Squamous cell carcinoma of penis

disease
On this page

Also known as epidermoid carcinoma of penisepidermoid carcinoma of the penisepidermoid cell carcinoma of penisepidermoid cell carcinoma of the penispenile epidermoid carcinomapenile epidermoid cell carcinomapenile squamous car.(epidermoid)penile squamous carcinoma (epidermoid)penile squamous cell cancerpenile squamous cell carcinomapenis squamous cell carcinomaPSCCsquamous cell carcinoma of the penis

Summary

Squamous cell carcinoma of penis (MONDO:0018352) is a cancer (an umbrella term covering 5 Mondo subtypes) and 19 clinical trials. Top therapeutic interventions include afatinib, enfortumab vedotin, and cabozantinib. A subtype of squamous cell carcinoma — broader associated-gene and molecular evidence is on the parent page (see Disease family below).

At a glance

  • Classification: Cancer
  • Prevalence: 1-9 / 1 000 000 (Europe) [Orphanet-validated]
  • Umbrella term: 5 Mondo subtypes
  • Clinical trials: 19

Clinical features

Epidemiology

Prevalence records

24 prevalence record(s), Orphanet, top 20 (validated / broadest geography first):

TypeClassValueGeographyValidation
Annual incidence1-9 / 1 000 0000.57EuropeValidated
Annual incidence1-9 / 1 000 0000.612NetherlandsValidated
Annual incidence1-9 / 1 000 0000.491AustriaValidated
Annual incidence1-9 / 1 000 0000.605BelgiumValidated
Annual incidence1-9 / 1 000 0000.516BulgariaValidated
Annual incidence1-9 / 1 000 0000.423CroatiaValidated
Annual incidence1-9 / 1 000 0000.684Czech RepublicValidated
Annual incidence1-9 / 1 000 0000.6EstoniaValidated
Annual incidence1-9 / 1 000 0000.426FinlandValidated
Annual incidence1-9 / 1 000 0000.638GermanyValidated
Annual incidence1-9 / 1 000 0000.682IcelandValidated
Annual incidence1-9 / 1 000 0000.475IrelandValidated
Annual incidence1-9 / 1 000 0000.606ItalyValidated
Annual incidence1-9 / 1 000 0000.552LatviaValidated
Annual incidence1-9 / 1 000 0000.517LithuaniaValidated
Annual incidence1-9 / 1 000 0000.628MaltaValidated
Annual incidence1-9 / 1 000 0000.744NorwayValidated
Annual incidence1-9 / 1 000 0000.396PolandValidated
Annual incidence1-9 / 1 000 0000.745PortugalValidated
Annual incidence1-9 / 1 000 0000.499SlovakiaValidated

Identifiers

Disease identifiers

FieldValue
Canonical namesquamous cell carcinoma of penis
Mondo IDMONDO:0018352
Orphanet398058
DOIDDOID:5518
ICD-11186592209
NCITC7729
SNOMED CT403468003
UMLSC0238348
MedGen116057
GARD0021639
Anatomy (UBERON)UBERON:0000989
Is cancer (heuristic)yes

Also known as: epidermoid carcinoma of penis · epidermoid carcinoma of the penis · epidermoid cell carcinoma of penis · epidermoid cell carcinoma of the penis · penile epidermoid carcinoma · penile epidermoid cell carcinoma · penile squamous car.(epidermoid) · penile squamous carcinoma (epidermoid) · penile squamous cell cancer · penile squamous cell carcinoma · penis squamous cell carcinoma · PSCC · squamous cell carcinoma of penis · squamous cell carcinoma of the penis

Data availability: 12 cell lines.

Disease family

This is a subtype of squamous cell carcinoma. Genetic, therapeutic, and trial evidence is largely curated at the broader-term level — see the parent page for the associated-gene cohort and molecular evidence.

Classification path: disease › human disease › disease by etiologic mechanism › cancer or benign tumorneoplastic disease or syndromeneoplasm › epithelial neoplasm › squamous cell neoplasm › squamous cell carcinomasquamous cell carcinoma of penis

Related subtypes (38): bone squamous cell carcinoma, prostate squamous cell carcinoma, trachea squamous cell carcinoma, scrotum squamous cell carcinoma, skin squamous cell carcinoma, bladder squamous cell carcinoma, urethra squamous cell carcinoma, papillary squamous carcinoma, basaloid squamous cell carcinoma, pseudoglandular squamous cell carcinoma, thymus squamous cell carcinoma, ovarian squamous cell carcinoma, renal pelvis squamous cell carcinoma, ureter squamous cell carcinoma, fallopian tube squamous cell carcinoma, squamous carcinoma in situ, keratinizing squamous cell carcinoma, squamous cell lung carcinoma, esophageal squamous cell carcinoma, squamous cell breast carcinoma, adenosquamous carcinoma, cervical squamous cell carcinoma, colorectal squamous cell carcinoma, endometrial squamous cell carcinoma, gallbladder squamous cell carcinoma, gastric squamous cell carcinoma, thyroid gland squamous cell carcinoma, vaginal squamous cell carcinoma, head and neck squamous cell carcinoma, squamous cell carcinoma of the corpus uteri, squamous cell carcinoma of the small intestine, squamous cell carcinoma of pancreas, squamous cell carcinoma of liver and intrahepatic biliary tract, human papillomavirus-related squamous cell carcinoma, sarcomatoid squamous cell carcinoma, vulvar squamous cell carcinoma, metastatic squamous cell carcinoma, pure squamous carcinoma of the urothelial tract

Subtypes (5): sarcomatoid penile squamous cell carcinoma, penis mixed squamous cell carcinoma, papillary carcinoma of the penis, penis carcinoma in situ, human papillomavirus-related penile squamous cell carcinoma

Genetics & variants

GWAS landscape

No GWAS associations recorded — common-variant (GWAS) studies don’t cover this disease (typical for Mendelian / rare diseases). See the curated gene cohort and Mendelian overlap below.

