ICOS
gene geneOn this page
Also known as AILIMCD278
Summary
ICOS (inducible T cell costimulator, HGNC:5351) is a protein-coding gene on chromosome 2q33.2, encoding Inducible T-cell costimulator (Q9Y6W8). Stimulatory receptor expressed in activated or antigen-experienced T-cells that plays an important role in the immune response.
The protein encoded by this gene belongs to the CD28 and CTLA-4 cell-surface receptor family. It forms homodimers and plays an important role in cell-cell signaling, immune responses, and regulation of cell proliferation.
Source: NCBI Gene 29851 — RefSeq curated summary.
At a glance
- Gene–disease (curated): common variable immunodeficiency (Definitive, ClinGen) — +1 more curated relationship
- GWAS associations: 17
- Clinical variants (ClinVar): 208 total — 9 pathogenic, 5 likely-pathogenic
- GTEx eGene: eQTL in 3 tissues, sQTL in 0 (q < 0.05)
- Phenotypes (HPO): 32
- Drug target: yes — 4 curated mechanism-of-action drugs
- Constraint (gnomAD): pLI 0.00 (LoF-tolerant), LOEUF 1.27 (unconstrained)
- MANE Select transcript:
NM_012092 - Interaction hub: 2,132 STRING partners (top 6% of genes corpus-wide)
Identifiers
Gene identifiers
| Field | Value |
|---|---|
| HGNC ID | HGNC:5351 |
| Approved symbol | ICOS |
| Name | inducible T cell costimulator |
| Location | 2q33.2 |
| Locus type | gene with protein product |
| Status | Approved |
| Aliases | AILIM, CD278 |
| Ensembl gene | ENSG00000163600 |
| Ensembl biotype | protein_coding |
| OMIM | 604558 |
| Entrez | 29851 |
Gene structure
Transcript identifiers
Ensembl transcripts: 4 — 4 protein_coding
MANE Select: ENST00000316386
Transcript support level (Ensembl TSL; 1 = fully mRNA-supported): TSL 1: 2
ENST00000316386, ENST00000435193, ENST00000897354, ENST00001138099
RefSeq mRNA: 1 — MANE Select: NM_012092
NM_012092
CCDS: CCDS2363
Canonical transcript exons
ENST00000316386 — 5 exons
| Exon | Start | End |
|---|---|---|
| ENSE00001076433 | 203957799 | 203957883 |
| ENSE00001076434 | 203936763 | 203936872 |
| ENSE00001076436 | 203955636 | 203955971 |
| ENSE00001076437 | 203956659 | 203956765 |
| ENSE00003507544 | 203959586 | 203961577 |
Expression profiles
Bgee: expression breadth ubiquitous, 110 present calls, max score 79.37.
FANTOM5 (CAGE): breadth tissue_specific, TPM avg 7.1984 / max 718.3986, expressed in 181 samples.
Highest expression (Bgee): lymph node, vermiform appendix, thymus, granulocyte, epithelium of nasopharynx.
Genetic regulation across tissues (GTEx eQTL / sQTL)
ICOS is an eGene in GTEx v10 — its expression is genetically regulated (eQTL) in 3 tissues and its splicing (sQTL) in 0 (q < 0.05). Strongest associations first; slope = normalized effect of the lead variant’s alternative allele.
3 significant tissue × QTL associations:
| Tissue | QTL | q-value | Slope | Lead variant |
|---|---|---|---|---|
| Thyroid | eqtl | 3.9e-03 | -0.38 | 2:203633118:C:G |
| Artery Aorta | eqtl | 3.0e-02 | -0.36 | 2:204197738:A:G |
| Skin Sun Exposed Lower leg | eqtl | 3.9e-02 | +0.31 | 2:203761998:T:C |
FANTOM5 promoters
3 alternative TSS:
| Promoter ID | TPM avg | Samples expressed |
|---|---|---|
| 24785 | 6.5113 | 177 |
| 24786 | 0.4788 | 69 |
| 24784 | 0.2082 | 65 |
Top tissues by expression
showing 100 of 266 tissues by Bgee expression score (0-100, higher = more expressed):
| Tissue | Anatomy ID | Expression score | Quality |
|---|---|---|---|
| lymph node | UBERON:0000029 | 79.37 | gold quality |
| vermiform appendix | UBERON:0001154 | 76.97 | gold quality |
| thymus | UBERON:0002370 | 75.66 | silver quality |
| granulocyte | CL:0000094 | 75.36 | gold quality |
| epithelium of nasopharynx | UBERON:0001951 | 73.47 | gold quality |
| blood | UBERON:0000178 | 72.48 | gold quality |
| male germ line stem cell (sensu Vertebrata) in testis | CL:0000089 ∩ UBERON:0000473 | 71.18 | gold quality |
| caecum | UBERON:0001153 | 70.66 | gold quality |
| superficial temporal artery | UBERON:0001614 | 67.54 | gold quality |
| bone marrow | UBERON:0002371 | 66.27 | gold quality |
| tonsil | UBERON:0002372 | 65.23 | gold quality |
| spleen | UBERON:0002106 | 65.17 | gold quality |
