phase 4)
SulindacApproved (phase 4)
SuprofenApproved (phase 4)
Tiaprofenic AcidApproved (phase 4)
TolmetinApproved (phase 4)
ValdecoxibApproved (phase 4)
ZomepiracApproved (phase 4)
BucillaminePhase 3 (in late-stage trials)
Chondroitin Sulfate SodiumPhase 3 (in late-stage trials)
NaproxcinodPhase 3 (in late-stage trials)
PelubiprofenPhase 3 (in late-stage trials)
PolmacoxibPhase 3 (in late-stage trials)

Clinical trials & evidence

Clinical trials

Clinical trials: 172.

Phase distribution (across all retrieved trials)

PhaseTrials
Not specified143
PHASE29
PHASE46
PHASE34
PHASE1/PHASE24
PHASE14
EARLY_PHASE12

Top trials by phase / activity

NCTPhaseStatusTitle
NCT05543642PHASE4ACTIVE_NOT_RECRUITINGThe COVID-19 VaccinE Response and Co-Administration in Rheumatology Patients (COVER-CoAd)
NCT00377364PHASE4COMPLETEDAcetaminophen (Tylenol) for Mood and Memory Changes Associated With Corticosteroid Therapy
NCT01022905PHASE4COMPLETEDVaccine Responses to Influenza A H1N1/09 Immunization in High-risk Patients
NCT03492658PHASE4COMPLETEDAbatacept to Silence Anti-citrullinated Protein Antibody-expressing B Cells in Rheumatoid Arthritis (ASCARA)
NCT03558971PHASE4COMPLETEDPatient Self-administration of Cortisol for Cortisol-responding Disorders in Men and Women Over the Age of 17
NCT04754698PHASE4COMPLETEDCOVID-19 CoronaVac in Patients With Autoimmune Rheumatic Diseases and HIV/AIDS
NCT02111564PHASE3COMPLETEDA Study of Rivaroxaban (JNJ-39039039) on the Venous Thromboembolic Risk in Post-Hospital Discharge Patients
NCT02436096PHASE3COMPLETEDA Study to Evaluate eFFIcacy and Safety of Sublingual TNX-102 SL Tablet Taken at Bedtime in Patients With fibRoMyalgia
NCT02829814PHASE3TERMINATEDRepeat of: A Study to Evaluate Efficacy and Safety of Sublingual TNX-102 SL Tablet Taken at Bedtime in Patients With Fibromyalgia
NCT04806113PHASE3COMPLETEDCOVID-19 Vaccine in Immunosuppressed Adults With Autoimmune Diseases
NCT07078357PHASE1/PHASE2NOT_YET_RECRUITINGClinical Trial Phase I/IIa to Evaluate the Safety and Immunogenicity of StreptInCor
NCT07138898PHASE2NOT_YET_RECRUITINGImmunosuppressant Management in Rheumatology Patients Undergoing Elective Total Shoulder Arthroplasty
NCT07148414PHASE2RECRUITINGA Study of SPY072 in Rheumatic Disease
NCT00000407PHASE2COMPLETEDImproving Vocational Outcomes in Arthritis
NCT00244153PHASE1/PHASE2UNKNOWNIntraarticular Opioids Vs Glucocorticosteroids in Gonarthritis
NCT00372177PHASE1/PHASE2COMPLETEDThe Use of Anti-CD4 Monoclonal Antibody (mAb)-Fragment for the Imaging of Chronic Inflammation in Patients With Active Rheumatoid Arthritis
NCT01006681PHASE2UNKNOWNVaccination Against Influenza H1N1 in Rheumatic Diseases
NCT01227694PHASE1/PHASE2COMPLETEDAdult Stem Cell Therapy for Repairing Articular Cartilage in Gonarthrosis
NCT01685372PHASE2COMPLETEDImmunogenicity of Fluzone High Dose in Immunocompromised Children and Young Adults
NCT02944448PHASE2COMPLETEDA Study Evaluating Pain Relief and Safety of Orally Administered CR845 in Patients With Osteoarthritis of Hip or Knee
NCT03277703PHASE2COMPLETEDFlu Vaccine Response in Patients on Biologic Therapies
NCT05516758PHASE2TERMINATEDA Study of Peresolimab (LY3462817) in Participants With Moderately-to-Severely Active Rheumatoid Arthritis
NCT05618782PHASE2COMPLETEDClinical Trial to Evaluate the Efficacy and Safety of LEVI-04 in Patients With Osteoarthritis of the Knee
NCT00946790PHASE1COMPLETEDTo Demonstrate the Relative Bioavailability of Hydroxychloroquine Sulfate, 200 mg Tablets
NCT02291471PHASE1COMPLETEDTolerance and Pharmacokinetics of T0001 in Healthy Adult Chinese Volunteers
NCT03337165PHASE1COMPLETEDAutologous Tolerogenic Dendritic Cells for Treatment of Patients With Rheumatoid Arthritis
NCT04205851PHASE1COMPLETEDPhase 1 Study With KIN-1901 in Healthy Subjects and Subjects With Ankylosing Spondylitis
NCT07490041EARLY_PHASE1RECRUITINGExploratory Clinical Study on the Safety and Efficacy of Anti- CD19/BCMA CAR-NK Cell Injection for the Treatment of Refractory Pediatric Rheumatic Diseases
NCT02484053EARLY_PHASE1COMPLETEDRapid Infusion Rituximab, Hematologic, Oncologic, and Rheumatologic Disorders
NCT00024479Not specifiedRECRUITINGStudies of the Natural History of Rheumatic Diseases
NCT02504879Not specifiedRECRUITINGNatural History, Pathogenesis and Outcome of Melorheostosis A Rare Osteosclerotic Disease
NCT03813862Not specifiedRECRUITINGObservational Pharmaco-Epidemiology Research & Analysis
NCT04037735Not specifiedRECRUITINGRSA-RCT: Attune S+ TKA Versus Sigma TKA
NCT04244968Not specifiedACTIVE_NOT_RECRUITINGSatisfaction, QoL,Health Status & Clinic Outcomes for Patients Attending MSK Triage Clinics in Rheumatology
NCT04402086Not specifiedRECRUITINGRheumatology Patient Registry and Biorepository
NCT04817072Not specifiedRECRUITINGEvaluation of Mood Disorders Under Biologics in Chronic Inflammatory Rheumatic Disease
NCT04890483Not specifiedRECRUITINGtDCS in Post-Acute COVID-19 Patients With SARDs
NCT05007340Not specifiedRECRUITINGILD-SARDs Registry and Biorepository
NCT05443321Not specifiedENROLLING_BY_INVITATIONAdvancing Health Information Exchange (HIE) During Inter-hospital Transfer (IHT) to Improve Patient Outcomes
NCT05786235Not specifiedRECRUITINGPatients Pregnant Women With or Without Primary Antiphospholipid Antibody Syndrome

Drugs tested across these trials (top 30)

MoleculeMax phaseTrials referencing
ABATACEPT42
AZATHIOPRINE41
BELIMUMAB41
BIMEKIZUMAB41
CANAKINUMAB41
GOLIMUMAB41
GUSELKUMAB41
HYDROCORTISONE41
IXEKIZUMAB41
LEFLUNOMIDE41
MYCOPHENOLIC ACID41
RISANKIZUMAB41
RIVAROXABAN41
SULFASALAZINE41
TOFACITINIB41
UPADACITINIB41
CERTOLIZUMAB31
PERESOLIMAB21
CHEMBL478396601