Rheumatoid factor-positive polyarticular juvenile idiopathic arthritis

disease
On this page

Also known as juvenile idiopathic rheumatoid factor-positive polyarthritispolyarthritis with rheumatoid factorpolyarticular JIA, RF+polyarticular juvenile idiopathic arthritis, RF+polyarticular juvenile idiopathic arthritis, rheumatoid Factor Positiverheumatoid factor-positive polyarticular JIA

Summary

Rheumatoid factor-positive polyarticular juvenile idiopathic arthritis (MONDO:0019435) is a disease. A subtype of polyarticular juvenile idiopathic arthritis — broader associated-gene and molecular evidence is on the parent page (see Disease family below).

At a glance

  • Prevalence: 1-9 / 100 000 (Europe)
  • Phenotypes (HPO): 19

Clinical features

Epidemiology

Prevalence records

1 prevalence record(s), Orphanet:

TypeClassValueGeographyValidation
Point prevalence1-9 / 100 0004.2EuropeNot yet validated

Signs & symptoms

Clinical features (HPO)

19 HPO clinical features (Orphanet curated; top 19 by frequency):

HPO IDTermFrequency
HP:0001369ArthritisVery frequent (80-99%)
HP:0002829ArthralgiaVery frequent (80-99%)
HP:0002923Rheumatoid factor positiveVery frequent (80-99%)
HP:0005764Polyarticular arthritisVery frequent (80-99%)
HP:0011117Abnormal circulating interleukin concentrationFrequent (30-79%)
HP:0001376Limitation of joint mobilityFrequent (30-79%)
HP:0001386Joint swellingFrequent (30-79%)
HP:0002813Abnormality of limb bone morphologyFrequent (30-79%)
HP:0003565Elevated erythrocyte sedimentation rateFrequent (30-79%)
HP:0005187Progressive joint destructionFrequent (30-79%)
HP:0005930Abnormality of epiphysis morphologyFrequent (30-79%)
HP:0006252Interphalangeal joint erosionsFrequent (30-79%)
HP:0011227Elevated circulating C-reactive protein concentrationFrequent (30-79%)
HP:0040311Symetrical distal arthritisFrequent (30-79%)
HP:0100769SynovitisFrequent (30-79%)
HP:0000938OsteopeniaOccasional (5-29%)
HP:0004349Reduced bone mineral densityOccasional (5-29%)
HP:0010588Premature epimetaphyseal fusionOccasional (5-29%)
HP:0100555Asymmetric growthOccasional (5-29%)

Identifiers

Disease identifiers

FieldValue
Canonical namerheumatoid factor-positive polyarticular juvenile idiopathic arthritis
Mondo IDMONDO:0019435
EFOEFO:0009731
Orphanet85435
NCITC119034
UMLSC3890733
MedGen855737
GARD0019064
Is cancer (heuristic)no

Also known as: juvenile idiopathic rheumatoid factor-positive polyarthritis · polyarthritis with rheumatoid factor · polyarticular JIA, RF+ · polyarticular juvenile idiopathic arthritis, RF+ · polyarticular juvenile idiopathic arthritis, rheumatoid Factor Positive · rheumatoid factor-positive polyarticular JIA

Disease family

This is a subtype of polyarticular juvenile idiopathic arthritis. Genetic, therapeutic, and trial evidence is largely curated at the broader-term level — see the parent page for the associated-gene cohort and molecular evidence.

Classification path: disease › human disease › disease by body system or component › connective tissue disorderrheumatic disorderjuvenile idiopathic arthritispolyarticular juvenile idiopathic arthritisrheumatoid factor-positive polyarticular juvenile idiopathic arthritis

Related subtypes (1): rheumatoid factor-negative juvenile idiopathic arthritis

Genetics & variants

GWAS landscape

No GWAS associations recorded — common-variant (GWAS) studies don’t cover this disease (typical for Mendelian / rare diseases). See the curated gene cohort and Mendelian overlap below.

Variant details and genetic-evidence tiers

No tiered GWAS variants or ClinVar records for this disease.

Genes & proteins

No associated-gene cohort resolved for this disease. Atlas builds the molecular and therapeutic sections — associated genes, protein families, druggability, pathways, interactions, and drug associations — by aggregating over a disease’s associated genes (resolved via GWAS / GenCC / ClinVar / CIViC), and none resolved here. This is expected for antibody-mediated, autoimmune, or otherwise non-gene-defined conditions; the curated evidence for this disease is its clinical features, GWAS susceptibility, and clinical trials (above).

Function

No pathway enrichment — requires an associated-gene cohort.

Therapeutics

No druggable-target or therapeutic data for this disease’s cohort.

Clinical trials & evidence

Clinical trials

Clinical trials: 0.

No linked Atlas pages yet — the cross-entity mesh grows as the corpus expands.