Skin sensitivity to sun

disease
On this page

Summary

Skin sensitivity to sun (MONDO:0005434) is a disease with 8 cohort genes (85 GWAS associations across 13 studies).

At a glance

  • Cohort genes: 8
  • GWAS associations: 85
  • ClinVar variants: 3

Clinical features

No curated clinical features (Orphanet) for this disease.

Identifiers

Disease identifiers

FieldValue
Canonical nameskin sensitivity to sun
Mondo IDMONDO:0005434
EFOEFO:0004795
UMLSC0349506
MedGen87601
Is cancer (heuristic)no

Data availability: 3 ClinVar variants · 85 GWAS associations (13 studies).

Disease family

Classification path: disease › human disease › disease by body system or component › integumentary system disorder › skin disorderdermatitisradiodermatitisphotosensitivity diseaseskin sensitivity to sun

Related subtypes (3): photoallergic dermatitis, phototoxic dermatitis, polymorphic light eruption

Genetics & variants

GWAS landscape

85 GWAS associations across 13 studies. Top hits map to 11 distinct genes (as reported by GWAS).

Top associations by p-value

rsIDp-valueGeneRisk alleleOdds ratio
chr15:279851011e-192T2.3
chr16:899193422e-163CA2.72
rs168919821e-58SLC45A2C0.58
rs18050072e-55MC1RT2.94
chr16:900403617e-50G2.01
chr16:891541481e-42T1.59
rs354126e-36SLC45A2C0.54
chr16:895467371e-28T1.39
rs49114142e-24RPS2P1 - ASIP; RPS2P1 - ASIPG1.76
chr16:896694835e-23CTG0.64
rs77132796e-23ADAMTS12 - RXFP3G0.3
rs129312678e-23FANCAG0.44
rs354062e-22SLC45A2G0.5
rs122035928e-20IRF4T0.23
chr16:139342246e-19T1.34
rs131777871e-18ADAMTS12 - RXFP3T0.34
rs100800405e-18SLC45A2T0.61
rs117424675e-17ADAMTS12 - RXFP3G0.27
rs19462672e-16ADAMTS12 - RXFP3A0.18
rs22780079e-16SLC45A2G0.45
rs73805381e-15SLC45A2A0.38
chr16:897757682e-14G0.61
rs129138324e-14HERC2G0.2
rs18339232e-13ADAMTS12 - RXFP3A0.19
chr15:278711704e-13A3.42
rs11840301884e-13SLC45A2C0.53
chr11:891781955e-13T2.88
rs64510471e-12SLC45A2T0.82
rs23313432e-12ADAMTS12 - RXFP3G0.36
rs25917193e-12ADAMTS12A0.34

Top studies (by case count)

StudyLead authorYearCasesControlsTitle
GCST90077603Backman JD2021173,164249,406Exome sequencing and analysis of 454,787 UK Biobank participants.
GCST90081589Backman JD2021173,164249,406Exome sequencing and analysis of 454,787 UK Biobank participants.
GCST90077604Backman JD202193,163329,407Exome sequencing and analysis of 454,787 UK Biobank participants.
GCST90081590Backman JD202193,163329,407Exome sequencing and analysis of 454,787 UK Biobank participants.
GCST90077602Backman JD202189,584332,986Exome sequencing and analysis of 454,787 UK Biobank participants.
GCST90081588Backman JD202189,584332,986Exome sequencing and analysis of 454,787 UK Biobank participants.
GCST90077605Backman JD202175,919346,651Exome sequencing and analysis of 454,787 UK Biobank participants.
GCST90081591Backman JD202175,919346,651Exome sequencing and analysis of 454,787 UK Biobank participants.
GCST90255686Farre X202300Skin Phototype and Disease: A Comprehensive Genetic Approach to Pigmentary Traits Pleiotropy Using PRS in the GCAT Cohort.
GCST90255687Farre X202300Skin Phototype and Disease: A Comprehensive Genetic Approach to Pigmentary Traits Pleiotropy Using PRS in the GCAT Cohort.