| gall bladder | UBERON:0002110 | 64.88 | gold quality |
| palpebral conjunctiva | UBERON:0001812 | 63.07 | gold quality |
| rectum | UBERON:0001052 | 62.64 | gold quality |
| colonic epithelium | UBERON:0000397 | 60.97 | silver quality |
| right lung | UBERON:0002167 | 60.58 | gold quality |
| small intestine Peyer’s patch | UBERON:0003454 | 59.07 | gold quality |
| upper lobe of left lung | UBERON:0008952 | 59.06 | gold quality |
| upper lobe of lung | UBERON:0008948 | 58.63 | gold quality |
| bone marrow cell | CL:0002092 | 58.40 | silver quality |
| small intestine | UBERON:0002108 | 57.34 | gold quality |
| epithelial cell of pancreas | CL:0000083 | 57.33 | gold quality |
| gluteal muscle | UBERON:0002000 | 57.26 | gold quality |
| lung | UBERON:0002048 | 56.92 | gold quality |
| tendon of biceps brachii | UBERON:0008188 | 56.68 | gold quality |
| visceral pleura | UBERON:0002401 | 56.57 | silver quality |
| oral cavity | UBERON:0000167 | 56.41 | silver quality |
| triceps brachii | UBERON:0001509 | 56.16 | gold quality |
| esophagus squamous epithelium | UBERON:0006920 | 54.95 | silver quality |
| duodenum | UBERON:0002114 | 54.60 | gold quality |
| myocardium | UBERON:0002349 | 54.25 | gold quality |
| lower lobe of lung | UBERON:0008949 | 53.05 | silver quality |
| nasal cavity mucosa | UBERON:0001826 | 52.98 | gold quality |
| smooth muscle tissue | UBERON:0001135 | 52.96 | gold quality |
| mucosa of transverse colon | UBERON:0004991 | 52.94 | gold quality |
| omental fat pad | UBERON:0010414 | 52.89 | gold quality |
| peritoneum | UBERON:0002358 | 52.85 | gold quality |
| adipose tissue of abdominal region | UBERON:0007808 | 52.21 | gold quality |
| mucosa of sigmoid colon | UBERON:0004993 | 52.00 | gold quality |
| left uterine tube | UBERON:0001303 | 51.71 | gold quality |
| cervix squamous epithelium | UBERON:0006922 | 50.96 | gold quality |
| mucosa of urinary bladder | UBERON:0001259 | 50.75 | silver quality |
| olfactory segment of nasal mucosa | UBERON:0005386 | 50.67 | gold quality |
| frontal pole | UBERON:0002795 | 50.41 | gold quality |
| male germ cell | CL:0000015 | 50.33 | gold quality |
| middle frontal gyrus | UBERON:0002702 | 50.30 | gold quality |
| paraflocculus | UBERON:0005351 | 50.18 | gold quality |
| Brodmann (1909) area 10 | UBERON:0013541 | 50.18 | gold quality |
| right coronary artery | UBERON:0001625 | 50.15 | gold quality |
| sperm | CL:0000019 | 50.00 | gold quality |
| quadriceps femoris | UBERON:0001377 | 49.98 | gold quality |
| cardia of stomach | UBERON:0001162 | 49.95 | gold quality |
| urinary bladder | UBERON:0001255 | 49.62 | gold quality |
| vastus lateralis | UBERON:0001379 | 49.61 | gold quality |
| buccal mucosa cell | CL:0002336 | 49.49 | gold quality |
| cervix epithelium | UBERON:0004801 | 49.34 | gold quality |
| Brodmann (1909) area 46 | UBERON:0006483 | 49.30 | gold quality |
| blood vessel layer | UBERON:0004797 | 49.29 | gold quality |
| cerebellar vermis | UBERON:0004720 | 49.25 | gold quality |
| hair follicle | UBERON:0002073 | 49.18 | gold quality |
| olfactory bulb | UBERON:0002264 | 48.92 | gold quality |
| choroid plexus epithelium | UBERON:0003911 | 48.89 | gold quality |
| oviduct epithelium | UBERON:0004804 | 48.88 | gold quality |
| penis | UBERON:0000989 | 48.85 | gold quality |
| type B pancreatic cell | CL:0000169 | 48.83 | gold quality |
| cardiac muscle of right atrium | UBERON:0003379 | 48.55 | gold quality |
| CA1 field of hippocampus | UBERON:0003881 | 48.50 | gold quality |
| nasal cavity epithelium | UBERON:0005384 | 48.45 | gold quality |
| layer of synovial tissue | UBERON:0007616 | 48.43 | gold quality |
| left ventricle myocardium | UBERON:0006566 | 48.24 | gold quality |
| orbitofrontal cortex | UBERON:0004167 | 48.20 | gold quality |
| intestine | UBERON:0000160 | 48.16 | gold quality |
| upper arm skin | UBERON:0004263 | 48.06 | gold quality |
| tongue squamous epithelium | UBERON:0006919 | 47.92 | gold quality |
| metanephric glomerulus | UBERON:0004736 | 47.74 | gold quality |
| renal glomerulus | UBERON:0000074 | 47.60 | gold quality |
