T-lymphoblastic lymphoma

disease
On this page

Also known as Precur. T-lymphoblastic lymphomaprecursor T Lymphoblastic lymphomaprecursor T-cell Lymphoblastic lymphomaprecursor T-Lymphoblastic lymphomaT Lymphoblastic lymphoma

Summary

T-lymphoblastic lymphoma (MONDO:0044917) is a cancer and 27 clinical trials. Top therapeutic interventions include mercaptopurine anhydrous, nelarabine, and pegaspargase. A subtype of lymphoblastic lymphoma — broader associated-gene and molecular evidence is on the parent page (see Disease family below).

At a glance

  • Classification: Cancer
  • Clinical trials: 27

Clinical features

No curated clinical features (Orphanet) for this disease.

Identifiers

Disease identifiers

FieldValue
Canonical nameT-lymphoblastic lymphoma
Mondo IDMONDO:0044917
NCITC6919
SNOMED CT421246008
UMLSC1292758
MedGen266232
GARD0025922
Is cancer (heuristic)yes

Also known as: Precur. T-lymphoblastic lymphoma · precursor T Lymphoblastic lymphoma · precursor T-cell Lymphoblastic lymphoma · precursor T-Lymphoblastic lymphoma · precursor T-lymphoblastic lymphoma · T Lymphoblastic lymphoma · T-Lymphoblastic lymphoma · T-lymphoblastic lymphoma

Disease family

This is a subtype of lymphoblastic lymphoma. Genetic, therapeutic, and trial evidence is largely curated at the broader-term level — see the parent page for the associated-gene cohort and molecular evidence.

Classification path: human disease › disease by etiologic mechanism › cancer or benign tumorneoplastic disease or syndromeneoplasmhematopoietic and lymphoid system neoplasmhematopoietic and lymphoid cell neoplasmlymphoid neoplasm › precursor lymphoblastic lymphoma/leukemia › lymphoblastic lymphomaT-lymphoblastic lymphoma

Related subtypes (1): T-cell childhood lymphoblastic lymphoma

Genetics & variants

GWAS landscape

No GWAS associations recorded — common-variant (GWAS) studies don’t cover this disease (typical for Mendelian / rare diseases). See the curated gene cohort and Mendelian overlap below.

Variant details and genetic-evidence tiers

No tiered GWAS variants or ClinVar records for this disease.

Genes & proteins

No associated-gene cohort resolved for this disease. Atlas builds the molecular and therapeutic sections — associated genes, protein families, druggability, pathways, interactions, and drug associations — by aggregating over a disease’s associated genes (resolved via GWAS / GenCC / ClinVar / CIViC), and none resolved here. This is expected for antibody-mediated, autoimmune, or otherwise non-gene-defined conditions; the curated evidence for this disease is its clinical features, GWAS susceptibility, and clinical trials (above).

Function

No pathway enrichment — requires an associated-gene cohort.

Therapeutics

No druggable-target or therapeutic data for this disease’s cohort.

Clinical trials & evidence

Clinical trials

Clinical trials: 27.

Phase distribution (across all retrieved trials)

PhaseTrials
PHASE27
PHASE15
PHASE1/PHASE24
Not specified4
EARLY_PHASE13
PHASE32
PHASE41
PHASE2/PHASE31

