T-cell childhood lymphoblastic lymphoma

disease
On this page

Also known as childhood precursor T-lymphoblastic lymphomachildhood T lymphoblastic lymphomaT lymphoblastic lymphoma

Summary

T-cell childhood lymphoblastic lymphoma (MONDO:0000874) is a cancer and 10 clinical trials. Top therapeutic interventions include mercaptopurine anhydrous, nelarabine, and pegaspargase. A subtype of lymphoblastic lymphoma — broader associated-gene and molecular evidence is on the parent page (see Disease family below).

At a glance

  • Classification: Cancer
  • Clinical trials: 10

Clinical features

No curated clinical features (Orphanet) for this disease.

Identifiers

Disease identifiers

FieldValue
Canonical nameT-cell childhood lymphoblastic lymphoma
Mondo IDMONDO:0000874
DOIDDOID:0080148
NCITC7210
UMLSC1332998
MedGen232068
GARD0022836
Is cancer (heuristic)yes

Also known as: childhood precursor T-lymphoblastic lymphoma · childhood T lymphoblastic lymphoma · T lymphoblastic lymphoma

Data availability: 17 cell lines.

Disease family

This is a subtype of lymphoblastic lymphoma. Genetic, therapeutic, and trial evidence is largely curated at the broader-term level — see the parent page for the associated-gene cohort and molecular evidence.

Classification path: human disease › disease by etiologic mechanism › cancer or benign tumorneoplastic disease or syndromeneoplasmhematopoietic and lymphoid system neoplasmhematopoietic and lymphoid cell neoplasmlymphoid neoplasm › precursor lymphoblastic lymphoma/leukemia › lymphoblastic lymphomaT-cell childhood lymphoblastic lymphoma

Related subtypes (1): T-lymphoblastic lymphoma

Genetics & variants

GWAS landscape

No GWAS associations recorded — common-variant (GWAS) studies don’t cover this disease (typical for Mendelian / rare diseases). See the curated gene cohort and Mendelian overlap below.

Variant details and genetic-evidence tiers

No tiered GWAS variants or ClinVar records for this disease.

Genes & proteins

No associated-gene cohort resolved for this disease. Atlas builds the molecular and therapeutic sections — associated genes, protein families, druggability, pathways, interactions, and drug associations — by aggregating over a disease’s associated genes (resolved via GWAS / GenCC / ClinVar / CIViC), and none resolved here. This is expected for antibody-mediated, autoimmune, or otherwise non-gene-defined conditions; the curated evidence for this disease is its clinical features, GWAS susceptibility, and clinical trials (above).

Function

No pathway enrichment — requires an associated-gene cohort.

Therapeutics

No druggable-target or therapeutic data for this disease’s cohort.

Clinical trials & evidence

Clinical trials

Clinical trials: 10.

Phase distribution (across all retrieved trials)

PhaseTrials
PHASE24
PHASE1/PHASE22
PHASE31
PHASE2/PHASE31
EARLY_PHASE11
Not specified1

Top trials by phase / activity

NCTPhaseStatusTitle
NCT07072585PHASE2/PHASE3NOT_YET_RECRUITINGTesting the Addition of Daratumumab to Chemotherapy for Treating Patients With Newly-Diagnosed T-Cell Lymphoblastic Leukemia (T-ALL) and T-Cell Lymphoblastic Lymphoma (T-LL)
NCT00408005PHASE3COMPLETEDCombination Chemotherapy in Treating Young Patients With Newly Diagnosed T-Cell Acute Lymphoblastic Leukemia or T-cell Lymphoblastic Lymphoma
NCT00501826PHASE2RECRUITINGCombination Chemotherapy and Nelarabine in Treating Patients With T-cell Acute Lymphoblastic Leukemia or Lymphoblastic Lymphoma
NCT03504644PHASE1/PHASE2ACTIVE_NOT_RECRUITINGVenetoclax and Vincristine in Treating Patients With Relapsed or Refractory T-cell or B-cell Acute Lymphoblastic Leukemia
NCT04315324PHASE1/PHASE2RECRUITINGStudy to Test OBI-3424 in Patients With T-Cell Acute Lymphoblastic Leukemia (T-ALL) or T-Cell Lymphoblastic Lymphoma (T-LBL)
NCT01028716PHASE2TERMINATEDDonor Peripheral Blood Stem Cell Transplant in Treating Patients With Hematologic Malignancies
NCT02538926PHASE2WITHDRAWNEtoposide, Prednisone, Vincristine Sulfate, Cyclophosphamide, and Doxorubicin Hydrochloride With Asparaginase in Treating Patients With Acute Lymphoblastic Leukemia or Lymphoblastic Lymphoma
NCT06210750PHASE2WITHDRAWNAdding Targeted Drugs to Usual Chemotherapy for Adults With Newly Diagnosed T-Cell Acute Lymphoblastic Leukemia (T-ALL) and T-Cell Lymphoblastic Lymphoma (T-LBL)
NCT07476027EARLY_PHASE1NOT_YET_RECRUITINGEfficacy and Safety of CD7 CAR-T in Newly Diagnosed High-Risk T-LBL/ALL
NCT06741813Not specifiedNOT_YET_RECRUITINGAllo-HSCT vs ASCT in Adult T-LBL

Drugs tested across these trials (top 30)

MoleculeMax phaseTrials referencing
MERCAPTOPURINE ANHYDROUS48
NELARABINE44
PEGASPARGASE43
THIOGUANINE43
ASPARAGINASE42
CALASPARGASE PEGOL42
DARATUMUMAB41
DAUNORUBICIN41
LEUCOVORIN41
VENETOCLAX41
NAVITOCLAX31
CHEMBL397000101