Variant details and genetic-evidence tiers

Tier distribution (top 50 variants)

TierVariants
Tier 1: coding3
Tier 2: splice/UTR4
Tier 3: regulatory1
Tier 4: intronic/intergenic42

MAF distribution

BucketVariants
common (>=0.05)28
low_freq (0.01-0.05)11
rare (<0.01)9
unknown2

Functional consequences

ConsequenceCount
intron_variant18
unknown12
intergenic_variant11
3_prime_UTR_variant4
missense_variant3
intergenic_variant; intergenic_variant1
regulatory_region_variant1

Top variants

rsIDChrPosAllelesMAFConsequenceGenep-valueTier
chr15:279851010.0091e-192Tier 4: intronic/intergenic
chr16:899193420.0052e-163Tier 4: intronic/intergenic
rs16891982533951588C>A,G0.15missense_variantSLC45A21e-58Tier 1: coding
rs18050071689919709C>A,G,T0.06missense_variantMC1R2e-55Tier 1: coding
chr16:900403610.0037e-50Tier 4: intronic/intergenic
chr16:891541480.0061e-42Tier 4: intronic/intergenic
rs35412533967040C>G,T0.103intron_variantSLC45A26e-36Tier 4: intronic/intergenic
chr16:895467370.0081e-28Tier 4: intronic/intergenic
rs491141420;2034141638T>A,G0.08intergenic_variant; intergenic_variantRPS2P1 - ASIP; RPS2P1 - ASIP2e-24Tier 4: intronic/intergenic
chr16:896694830.0055e-23Tier 4: intronic/intergenic
rs7713279533928797T>A,G0.228intergenic_variantADAMTS12 - RXFP36e-23Tier 4: intronic/intergenic
rs129312671689752324C>G0.091intron_variantFANCA8e-23Tier 4: intronic/intergenic
rs35406533946038A>C,G,T0.0683_prime_UTR_variantSLC45A22e-22Tier 2: splice/UTR
rs122035926396321C>G,T0.141intron_variantIRF48e-20Tier 4: intronic/intergenic
chr16:139342240.0076e-19Tier 4: intronic/intergenic
rs13177787533926949T>A,C0.129intergenic_variantADAMTS12 - RXFP31e-18Tier 4: intronic/intergenic
rs10080040533950346T>A0.034intron_variantSLC45A25e-18Tier 4: intronic/intergenic
rs11742467533899585G>A0.195intergenic_variantADAMTS12 - RXFP35e-17Tier 4: intronic/intergenic
rs1946267533921705A>G,T0.197intergenic_variantADAMTS12 - RXFP32e-16Tier 4: intronic/intergenic
rs2278007533951446A>C,G0.0253_prime_UTR_variantSLC45A29e-16Tier 2: splice/UTR
rs7380538533946450A>G0.0343_prime_UTR_variantSLC45A21e-15Tier 2: splice/UTR
chr16:897757680.0032e-14Tier 4: intronic/intergenic
rs129138321528120472A>C,G0.358intron_variantHERC24e-14Tier 4: intronic/intergenic
rs1833923533903329C>A0.476intergenic_variantADAMTS12 - RXFP32e-13Tier 4: intronic/intergenic
chr15:278711704e-13Tier 4: intronic/intergenic
rs11840301885339664280.04intron_variantSLC45A24e-13Tier 4: intronic/intergenic
chr11:891781955e-13Tier 4: intronic/intergenic
rs6451047533956911T>A,C,G0.015intron_variantSLC45A21e-12Tier 4: intronic/intergenic
rs2331343533921589T>C,G0.07intergenic_variantADAMTS12 - RXFP32e-12Tier 4: intronic/intergenic
rs2591719533835538G>A,C,T0.081intron_variantADAMTS123e-12Tier 4: intronic/intergenic

ClinVar germline variants

3 retrieved; paginated sample, class counts are floors:

1 conflicting classifications of pathogenicity; other; risk factor, 1 conflicting classifications of pathogenicity, 1 pathogenic

ClinVarVariant (HGVS)GeneClassificationReview
981245NM_001983.4(ERCC1):c.321+61_525+132delERCC1Pathogenicno assertion criteria provided
978472NM_001983.4(ERCC1):c.466C>T (p.Arg156Trp)ERCC1Conflicting classifications of pathogenicitycriteria provided, conflicting classifications
9NM_000410.4(HFE):c.845G>A (p.Cys282Tyr)HFEConflicting classifications of pathogenicity; other; risk factorcriteria provided, conflicting classifications