| cranial nerve II | UBERON:0000941 | 47.57 | silver quality |
| fallopian tube | UBERON:0003889 | 47.51 | gold quality |
| superior surface of tongue | UBERON:0007371 | 47.48 | gold quality |
| transverse colon | UBERON:0001157 | 47.46 | gold quality |
| kidney epithelium | UBERON:0004819 | 47.32 | gold quality |
| periodontal ligament | UBERON:0008266 | 47.14 | gold quality |
| diaphragm | UBERON:0001103 | 47.05 | gold quality |
| nephron tubule | UBERON:0001231 | 46.88 | gold quality |
| endometrium epithelium | UBERON:0004811 | 46.85 | gold quality |
| amniotic fluid | UBERON:0000173 | 46.78 | silver quality |
| deltoid | UBERON:0001476 | 46.38 | gold quality |
| muscle tissue | UBERON:0002385 | 46.31 | gold quality |
| esophagus mucosa | UBERON:0002469 | 46.12 | gold quality |
| body of stomach | UBERON:0001161 | 46.09 | gold quality |
| liver | UBERON:0002107 | 45.93 | silver quality |
| primordial germ cell in gonad | CL:0000670 ∩ UBERON:0000991 | 45.46 | silver quality |
| metanephros | UBERON:0000081 | 45.42 | gold quality |
| stomach | UBERON:0000945 | 45.40 | gold quality |
| pylorus | UBERON:0001166 | 45.35 | gold quality |
| dorsal motor nucleus of vagus nerve | UBERON:0002870 | 45.35 | gold quality |
| large intestine | UBERON:0000059 | 45.33 | gold quality |
| inferior olivary complex | UBERON:0002127 | 45.14 | gold quality |
| endometrium | UBERON:0001295 | 45.12 | gold quality |
Single-cell (SCXA)
Detected in 5 experiment(s), a significant marker in 5.
| Experiment | Marker? | Max mean expression |
|---|---|---|
| E-CURD-89 | yes | 1677.44 |
| E-CURD-122 | yes | 40.30 |
| E-CURD-88 | yes | 36.73 |
| E-CURD-46 | yes | 16.04 |
| E-ANND-3 | yes | 7.92 |
HPA expression
RNA tissue specificity: Group enriched
50 HPA tissues / cells by nTPM:
| Tissue / cell | Axis | nTPM | Protein (IHC) |
|---|---|---|---|
| Thymus | tissue | 18.8 | |
| Bone marrow | tissue | 15.6 | not detected |
| Tonsil | tissue | 15.2 | medium |
| Lymph node | tissue | 13.4 | medium |
| Appendix | tissue | 7.2 | low |
| Spleen | tissue | 3.1 | not detected |
| Urinary bladder | tissue | 2.5 | not detected |
| Lung | tissue | 2.5 | not detected |
| Gallbladder | tissue | 1.3 | not detected |
| Stomach 1 | tissue | 1.2 | not detected |
| Rectum | tissue | 1.2 | not detected |
| Small intestine | tissue | 1.0 | not detected |
| Colon | tissue | 0.7 | not detected |
| Duodenum | tissue | 0.7 | not detected |
| Esophagus | tissue | 0.5 | not detected |
| Spinal cord | tissue | 0.5 | |
| Prostate | tissue | 0.5 | not detected |
| Adipose tissue | tissue | 0.4 | not detected |
| Salivary gland | tissue | 0.4 | not detected |
| Liver | tissue | 0.4 | not detected |
| Breast | tissue | 0.3 | not detected |
| Smooth muscle | tissue | 0.3 | not detected |
| Cervix | tissue | 0.2 | not detected |
| Skin 1 | tissue | 0.2 | not detected |
| Testis | tissue | 0.2 | not detected |
| Vagina | tissue | 0.2 | not detected |
| Endometrium 1 | tissue | 0.2 | not detected |
| Thalamus | tissue | 0.2 | |
| Superior colliculi | tissue | 0.2 | |
| Substantia nigra | tissue | 0.2 | |
| Thyroid gland | tissue | 0.2 | not detected |
| Heart muscle | tissue | 0.1 | not detected |
| Pons | tissue | 0.1 | |
| Epididymis | tissue | 0.1 | not detected |
| Basal ganglia | tissue | 0.1 | not detected |
| Putamen | tissue | 0.1 | |
| Amygdala | tissue | 0.1 | |
| Medulla oblongata | tissue | 0.1 | |
| Hypothalamus | tissue | 0.1 | |
| Placenta | tissue | 0.1 | not detected |
| Kidney | tissue | 0.1 | not detected |
| Corpus callosum | tissue | 0.1 | |
| Adrenal gland | tissue | 0.1 | not detected |
| Hippocampal formation | tissue | 0.1 | |
| Entorhinal cortex | tissue | 0.1 | |
| Periaqueductal gray | tissue | 0.1 | |
| Olfactory bulb | tissue | 0.1 | |
| Fallopian tube | tissue | 0.1 | not detected |
| Septum | tissue | 0.1 | |
| Caudate putamen | tissue | 0.1 |
Brain sub-regions (HPA Brain Atlas): detected in 27; highest nTPM — Ventral spinal cord (0.5), Dorsal spinal cord (0.3), Motor hypoglossal nucleus (0.3), Nucleus gracilis (0.3), Nucleus tractus solitarii (0.3).
