Thyrotoxicosis

disease
On this page

Also known as Graves disease, susceptibility to, 1GRD1

Summary

Thyrotoxicosis (MONDO:0010138) is a disease with 53 GWAS associations across 24 studies and 8 clinical trials. Top therapeutic interventions include thiamine ion and corticorelin. A subtype of hyperthyroidism — broader associated-gene and molecular evidence is on the parent page (see Disease family below).

At a glance

  • GWAS associations: 53
  • Clinical trials: 8

Clinical features

No curated clinical features (Orphanet) for this disease.

Identifiers

Disease identifiers

FieldValue
Canonical namethyrotoxicosis
Mondo IDMONDO:0010138
EFOEFO:0009190
MeSHD013971
DOIDDOID:7997
ICD-10-CME05
ICD-111470387017
NCITC61469
SNOMED CT90739004
UMLSC0040156
MedGen11814
Is cancer (heuristic)no

Also known as: Graves disease, susceptibility to, 1 · GRD1

Data availability: 53 GWAS associations (24 studies).

Disease family

This is a subtype of hyperthyroidism. Genetic, therapeutic, and trial evidence is largely curated at the broader-term level — see the parent page for the associated-gene cohort and molecular evidence.

Classification path: disease › human disease › disease by body system or component › endocrine system disorderthyroid gland disorderhyperthyroidismthyrotoxicosis

Related subtypes (9): toxic diffuse goiter, thyroid crisis, selective pituitary resistance to thyroid hormone, generalized resistance to thyroid hormone, familial gestational hyperthyroidism, familial hyperthyroidism due to mutations in TSH receptor, hyperthyroxinemia, familial dysalbuminemic, primary hyperthyroidism, secondary hyperthyroidism

Subtypes (1): neonatal thyrotoxicosis

Genetics & variants

GWAS landscape

53 GWAS associations across 24 studies. Top hits map to 13 distinct genes (as reported by GWAS).

Top associations by p-value

rsIDp-valueGeneRisk alleleOdds ratio
chr6:326339605e-147AG0.51
chr14:809909135e-54C0.25
chr2:2038741963e-35A0.2
rs92687911e-34HLA-DRA - HLA-DRB9?
rs107998242e-29MICOS10G0.22
rs92724456e-27HLA-DQA1C0.57
rs68850991e-23PDE8BA0.17
chr1:1137611861e-23A0.25
rs735750858e-23LINC01229, MAFTRRG0.17
chr1:198362214e-22C0.26
rs582660672e-21TSHRT0.16
rs787756206e-20TGC0.51
chr14:814495341e-19T0.18
rs3347066e-19NFIAG0.25
rs733982642e-18FAM227BT0.16
rs30872433e-18CTLA4 - ICOSG0.14
chr5:765316485e-17C0.17
chr10:60568612e-16C0.13
chr11:955782588e-16C0.17
chr16:797539761e-15C0.16
chr8:324065493e-15G0.18
rs7537602e-14PDE10AC0.13
rs102236663e-14VEGFA - LINC02537G0.13
rs78251753e-14NRG1G0.15
chr15:493990845e-14C0.14
chr16:797196745e-14G0.13
rs37587232e-13PRDM11T0.13
rs130209353e-12TESHLG0.12
chr1:195080123e-12T0.15
chr6:1660501191e-11A0.14

Top studies (by case count)

StudyLead authorYearCasesControlsTitle
GCST90473161UK Biobank Whole-Genome Sequencing Consortium20257,956450,484Whole-genome sequencing of 490,640 UK Biobank participants.
GCST90667836UK Biobank Whole-Genome Sequencing Consortium20257,956450,484Whole-genome sequencing of 490,640 UK Biobank participants.
GCST90475643Verma A20245,526441,420Diversity and scale: Genetic architecture of 2068 traits in the VA Million Veteran Program.
GCST90651161Liu TY20255,056212,391Diversity and longitudinal records: Genetic architecture of disease associations and polygenic risk in the Taiwanese Han population.
GCST90077728Backman JD20213,510328,244Exome sequencing and analysis of 454,787 UK Biobank participants.
GCST90081714Backman JD20213,510328,244Exome sequencing and analysis of 454,787 UK Biobank participants.
GCST90079730Backman JD20213,102383,241Exome sequencing and analysis of 454,787 UK Biobank participants.
GCST90083716Backman JD20213,102383,241Exome sequencing and analysis of 454,787 UK Biobank participants.
GCST90077729Backman JD20212,796326,256Exome sequencing and analysis of 454,787 UK Biobank participants.
GCST90081715Backman JD20212,796326,256Exome sequencing and analysis of 454,787 UK Biobank participants.