Genes & proteins

Mendelian disease overlap and somatic drivers

GenCC: 0 · Orphanet: 16 · OMIM-shared: 0 · Dual-evidence (GWAS+Mendelian): 0

Orphanet rare-disease linkage (cohort genes)

GeneOrphanet IDRare disease
TYROrphanet:352734Minimal pigment oculocutaneous albinism type 1
TYROrphanet:352737Temperature-sensitive oculocutaneous albinism type 1
TYROrphanet:79431Oculocutaneous albinism type 1A
TYROrphanet:79434Oculocutaneous albinism type 1B
TYROrphanet:895Waardenburg syndrome type 2
SLC45A2Orphanet:79435Oculocutaneous albinism type 4
ERCC1Orphanet:1466COFS syndrome
ERCC1Orphanet:90322Cockayne syndrome type 2
HERC2Orphanet:329195Developmental delay with autism spectrum disorder and gait instability
HFEOrphanet:443057Sporadic porphyria cutanea tarda
HFEOrphanet:443062Familial porphyria cutanea tarda
HFEOrphanet:465508Symptomatic form of HFE-related hemochromatosis
HFEOrphanet:586Cystic fibrosis
HFEOrphanet:648581Digenic hemochromatosis
MC1ROrphanet:618Familial melanoma
MC1ROrphanet:79432Oculocutaneous albinism type 2

Cohort genes → proteins

8 cohort genes, 8 distinct canonical proteins.

Evidence partition

SubsetGenes
gwas_only6
multi_evidence2

Cohort genes (full)

SymbolHGNCEnsemblUniProtNameEvidence
TYRHGNC:12442ENSG00000077498P14679Tyrosinasegwas
RALYHGNC:15921ENSG00000125970Q9UKM9RNA-binding protein Ralygwas
SLC45A2HGNC:16472ENSG00000164175Q9UMX9Membrane-associated transporter proteingwas
ERCC1HGNC:3433ENSG00000012061P07992DNA excision repair protein ERCC-1clinvar
HERC2HGNC:4868ENSG00000128731O95714E3 ubiquitin-protein ligase HERC2gwas
HFEHGNC:4886ENSG00000010704Q30201Hereditary hemochromatosis proteinclinvar
MC1RHGNC:6929ENSG00000258839Q01726Melanocyte-stimulating hormone receptorgwas
ASIPHGNC:745ENSG00000101440P42127Agouti-signaling proteingwas

Cohort function summary

Lead sentence per gene, UniProt-curated.

SymbolProtein nameFunction (lead sentence)
TYRTyrosinaseThis is a copper-containing oxidase that functions in the formation of pigments such as melanins and other polyphenolic compounds.
RALYRNA-binding protein RalyRNA-binding protein that acts as a transcriptional cofactor for cholesterol biosynthetic genes in the liver.
SLC45A2Membrane-associated transporter proteinProton-associated glucose and sucrose transporter.
ERCC1DNA excision repair protein ERCC-1Non-catalytic component of a structure-specific DNA repair endonuclease responsible for the 5’-incision during DNA repair.
HERC2E3 ubiquitin-protein ligase HERC2E3 ubiquitin-protein ligase that regulates ubiquitin-dependent retention of repair proteins on damaged chromosomes.
HFEHereditary hemochromatosis proteinBinds to transferrin receptor (TFR) and reduces its affinity for iron-loaded transferrin.
MC1RMelanocyte-stimulating hormone receptorG protein-coupled receptor that binds melanocyte-stimulating hormones (alpha, beta, and gamma-MSH) and adrenocorticotropic hormone/ACTH, which are peptide products of the POMC precursor protein.
ASIPAgouti-signaling proteinSignaling protein that functions as an antagonist of melanocyte-stimulating-hormone receptor MC1R, thereby playing a role in the regulation of melanogenesis.

Protein-family classification

Druggable: 4 · Difficult: 1 · Unknown: 3 · Druggable fraction: 0.5

Family distribution

Cohort families vs a genome-wide background (hypergeometric, BH-FDR; fold = observed/expected). Counts kept; sorted by enrichment, so the catch-all Other/Unknown bucket no longer leads.