Regulation
Is transcription factor: no
Upstream regulators (CollecTRI, top): AP1, GATA3, HAND1, NFATC2, STAT3, STAT6, TBX21
miRNA regulators (miRDB)
Targeting ICOS by miRDB confidence (max_score; target_count = how many genes the miRNA targets in total — lower means more specific).
showing 30 of 117 miRNAs:
| miRNA | Max score | Avg score | miRNA target_count |
|---|---|---|---|
| HSA-MIR-29A-3P | 100.00 | 73.11 | 1835 |
| HSA-MIR-29B-3P | 100.00 | 73.18 | 1833 |
| HSA-MIR-29C-3P | 100.00 | 73.15 | 1833 |
| HSA-MIR-513A-5P | 100.00 | 69.77 | 2465 |
| HSA-MIR-3163 | 100.00 | 77.23 | 8605 |
| HSA-MIR-190A-3P | 100.00 | 80.35 | 5520 |
| HSA-MIR-4500 | 99.99 | 72.72 | 2367 |
| HSA-MIR-8068 | 99.98 | 73.85 | 2376 |
| HSA-MIR-27A-3P | 99.98 | 72.13 | 2955 |
| HSA-MIR-27B-3P | 99.98 | 72.13 | 2955 |
| HSA-MIR-9985 | 99.98 | 72.11 | 2939 |
| HSA-MIR-3692-3P | 99.98 | 70.27 | 2139 |
| HSA-LET-7A-5P | 99.98 | 72.29 | 1790 |
| HSA-LET-7B-5P | 99.98 | 72.31 | 1790 |
| HSA-LET-7C-5P | 99.98 | 72.29 | 1790 |
| HSA-LET-7E-5P | 99.98 | 72.29 | 1790 |
| HSA-LET-7F-5P | 99.98 | 72.56 | 1784 |
| HSA-LET-7G-5P | 99.98 | 72.37 | 1784 |
| HSA-LET-7I-5P | 99.98 | 72.37 | 1788 |
| HSA-MIR-98-5P | 99.98 | 72.33 | 1787 |
| HSA-MIR-570-3P | 99.96 | 72.41 | 4910 |
| HSA-MIR-590-3P | 99.96 | 74.34 | 6478 |
| HSA-MIR-4267 | 99.96 | 66.53 | 2368 |
| HSA-MIR-548AT-5P | 99.96 | 70.83 | 2666 |
| HSA-LET-7D-5P | 99.96 | 71.76 | 1632 |
| HSA-MIR-4458 | 99.96 | 71.64 | 1650 |
| HSA-MIR-767-5P | 99.95 | 70.85 | 993 |
| HSA-MIR-4731-5P | 99.89 | 67.23 | 2537 |
| HSA-MIR-5682 | 99.89 | 72.56 | 1005 |
| HSA-MIR-548AR-3P | 99.85 | 71.26 | 3889 |
Functional genomics
gnomAD constraint: pLI 0.00324, LOEUF 1.27, missense Z 0.851 — population loss-of-function intolerance (pLI ≥ 0.9 = LoF-intolerant; lower LOEUF = more constrained). gnomAD
Regional missense constraint (gnomAD RMC): no regional variation along ENST00000316386 — one region, missense o/e 0.86.
Literature-anchored findings (GeneRIF, showing 40)
- its polymorphism may contributes to the pathogenesis of spondyloarthropathy (PMID:11771526)
- Genetic polymorphism of the human ICOS gene. (PMID:11904679)
- role of ligation in modulating TCR-induced transcriptional profiles (PMID:12195015)
- ICOS reversely regulates IL-10 on re-activation of human effector T cells with mature dendritic cells. Interaction of ICOS with ICOS-L strongly promoted IL-10 secretion. (PMID:12207353)
- ICOS provides co-stimulation to memory t-cells [review] (PMID:12456021)
- Analysis of the upstream region of ICOS revealed an additional eight single nucleotide polymorphism (PMID:12753665)
- local immune responses may be modulated by H4/ICOS expressed on T cells in the joints of patients with rheumatoid arthritis, and thus it may be involved in the pathogenetic mechanism of rheumatoid arthritis. (PMID:12784384)
- ICOS is upregulated on human T cells after stimulation and can modulate both Th1 and Th2 cytokine production in the absence and presence of B7-1 (CD80) and B7-2 (CD86)costimulation. (PMID:12864987)
- Targeting of specific chemokine and chemokine receptor pathways and/or ICOS may have clinical application in the prevention and treatment of chronic allograft nephropathy. (PMID:12919091)
- AILIM has a role in regulating the signaling cascades for T-cell proliferation and IL-10 production (PMID:14550257)
- ICOS does not belong to the group of genes that, if mutated, present clinically as the hyper-IgM syndrome. (PMID:14610488)
- Highly expressed ICOS in activated CD4(+) lamina propria T cells of inflammatory bowel (IBD) contributes to dysregulated immune responses. Hyperexpression limited to inflammatory sites in IBD. Feasible therapeutic target for treatment of IBD. (PMID:14988837)
- A subtype of regulatory T cells in human blood can be identified by expression of ICOS after activation; these ICOS-expressing cells block the capacity of reciprocal ICOS-negative cells to proliferate and to produce cytokines. (PMID:15100277)
- ICOS expression on activated Th cells may provide a powerful means to amplify effector T cell responses in peripheral tissues, independently of the polarized state of the Th cells (PMID:15265908)
- AILIM/ICOS-B7h interactions play an important role in the endothelium in controlling the entry of memory/effector T-cells into inflamed tissues in the periphery. (PMID:15339883)
- The incidence of ICOS deficiency among patients with Common variable immunodeficiency is less than 5% (PMID:15507387)