Variant details and genetic-evidence tiers

No tiered GWAS variants or ClinVar records for this disease.

Genes & proteins

No associated-gene cohort resolved for this disease. Atlas builds the molecular and therapeutic sections — associated genes, protein families, druggability, pathways, interactions, and drug associations — by aggregating over a disease’s associated genes (resolved via GWAS / GenCC / ClinVar / CIViC), and none resolved here. This is expected for antibody-mediated, autoimmune, or otherwise non-gene-defined conditions; the curated evidence for this disease is its clinical features, GWAS susceptibility, and clinical trials (above).

Function

No pathway enrichment — requires an associated-gene cohort.

Therapeutics

No druggable-target or therapeutic data for this disease’s cohort.

Clinical trials & evidence

Clinical trials

Clinical trials: 19.

Phase distribution (across all retrieved trials)

PhaseTrials
PHASE212
PHASE13
Not specified3
PHASE1/PHASE21

Top trials by phase / activity

NCTPhaseStatusTitle
NCT02834013PHASE2ACTIVE_NOT_RECRUITINGNivolumab and Ipilimumab in Treating Patients With Rare Tumors
NCT06104618PHASE2RECRUITINGEnfortumab Vedotin for the Treatment of Patients With Metastatic or Unresectable Squamous Cell Carcinoma of the Penis
NCT06161532PHASE2RECRUITINGSacituzumab Govitecan With or Without Atezolizumab Immunotherapy in Rare Genitourinary Tumors (SMART) Such as High Grade Neuroendocrine Carcinomas, Adenocarcinoma, and Squamous Cell Bladder/Urinary Tract Cancer, Renal Medullary Carcinoma and Penile C…
NCT06353906PHASE2RECRUITINGCarboplatin/Paclitaxel + Pembrolizumab for Locoregionally Advanced Penile Cancer
NCT07110038PHASE2RECRUITINGDEPECA-1 - A Phase II Study to Evaluate a First-line Systemic Therapy With Enfortumab Vedotin Plus Avelumab for Advanced and Metastatic Penile Carcinoma
NCT01807546PHASE2COMPLETEDOral Rigosertib for Squamous Cell Carcinoma
NCT02014831PHASE2WITHDRAWNEfficacy and Safety of Cetuximab in Metastatic Penile Carcinoma (PENILANE)
NCT02279576PHASE2TERMINATEDStudy With Pazopanib and Weekly Paclitaxel in Penile Carcinoma (PAZOPEN-SOGUG)
NCT02541903PHASE2TERMINATEDTrial Using Gilotrif for Advanced Penile Squamous Cell Carcinoma
NCT02837042PHASE2TERMINATEDTrial of Pembrolizumab for Advanced Penile Squamous Cell Carcinoma
NCT03221400PHASE1/PHASE2UNKNOWNPEN-866 in Patients With Advanced Solid Malignancies
NCT03774901PHASE2UNKNOWNMaintenance Avelumab Immunotherapy in Patients With Locally Advanced or Metastatic Squamous Cell Penile Carcinoma
NCT03943602PHASE2UNKNOWNCabozantinib in Patients With Advanced Penile Squamous Cell Carcinoma (PSCC) (CaboPen)
NCT02496208PHASE1ACTIVE_NOT_RECRUITINGCabozantinib S-malate and Nivolumab With or Without Ipilimumab in Treating Patients With Metastatic Genitourinary Tumors
NCT07217171PHASE1RECRUITINGA Study Evaluating the Safety, Efficacy, and Pharmacokinetics (PK) of EVOLVE104 in Participants With Advanced Urothelial and Squamous Cell Carcinomas
NCT03517488PHASE1COMPLETEDA Study of XmAb®20717 in Subjects With Selected Advanced Solid Tumors
NCT02104063Not specifiedCOMPLETEDCharacterising Metastatic Penile Cancer Using Molecular Imaging - Hybrid MRI-PET [MRI-PET]
NCT04996849Not specifiedTERMINATEDContemporary Characteristics of Penile Cancer
NCT06068998Not specifiedCOMPLETEDMolecular Characterization of Penile Cancers in Developing Countries

Drugs tested across these trials (top 30)

MoleculeMax phaseTrials referencing
AFATINIB42
ENFORTUMAB VEDOTIN42
CABOZANTINIB41
CETUXIMAB41
NIRAPARIB41
SACITUZUMAB GOVITECAN41
RIGOSERTIB32
VUDALIMAB21
PEN-86611
CHEMBL375220401
CHEMBL421550101
CHEMBL484972101
EXELIXIS01
FOLINIC ACID01