FamilyGenesFoldFDR
Transporter19.7×0.578
Antibody/Immunoglobulin13.6×0.578
GPCR13.0×0.578
Enzyme (other)11.5×0.753
Transcription factor11.0×0.773
Other/Unknown30.7×0.919

Per-gene assignment

SymbolFamilyDruggable?ECInterPro (top 3)
TYREnzyme (other)yes1.14.18.1Tyrosinase_Cu-bd, Di-copper_centre_dom_sf, Tyrosinase/Hemocyanin
RALYOther/UnknownnoRRM_dom, Nucleotide-bd_a/b_plait_sf, hnRNP_C
SLC45A2TransporteryesMFS, MFS_trans_sf
ERCC1Other/UnknownnoERCC1/RAD10/SWI10, RuvA_2-like, Restrct_endonuc-II-like
HERC2Transcription factornoReg_chr_condens, Znf_ZZ, HECT_dom
HFEAntibody/ImmunoglobulinyesMHC_I_a_a1/a2, Ig/MHC_CS, Ig_C1-set
MC1RGPCRyesGPCR_Rhodpsn, MSH_rcpt, Melcrt_ACTH_rcpt
ASIPOther/UnknownnoAgouti, Agouti_dom, Agouti_dom_sf

Expression context

Cohort genes with no expression data: 0.

6 cohort genes are a single-cell marker in ≥1 SCXA experiment.

Breadth distribution (Bgee present_calls)

BucketGenes
narrow (1-5 tissues)0
moderate (6-20)0
broad (>20)8
unknown0

Top tissues across cohort

TissueCohort genes
male germ line stem cell (sensu Vertebrata) in testis2
pigmented layer of retina2
granulocyte2
apex of heart2
upper leg skin1
ganglionic eminence1
ventricular zone1
primordial germ cell in gonad1
parotid gland1
right atrium auricular region1
cerebellar cortex1
right hemisphere of cerebellum1
sural nerve1
olfactory bulb1
stromal cell of endometrium1
type B pancreatic cell1
left testis1
right uterine tube1
left ovary1
right ovary1

Per-gene tissue summary (top 30)

SymbolBgee breadthFANTOM5 breadthSCXATop tissues
TYR59tissue_specificmarkerpigmented layer of retina, male germ line stem cell (sensu Vertebrata) in testis, upper leg skin
RALY294ubiquitousmarkerganglionic eminence, granulocyte, ventricular zone
SLC45A2100tissue_specificmarkermale germ line stem cell (sensu Vertebrata) in testis, pigmented layer of retina, primordial germ cell in gonad
ERCC1285ubiquitousmarkerapex of heart, parotid gland, right atrium auricular region
HERC2146markersural nerve, right hemisphere of cerebellum, cerebellar cortex
HFE238ubiquitousmarkertype B pancreatic cell, olfactory bulb, stromal cell of endometrium
MC1R180broadyesgranulocyte, right uterine tube, left testis
ASIP158tissue_specificyesapex of heart, left ovary, right ovary

Protein interactions among cohort

Intra-cohort edges: 8.

Hub genes (top 10 by interactor count)

SymbolInteractor count
TYR3,663
RALY3,651
HERC22,843
ERCC12,085
HFE1,569
SLC45A21,295
MC1R1,169
ASIP473

Intra-cohort edges

ABSources
ASIPMC1Rstring_interaction
ASIPRALYstring_interaction
ASIPSLC45A2string_interaction
ASIPTYRstring_interaction
MC1RRALYstring_interaction
MC1RSLC45A2string_interaction
MC1RTYRstring_interaction
SLC45A2TYRstring_interaction

Structural data

PDB: 7 · AlphaFold-only: 1 · No structure: 0

Cohort genes with PDB structures (top 30)

SymbolUniProtPDB entries
HERC2O9571415
ERCC1P0799214
MC1RQ017265
ASIPP421274
HFEQ302012
TYRP146791
RALYQ9UKM91

AlphaFold-only cohort genes (top 30 by pLDDT)

SymbolUniProtpLDDT
SLC45A2Q9UMX977.96

Function

Pathway analysis

Distinct Reactome pathways touched by cohort: 26. Enrichment computed across 8 evidence-associated genes (6 with Reactome annotation).