Variant details and genetic-evidence tiers

Tier distribution (top 50 variants)

TierVariants
Tier 1: coding0
Tier 2: splice/UTR0
Tier 3: regulatory0
Tier 4: intronic/intergenic49

MAF distribution

BucketVariants
common (>=0.05)22
low_freq (0.01-0.05)1
rare (<0.01)0
unknown26

Functional consequences

ConsequenceCount
unknown34
intron_variant14
intergenic_variant1

Top variants

rsIDChrPosAllelesMAFConsequenceGenep-valueTier
chr6:326339605e-147Tier 4: intronic/intergenic
chr14:809909135e-54Tier 4: intronic/intergenic
chr2:2038741963e-35Tier 4: intronic/intergenic
rs9268791632453296T>A,C,G0.05intron_variantHLA-DRA - HLA-DRB91e-34Tier 4: intronic/intergenic
rs10799824119514680G>A0.167intron_variantMICOS102e-29Tier 4: intronic/intergenic
rs9272445632637643C>A,T0.076intron_variantHLA-DQA16e-27Tier 4: intronic/intergenic
rs6885099577234524A>C,G,T0.462intron_variantPDE8B1e-23Tier 4: intronic/intergenic
chr1:1137611861e-23Tier 4: intronic/intergenic
rs735750851679714179G>C0.296intron_variantLINC01229, MAFTRR8e-23Tier 4: intronic/intergenic
chr1:198362210.1484e-22Tier 4: intronic/intergenic
rs582660671481002132T>A,C0.339intron_variantTSHR2e-21Tier 4: intronic/intergenic
rs787756208132869226C>T0.019intron_variantTG6e-20Tier 4: intronic/intergenic
chr14:814495340.3971e-19Tier 4: intronic/intergenic
rs334706161150575G>A,C0.086intron_variantNFIA6e-19Tier 4: intronic/intergenic
rs733982641549414220T>C0.22intron_variantFAM227B2e-18Tier 4: intronic/intergenic
rs30872432203874196G>A,T0.403intergenic_variantCTLA4 - ICOS3e-18Tier 4: intronic/intergenic
chr5:765316480.3835e-17Tier 4: intronic/intergenic
chr10:60568612e-16Tier 4: intronic/intergenic
chr11:955782588e-16Tier 4: intronic/intergenic
chr16:797539760.3131e-15Tier 4: intronic/intergenic
chr8:324065490.2013e-15Tier 4: intronic/intergenic
rs7537606165632995C>A,G,T0.317intron_variantPDE10A2e-14Tier 4: intronic/intergenic
rs10223666643837765G>A,C,T0.302intron_variantVEGFA - LINC025373e-14Tier 4: intronic/intergenic
rs7825175832558756G>A,C0.18intron_variantNRG13e-14Tier 4: intronic/intergenic
chr15:493990845e-14Tier 4: intronic/intergenic
chr16:797196745e-14Tier 4: intronic/intergenic
rs37587231145221961T>C0.252intron_variantPRDM112e-13Tier 4: intronic/intergenic
rs130209352216760956G>A,C,T0.334intron_variantTESHL3e-12Tier 4: intronic/intergenic
chr1:195080123e-12Tier 4: intronic/intergenic
chr6:1660501190.3211e-11Tier 4: intronic/intergenic

Genes & proteins

No associated-gene cohort resolved for this disease. Atlas builds the molecular and therapeutic sections — associated genes, protein families, druggability, pathways, interactions, and drug associations — by aggregating over a disease’s associated genes (resolved via GWAS / GenCC / ClinVar / CIViC), and none resolved here. This is expected for antibody-mediated, autoimmune, or otherwise non-gene-defined conditions; the curated evidence for this disease is its clinical features, GWAS susceptibility, and clinical trials (above).

Function

No pathway enrichment — requires an associated-gene cohort.

Therapeutics

Drugs indicated for this disease

0 approved, 2 in late-stage (phase 3) trials. Disease-direct ChEMBL indications, not inferred from the associated-gene cohort below.

DrugDevelopment status
CarbimazolePhase 3 (in late-stage trials)
PropylthiouracilPhase 3 (in late-stage trials)

Clinical trials & evidence

Clinical trials

Clinical trials: 8.

Phase distribution (across all retrieved trials)

PhaseTrials
Not specified8

Top trials by phase / activity

NCTPhaseStatusTitle
NCT06264544Not specifiedNOT_YET_RECRUITINGTrial to Evaluate the Efficacy of a Zinc, Selenium, and L-Tyrosine Supplement in the Prevention of Thyrotoxicosis in Subjects With r25191G/A SEPP1 Polymorphism
NCT01227499Not specifiedCOMPLETEDDifferential Diagnosis of STA-PSV in Thyrotoxicosis
NCT02767245Not specifiedCOMPLETEDThiamine Supplement in Patients With Severe Hyperthyroidism
NCT02886949Not specifiedUNKNOWNThe Association Between Autoimmune or Inflammation and Thyroid Disease
NCT03009357Not specifiedCOMPLETEDClinical Application of Pulse Rate-monitoring Activity Trackers in Thyrotoxicosis
NCT04485975Not specifiedCOMPLETEDTherapeutic Plasma Exchange in Thyrotoxicosis
NCT04806269Not specifiedUNKNOWNBiosignals by Wearables in Thyroid Dysfunction
NCT06391515Not specifiedCOMPLETEDSubacute Thyroiditis in the SARS-CoV-2 Era

Drugs tested across these trials (top 30)

MoleculeMax phaseTrials referencing
THIAMINE ION42
CORTICORELIN31