Top trials by phase / activity

NCTPhaseStatusTitle
NCT03558412PHASE4UNKNOWNA Clinical Trial of Decitabine in Relapsed or Refractory T-lymphoblastic Lymphoma
NCT06434467PHASE3NOT_YET_RECRUITINGThe Efficacy and Safety of Nelarabine Injection in Patients With T-lymphoblastic Leukemia and T-lymphoblastic Lymphoma
NCT07072585PHASE2/PHASE3NOT_YET_RECRUITINGTesting the Addition of Daratumumab to Chemotherapy for Treating Patients With Newly-Diagnosed T-Cell Lymphoblastic Leukemia (T-ALL) and T-Cell Lymphoblastic Lymphoma (T-LL)
NCT00408005PHASE3COMPLETEDCombination Chemotherapy in Treating Young Patients With Newly Diagnosed T-Cell Acute Lymphoblastic Leukemia or T-cell Lymphoblastic Lymphoma
NCT00501826PHASE2RECRUITINGCombination Chemotherapy and Nelarabine in Treating Patients With T-cell Acute Lymphoblastic Leukemia or Lymphoblastic Lymphoma
NCT03504644PHASE1/PHASE2ACTIVE_NOT_RECRUITINGVenetoclax and Vincristine in Treating Patients With Relapsed or Refractory T-cell or B-cell Acute Lymphoblastic Leukemia
NCT04315324PHASE1/PHASE2RECRUITINGStudy to Test OBI-3424 in Patients With T-Cell Acute Lymphoblastic Leukemia (T-ALL) or T-Cell Lymphoblastic Lymphoma (T-LBL)
NCT06376721PHASE1/PHASE2RECRUITINGLinperlisib Combined With Camrelizumab and Pegaspargase in Advanced or Relapsed/Refractory NK/T-cell Lymphoma
NCT07523555PHASE1/PHASE2RECRUITINGAdaptive Dual-Target CAR-T Cells for Relapsed or Refractory Hematologic Malignancies
NCT01028716PHASE2TERMINATEDDonor Peripheral Blood Stem Cell Transplant in Treating Patients With Hematologic Malignancies
NCT02538926PHASE2WITHDRAWNEtoposide, Prednisone, Vincristine Sulfate, Cyclophosphamide, and Doxorubicin Hydrochloride With Asparaginase in Treating Patients With Acute Lymphoblastic Leukemia or Lymphoblastic Lymphoma
NCT02999633PHASE2TERMINATEDSafety and Efficacy of Isatuximab in Lymphoblastic Leukemia
NCT05576532PHASE2UNKNOWNVenetoclax Plus IM2 Regimen for Relapsed and Refractory T Lymphoblastic Lymphoma/Leukemia
NCT05745181PHASE2UNKNOWNClinical Study of Anti-CD1a CAR-T in the Treatment of R/R Acute T-lymphoblastic Leukemia/Lymphoblastic Lymphoma
NCT06210750PHASE2WITHDRAWNAdding Targeted Drugs to Usual Chemotherapy for Adults With Newly Diagnosed T-Cell Acute Lymphoblastic Leukemia (T-ALL) and T-Cell Lymphoblastic Lymphoma (T-LBL)
NCT06136364PHASE1RECRUITINGCD7 CAR-T in Adults With Relapsed or Refractory T-LBL/ALL Clinical Study
NCT01363817PHASE1COMPLETEDStudy to Evaluate the Safety and Tolerability of Weekly Intravenous (IV) Doses of BMS-906024 in Subjects With Acute T-cell Lymphoblastic Leukemia or T-cell Lymphoblastic Lymphoma
NCT04004637PHASE1UNKNOWNCD7 CAR-T Cells for Patients With R/R CD7+ NK/T Cell Lymphoma,T-lymphoblastic Lymphoma and Acute Lymphocytic Leukemia
NCT04828174PHASE1SUSPENDEDAnti-TRBC1 CAR-T Cell Therapy in Patients With TRBC1 Positive T Cell Malignancies
NCT05170828PHASE1WITHDRAWNCryopreserved MMUD BM With PTCy for Hematologic Malignancies
NCT06633341EARLY_PHASE1RECRUITINGTargeting CD5 CAR-T Cells in the Treatment of r/r CD5+ T-lymphoma
NCT07476027EARLY_PHASE1NOT_YET_RECRUITINGEfficacy and Safety of CD7 CAR-T in Newly Diagnosed High-Risk T-LBL/ALL
NCT04860817EARLY_PHASE1WITHDRAWNA Study of Anti-CD7 CAR-T Cells in Pediatric and Young Adult Patients With Relapse and Refractory T-ALL/ T-LBL
NCT06741813Not specifiedNOT_YET_RECRUITINGAllo-HSCT vs ASCT in Adult T-LBL
NCT04320992Not specifiedUNKNOWNA Multicenter Prospective Study of High Risk Molecular Typing in Patients With Adult T Lymphoblastic Lymphoma
NCT04582487Not specifiedUNKNOWNAdvancing Chemical and Genomic Strategies for Relapsed/Refractory T-ALL and ETP-ALL
NCT04620655Not specifiedUNKNOWNRD13-01 for Patients With r/r CD7+ T-ALL/T-LBL

Drugs tested across these trials (top 30)

MoleculeMax phaseTrials referencing
MERCAPTOPURINE ANHYDROUS47
NELARABINE45
PEGASPARGASE43
THIOGUANINE43
ASPARAGINASE42
CALASPARGASE PEGOL42
2-MERCAPTOETHANESULFONIC ACID41
DARATUMUMAB41
DAUNORUBICIN41
DECITABINE41
DIPHENHYDRAMINE41
ISATUXIMAB41
LEUCOVORIN41
RANITIDINE41
VENETOCLAX41
NAVITOCLAX31
LINPERLISIB21
OSUGACESTAT21
CHEMBL397000101
ZEBULARINE01