- invariant NKT cell activation is regulated by CD28 and IOCS independently (PMID:15629449)
- A predominant effect of ICOS-mediated costimulation on T helper type 2 (Th2) cell differentiation in transgenic ICOS-deficient mice may be achieved by the enhancement of IL-4 receptor-mediated signaling. (PMID:15699127)
- ICOS is an influential costimulatory pathway in atherosclerosis & may play a protective role. It localizes with T cells in human aortic plaque. (PMID:15941568)
- This study could not confirm association with the CD28/CTLA4/ICOS gene region in multiple sclerosis. (PMID:16005527)
- Two variants in the ICOS promoter region are significantly associated with allergic sensitization and production of type 2 T helper (Th2) cell cytokines (PMID:16081771)
- ICOS is involved in abnormal T cell activation in systsemic lupus erythematosus (SLE) and blockade of the interaction between ICOS and its receptor may have therapeutic value in the treatment of this intractable disease. (PMID:16563187)
- There are no major effects of the CD28/CTLA4/ICOS gene region on susceptibility to primary sclerosing cholangitis but minor contributions cannot be excluded. (PMID:16638702)
- ICOS activation is associated with T helper type 1 (Th1) cell responses in human intracellular tuberculosis infection and may contribute to the amplification of those responses. (PMID:16670305)
- This review summarizes the evidence that ICOS expression regulates T-cell-dependent B cell responses and proposes a model for the role of ICOS in diseases characterized by dysregulated humoral immunity. (PMID:16790364)
- genetic variation in ICOS gene regulates the expression of both CTLA4 and ICOS and not only the splicing of sCTLA4 as suggested earlier. (PMID:16996590)
- Both the PI3-kinase/Akt and Rho family cascades operate coordinately to induce the forward migration of activated T cells by AILIM/ICOS signaling. (PMID:17077177)
- With multiethnic DNA panels that represent a wide spectrum of ethnic groups, we demonstrate long-range linkage disequilibrium among CD28, CTLA4, and ICOS costimulatory genes. (PMID:17197413)
- ICOS may be relevant in inducing an acute immune response and may be critically involved in perpetuating inflammation in chronically immune-mediated disorders of the peripheral nervous system. (PMID:17242332)
- These results define elevated populations of memory T-lymphocytes expressing B7 molecules in rheumatoid arthritis (RA) synovial fluid that either stimulate T cells through ICOS, or down-regulate RA synovial tissue T-lymphocytes through B7H1 and B7H2. (PMID:17323353)
- The whole blood gene expression quantities of costimulatory molecules CD154 and ICOS reasonably robustly differentiated rejection patients from control patients. (PMID:17414714)
- ICOS gene haplotypes correlate with IL10 secretion and multiple sclerosis. (PMID:17481737)
- Of 9 CVID patients…No mutations of SAP, ICOS, TACI, BAFFR, and CD19 were identified (PMID:18051214)
- definition of a newly discovered pathway that prevents autoimmunity by limiting the levels on T lymphocytes of aco-stimulatory receptor, the inducible T-cell co-stimulator(ICOS) (PMID:18172933)
- Modulation of immune responses by ICOS-expressing naturally occurring T regulatory cells present in melanoma tissue depends upon costimulatory signals delivered to the CD4-positive CD25-negative responder cells and the cytokine milieu. (PMID:18292519)
- p50alpha is likely a determining factor in ICOS-mediated PI3K activity in T cells (PMID:18641334)
- Children with type 1 diabetes show decreased inducrion of ICOS in T cells. (PMID:18973208)
- The shared CTLA4-ICOS risk locus in celiac disease, IgA deficiency and common variable immunodeficiency. (PMID:19020530)
- ICOS-induced T cell spreading and filopodia/microspike formation may promote antigen recognition by enhancing a T cell’s scanning potential of an adherent APC surface. (PMID:19095735)
- ICOS variants do not play a major role in the development of atopy in European children. (PMID:19175887)
Cross-species orthologs
2 orthologs
| Organism | Symbol | Gene ID |
|---|---|---|
| mus_musculus | Icos | ENSMUSG00000026009 |
| rattus_norvegicus | Icos | ENSRNOG00000046196 |
Mouse-model phenotypes
Observed phenotypes of the mouse ortholog (MGI:1858745) from MGI (Alliance of Genome Resources) — knockout/mutant phenotypes, ranked by annotation count. 53 distinct phenotype terms.