Pathways by enrichment

Over-representation of cohort genes vs the genome-wide background (hypergeometric test, Benjamini-Hochberg FDR; fold = observed/expected over 6 annotated cohort genes). Counts and members are kept as ground-truth; sorted by enrichment.

PathwayCohort genesFoldFDRSample cohort genes
Melanin biosynthesis2761.3×6e-05TYR, SLC45A2
Transferrin endocytosis and recycling161.4×0.087HFE
HDR through Single Strand Annealing (SSA)148.8×0.087ERCC1
Fanconi Anemia Pathway146.4×0.087ERCC1
Regulation of MITF-M-dependent genes involved in pigmentation144.3×0.087TYR
Dual Incision in GG-NER143.3×0.087ERCC1
Formation of Incision Complex in GG-NER142.3×0.087ERCC1
Transcriptional and post-translational regulation of MITF-M expression and activity129.7×0.087MC1R
Dual incision in TC-NER128.8×0.087ERCC1
Nonhomologous End-Joining (NHEJ)128.0×0.087HERC2
SUMOylation of DNA damage response and repair proteins124.4×0.087HERC2
Recruitment and ATM-mediated phosphorylation of repair and signaling proteins at DNA double strand breaks124.4×0.087HERC2
G2/M DNA damage checkpoint120.0×0.089HERC2
Processing of DNA double-strand break ends119.0×0.089HERC2
MITF-M-regulated melanocyte development119.0×0.089MC1R
Class A/1 (Rhodopsin-like receptors)112.4×0.114MC1R
Peptide ligand-binding receptors112.4×0.114MC1R
G alpha (s) signalling events112.2×0.114MC1R
Metabolism of amino acids and derivatives111.3×0.117SLC45A2
GPCR ligand binding110.7×0.117MC1R
GPCR downstream signalling17.2×0.162MC1R
Signaling by GPCR16.7×0.166MC1R
Antigen processing: Ubiquitination & Proteasome degradation16.2×0.171HERC2
Developmental Biology12.4×0.379MC1R
Metabolism11.9×0.434SLC45A2
Signal Transduction11.7×0.463MC1R

GO biological processes by enrichment

Over-representation of cohort genes vs the genome-wide background (hypergeometric test, Benjamini-Hochberg FDR; fold = observed/expected over 8 annotated cohort genes). Counts and members are kept as ground-truth; sorted by enrichment.

GO termCohort genesFoldFDRSample cohort genes
melanin biosynthetic process3486.1×2e-06TYR, MC1R, ASIP
melanin biosynthetic process from tyrosine21053.2×6e-05TYR, SLC45A2
positive regulation of melanin biosynthetic process2351.1×3e-04MC1R, ASIP
UV-damage excision repair2324.1×3e-04ERCC1, MC1R
UV protection2300.9×3e-04ERCC1, MC1R
pigmentation2175.5×8e-04TYR, MC1R
negative regulation of antigen processing and presentation of endogenous peptide antigen via MHC class I12106.5×0.006HFE
eye pigment biosynthetic process11053.2×0.010TYR
regulation of iron ion transport11053.2×0.010HFE
sucrose transport1702.2×0.010SLC45A2
response to iron ion starvation1702.2×0.010HFE
pyrimidine dimer repair by nucleotide-excision repair1526.6×0.010ERCC1
obsolete syncytium formation1526.6×0.010ERCC1
telomeric DNA-containing double minutes formation1526.6×0.010ERCC1
positive regulation of t-circle formation1526.6×0.010ERCC1
negative regulation of protection from non-homologous end joining at telomere1526.6×0.010ERCC1
negative regulation of CD8-positive, alpha-beta T cell activation1526.6×0.010HFE
response to blue light1421.3×0.012TYR
lysosomal lumen pH elevation1421.3×0.012SLC45A2
mitotic recombination1351.1×0.012ERCC1
negative regulation of telomere maintenance1351.1×0.012ERCC1
post-embryonic hemopoiesis1351.1×0.012ERCC1
negative regulation of T cell cytokine production1300.9×0.012HFE
negative regulation of melanin biosynthetic process1300.9×0.012ASIP
cellular response to iron ion1300.9×0.012HFE
positive regulation of feeding behavior1300.9×0.012MC1R
cell population proliferation225.7×0.012TYR, ERCC1
developmental pigmentation1263.3×0.013SLC45A2
epigenetic programming in the zygotic pronuclei1234.1×0.013ASIP
visual perception219.9×0.013TYR, SLC45A2

Therapeutics

Drug target analysis

Approved (phase 4): 2 · Phase ≥3: 2 · Phased (≥1): 2 · Undrugged: 6

Druggability breadth: 3 of 8 evidence-associated genes (38%) have a ChEMBL target (buckets above are over the deeply-mined display cohort).