| Mouse phenotype (MP) | Records |
|---|---|
| decreased IgG1 level | 4 |
| abnormal immune system physiology | 3 |
| decreased IgG level | 3 |
| decreased IgE level | 3 |
| abnormal spleen morphology | 2 |
| abnormal Peyer’s patch germinal center morphology | 2 |
| abnormal T cell physiology | 2 |
| abnormal B cell physiology | 2 |
| abnormal immunoglobulin level | 2 |
| abnormal class switch recombination | 2 |
| abnormal CD4-positive, alpha-beta T cell physiology | 2 |
| small Peyer’s patches | 2 |
| decreased spleen germinal center number | 2 |
| decreased interleukin-4 secretion | 2 |
| abnormal interleukin level | 2 |
| abnormal leukocyte cell number | 1 |
| abnormal small intestine morphology | 1 |
| decreased IgA level | 1 |
| abnormal T cell differentiation | 1 |
| small lymph nodes | 1 |
| abnormal spleen germinal center morphology | 1 |
| abnormal B cell number | 1 |
| short tibia | 1 |
| decreased anti-insulin autoantibody level | 1 |
| abnormal cytokine secretion | 1 |
+28 more (showing top 25).
Additional cross-species homologs
Sequence homologs in species beyond Ensembl Compara’s model organisms, by Diamond local protein alignment (% sequence identity; best hit per species). Lower-identity rows are more distant homologs. The matched accessions’ gene symbols aren’t in biobtree yet, so each row shows the UniProt accession.
| Organism | UniProt | Identity | Method |
|---|---|---|---|
| Bos taurus | Q58DF9 | 73.4% | Diamond |
| Canis lupus familiaris | Q7YR73 | 72.7% | Diamond |
Genomic neighbors (locus context)
Genes flanking this one on the chromosome (NCBI/Entrez gene neighborhood). Positional context only — some neighbors share regulatory elements (bidirectional promoters, antisense/overlapping transcripts), but chromosomal adjacency is not itself a functional relationship (see Interactions for that).
| Symbol | Type | Entrez |
|---|---|---|
| CTLA4 | protein-coding | 1493 |
Protein
Protein identifiers
Inducible T-cell costimulator — Q9Y6W8 (reviewed: Q9Y6W8)
Alternative names: Activation-inducible lymphocyte immunomediatory molecule
All UniProt accessions (2): Q9Y6W8, Q53QY6
UniProt curated annotations — full annotation on UniProt →
Function. Stimulatory receptor expressed in activated or antigen-experienced T-cells that plays an important role in the immune response. Upon binding to its ligand ICOSL expressed on antigen presenting cells (APCs), delivers costimulatory signals that enhances all basic T-cell responses to a foreign antigen, namely proliferation, secretion of lymphokines including IL10, up-regulation of molecules that mediate cell-cell interaction, and effective help for antibody secretion by B-cells. Also acts as a costimulatory receptor critical for the differentiation of T follicular regulatory cells upon immune challenges such as viral infection. Mechanistically, potentiates TCR-induced calcium flux by augmenting PLCG1 activation and actin remodeling. In addition, activates PI3K signaling pathways independently of calcium flux. Essential both for efficient interaction between T and B-cells and for normal antibody responses to T-cell dependent antigens. Prevents the apoptosis of pre-activated T-cells. Plays a critical role in CD40-mediated class switching of immunoglobin isotypes.
Subunit / interactions. Homodimer; disulfide-linked. Interacts with ICOSLG. Interacts with PIK3R1. Interacts with TBK1; this interaction is critical for the maturation of T follicular regulatory cells.
Subcellular location. Cell membrane Secreted.
Tissue specificity. Activated T-cells. Highly expressed on tonsillar T-cells, which are closely associated with B-cells in the apical light zone of germinal centers, the site of terminal B-cell maturation. Expressed at lower levels in thymus, lung, lymph node and peripheral blood leukocytes. Expressed in the medulla of fetal and newborn thymus.
Post-translational modifications. N-glycosylated.
Disease relevance. Immunodeficiency, common variable, 1 (CVID1) [MIM:607594] A primary immunodeficiency characterized by antibody deficiency, hypogammaglobulinemia, recurrent bacterial infections and an inability to mount an antibody response to antigen. The defect results from a failure of B-cell differentiation and impaired secretion of immunoglobulins; the numbers of circulating B-cells is usually in the normal range, but can be low. The disease is caused by variants affecting the gene represented in this entry.
Induction. By phorbol myristate acetate (PMA) and ionomycin. Up-regulated early on T-cells and continues to be expressed into the later phases of T-cell activation.