Genes with an approved drug

The molecule shown is one approved compound that hits the gene — not necessarily a drug of choice or one indicated for this disease.

SymbolExample approved molecule
TYRASCORBIC ACID
MC1RBREMELANOTIDE

Top cohort targets by molecule count

SymbolMoleculesMax phase
TYR104
MC1R64
RALY00
SLC45A200
ERCC100
HERC200
HFE00
ASIP00

Drugs targeting cohort genes (top 30)

MoleculeMax phaseTargets in cohort
ASCORBIC ACID4TYR
HEXYLRESORCINOL4TYR
HYDROQUINONE4TYR
BREMELANOTIDE4MC1R
SETMELANOTIDE4MC1R
AFAMELANOTIDE4MC1R
CURCUMIN3TYR
RESVERATROL3TYR
QUERCETIN3TYR
BUTYLATED HYDROXYTOLUENE2TYR
LUTEOLIN2TYR
ARBUTIN2TYR
INTERMEDINE2MC1R
PL-81772MC1R
KAEMPFEROL1TYR
DERSIMELAGON PHOSPHATE1MC1R

Bioactivity and enzyme data

Enzyme cohort genes (≥1 EC): 1.

Cohort genes with ChEMBL bioactivity (full, sorted by assay count)

SymbolAssaysType breakdown
MC1R319Functional:164, Binding:155
TYR211Binding:209, ADMET:2
ERCC128Binding:28

Cohort enzymes (BRENDA EC)

SymbolEC numbersNames
TYR1.14.18.1tyrosinase

Cohort genes with high screening signal

≥100 ChEMBL assays — a studied-ness signal; see Therapeutics for approved-drug status.

SymbolChEMBL assays
TYR211
MC1R319

Pharmacogenomics

Cohort genes with a PharmGKB record: 8; with CPIC/DPWG dosing guidelines: 0.

No cohort gene has a CPIC/DPWG genotype-guided dosing guideline (PharmGKB).

Chemical tractability of cohort targets

16 approved/phased compounds have measured bioactivity against a cohort gene (and aren’t yet in disease-level trials). This is a research / tractability signal, NOT a therapeutic recommendation — a bioactivity row often reflects off-target or screening binding (e.g. promiscuous kinase inhibitors against a cohort kinase), implying no disease mechanism.

CompoundMax phaseCohort target (bioactivity)
ASCORBIC ACID4TYR
HEXYLRESORCINOL4TYR
HYDROQUINONE4TYR
BREMELANOTIDE4MC1R
SETMELANOTIDE4MC1R
AFAMELANOTIDE4MC1R
CURCUMIN3TYR
RESVERATROL3TYR
QUERCETIN3TYR
BUTYLATED HYDROXYTOLUENE2TYR
LUTEOLIN2TYR
ARBUTIN2TYR
INTERMEDINE2MC1R
PL-81772MC1R
KAEMPFEROL1TYR
DERSIMELAGON PHOSPHATE1MC1R

Druggability pyramid

Cohort genes binned by druggability tier (high → low):

TierDefinitionGenesSymbols
AApproved (phase 4 drug)2TYR, MC1R
BPhased (≥1) drug, not yet approved0
CDruggable family + PDB, no drug1HFE
DDruggable family + AlphaFold only, no drug1SLC45A2
EDifficult family or no structure, no drug4RALY, ERCC1, HERC2, ASIP

Undrugged target profiles

6 cohort genes are undrugged. Ranked by ‘starting-point quality’ (assay depth + drugged-partner adjacency).

SymbolChEMBL assaysDrugged partners (top 3)
RALY0MC1R
SLC45A20TYR, MC1R
ASIP0MC1R
ERCC128
HERC20
HFE0

Clinical trials & evidence

Clinical trials

Clinical trials: 0.