Isoforms (2)
| UniProt ID | Names | Canonical? |
|---|---|---|
| Q9Y6W8-1 | 1 | yes |
| Q9Y6W8-2 | 2 |
RefSeq proteins (1): NP_036224* (*=MANE)
Domains & families (InterPro)
| ID | Name | Type |
|---|---|---|
| IPR013106 | Ig_V-set | Domain |
| IPR013783 | Ig-like_fold | Homologous_superfamily |
| IPR039943 | ICOS | Family |
Pfam: PF15910
UniProt features (22 total): strand 9, topological domain 2, glycosylation site 2, disulfide bond 2, signal peptide 1, chain 1, splice variant 1, mutagenesis site 1, helix 1, transmembrane region 1, domain 1
Structure
Experimental structures (PDB)
2 structures by resolution:
| PDB | Title | Method | Resolution (Å) |
|---|---|---|---|
| 7JOO | Crystal structure of ICOS in complex with antibody STIM003 and anti-kappa VHH domain | X-RAY DIFFRACTION | 2.4 |
| 6X4G | Crystal structure of ICOS in complex with ICOS-L and an anti ICOS-L VNAR domain | X-RAY DIFFRACTION | 3.5 |
Predicted structure (AlphaFold)
| Model | pLDDT | Fraction very-high |
|---|---|---|
| AF-Q9Y6W8-F1 | 74.24 | 0.22 |
Antibody-complex structures (SAbDab)
3 antibodies co-crystallized with this protein: 6X4G, 7JOO, ALOMFILIMAB
Human Protein Atlas
Protein class: CD markers, Predicted membrane proteins, Disease related genes, Human disease related genes, Primary immunodeficiency
Protein evidence: Evidence at protein level
Subcellular location (HPA, imaging): plasma membrane; actin filaments
Antibody reliability (HPA): IH approved · IF approved
Functional residue map
Curated UniProt residues grouped by drug-discovery relevance — catalytic, ligand-binding, modification, and mutation-validated positions. Source: UniProtKB sequence features.
Disulfide bonds (2)
| Type | Positions |
|---|---|
| Disulfide bond | 42–109, 63–83 |
Glycosylation sites (2)
| Type | Positions |
|---|---|
| N-linked (glcnac…) asparagine | 89, 110 |
Mutagenesis-validated functional residues (1)
| Position | Phenotype |
|---|---|
| 110 | about 4.3-fold improvement in binding affinity to icoslg. |
Function
Pathways and Gene Ontology
Reactome pathways
5 curated (TAS) of 10; 6 disease pathways. Curated-first; evidence = TAS (manually curated) vs IEA (electronic inference).
10 pathways:
| ID | Pathway | Evidence |
|---|---|---|
| R-HSA-2219530 | Constitutive Signaling by Aberrant PI3K in Cancer ⚕ | curated |
| R-HSA-9725371 | Nuclear events stimulated by ALK signaling in cancer ⚕ | curated |
| R-HSA-9927354 | Co-stimulation by ICOS | curated |
| R-HSA-6811558 | PI5P, PP2A and IER3 Regulate PI3K/AKT Signaling | curated |
| R-HSA-1257604 | PIP3 activates AKT signaling | curated |
| R-HSA-1643685 | Disease ⚕ | — |
| R-HSA-5663202 | Diseases of signal transduction by growth factor receptors and second messengers ⚕ | — |
| R-HSA-9725370 | Signaling by ALK fusions and activated point mutants ⚕ | — |
| R-HSA-9700206 | Signaling by ALK in cancer ⚕ | — |
| R-HSA-9938027 | Affinity selection of immunoglobulins | electronic |
MSigDB gene sets: 385 (showing top):
GOBP_REGULATION_OF_CELL_ACTIVATION, GOBP_TOLERANCE_INDUCTION, REACTOME_ADAPTIVE_IMMUNE_SYSTEM, GOBP_T_CELL_ACTIVATION_INVOLVED_IN_IMMUNE_RESPONSE, CHIARETTI_T_ALL_REFRACTORY_TO_THERAPY, GOBP_ALPHA_BETA_T_CELL_DIFFERENTIATION, GOBP_LYMPHOCYTE_COSTIMULATION, GOBP_POSITIVE_REGULATION_OF_CELL_ADHESION, GOBP_CELL_ACTIVATION_INVOLVED_IN_IMMUNE_RESPONSE, GOBP_CELL_CELL_ADHESION, GOBP_CD4_POSITIVE_ALPHA_BETA_T_CELL_ACTIVATION, DEURIG_T_CELL_PROLYMPHOCYTIC_LEUKEMIA_DN, GOBP_T_CELL_DIFFERENTIATION_INVOLVED_IN_IMMUNE_RESPONSE, GOBP_POSITIVE_REGULATION_OF_CELL_ACTIVATION, BYSTRYKH_HEMATOPOIESIS_STEM_CELL_AND_BRAIN_QTL_TRANS
GO Biological Process (5): T cell tolerance induction (GO:0002517), immune response (GO:0006955), T cell costimulation (GO:0031295), T follicular helper cell differentiation (GO:0061470), cell-cell adhesion (GO:0098609)
GO Molecular Function (2): signaling receptor activity (GO:0038023), protein binding (GO:0005515)
GO Cellular Component (3): extracellular region (GO:0005576), plasma membrane (GO:0005886), external side of plasma membrane (GO:0009897)
Reactome top-level categories
9 top-level categories:
| Category | Pathways |
|---|---|
| Signaling by ALK fusions and activated point mutants | 1 |
| Immunoglobulin maturation | 1 |
| Intracellular signaling by second messengers | 1 |
| PI3K/AKT Signaling in Cancer | 1 |
| Negative regulation of the PI3K/AKT network | 1 |
| Regulation of T cell activation by CD28 family | 1 |
| Disease | 1 |
| Diseases of signal transduction by growth factor receptors and second messengers | 1 |
| Signaling by ALK in cancer | 1 |
GO top-level categories
16 GO namespaces:
| Category | Terms |
|---|---|
| tolerance induction | 1 |
| immune system process | 1 |
| response to stimulus | 1 |
| lymphocyte costimulation | 1 |
| positive regulation of T cell activation | 1 |
| T-helper cell differentiation | 1 |
| exhausted T cell differentiation | 1 |
| cell adhesion | 1 |
| molecular transducer activity | 1 |
| binding | 1 |
| cellular anatomical structure | 1 |
| membrane | 1 |
| cell periphery | 1 |
| plasma membrane | 1 |
| cell surface | 1 |
| side of membrane | 1 |
Experimentally-supported GO annotations
GO terms backed by direct experimental evidence (ECO experimental codes) — 3 of 10 annotations. The rest are phylogenetic / computational / electronic (IEA).
3 experimentally-supported GO terms:
| GO term | NS | Evidence |
|---|---|---|
| T follicular helper cell differentiation | BP | direct assay |
| plasma membrane | CC | direct assay |
| signaling receptor activity | MF | direct assay |
Protein interactions and networks
STRING
showing 15 of 2,132 interactions by confidence (×1000):
| Protein A | Protein B | Partner UniProt | Score |
|---|---|---|---|
| ICOS | ICOSLG | O75144 | 952 |
| ICOS | CTLA4 | P16410 | 952 |
| ICOS | A0A087X1L8 | A0A087X1L8 | 944 |
| ICOS | CXCR5 | P32302 | 936 |
| ICOS | CD4 | P01730 | 919 |
| ICOS | PDCD1 | Q15116 | 892 |
| ICOS | CD274 | Q9NZQ7 | 884 |
| ICOS | CD80 | P33681 | 882 |
| ICOS | CD8A | P01732 | 866 |
| ICOS | CD40LG | P29965 | 862 |
| ICOS | FOXP3 | Q9BZS1 | 859 |
| ICOS | TNFRSF4 | P43489 | 857 |
| ICOS | IL2 | P01585 | 849 |
| ICOS | PDCD1LG2 | Q9BQ51 | 841 |
| ICOS | CD86 | P42081 | 836 |
IntAct
Human interaction partners of ICOS in IntAct, one row per partner (best MIscore; records = supporting IntAct interaction records).
7 partners by confidence:
| Partner | Interaction type | MIscore | Records |
|---|---|---|---|
| ICOSLG | physical association | 0.850 | 10 |
| PIK3R1 | association | 0.620 | 6 |
| TBK1 | physical association | 0.500 | 3 |
| WIF1 | physical association | 0.370 | 1 |
| GAK | association | 0.350 | 1 |
| TNF | association | 0.350 | 1 |
| TNFSF9 | association | 0.350 | 1 |
BioGRID (20 interactions; top human partners by supporting records): ACY1 (Affinity Capture-MS; 2 records), ICOSLG (Affinity Capture-MS; 2 records), TNF (Affinity Capture-MS; 2 records), CDC20B (Affinity Capture-MS), ITFG3 (Affinity Capture-MS), MFI2 (Affinity Capture-MS), NUFIP2 (Protein-RNA), PCDH1 (Affinity Capture-MS), PGK1 (Cross-Linking-MS (XL-MS)), PIK3R1 (Affinity Capture-Western), RC3H1 (Protein-RNA), TBK1 (Affinity Capture-Western), TNFSF9 (Affinity Capture-MS), TRHDE (Affinity Capture-MS), WIF1 (Two-hybrid)
SIGNOR signaling
4 signaling interactions:
| A | Effect | B | Mechanism |
|---|---|---|---|
| ICOSLG | “up-regulates activity” | ICOS | binding |
| ICOS | “up-regulates activity” | PIK3R1 | binding |
| hsa-mir-146a-5p | “down-regulates quantity by repression” | ICOS | “post transcriptional regulation” |
| hsa-mir-27a-3p | “down-regulates quantity by repression” | ICOS | “post transcriptional regulation” |
Ligand–receptor pairs (CellPhoneDB) (1)
Curated ligand–receptor partners (cell-cell communication), distinct from the protein–protein interactions above.
1 ligand–receptor pairs:
| Partner | This gene’s role | Signaling class |
|---|---|---|
| ICOSLG | receptor |
Disease & clinical
Genetic variants
Variant evidence for ICOS: 208 ClinVar records (14 pathogenic / likely pathogenic); 17 GWAS associations. Per-variant detail is on Sugi Variant.
ClinVar
208 variants total. Per-class counts are floors (≥ shown; pagination cap):
| Classification | Count (floor) |
|---|---|
| Pathogenic | 9 |
| Likely pathogenic | 5 |
| Uncertain significance | 84 |
| Likely benign | 66 |
| Benign | 24 |
Top pathogenic / likely-pathogenic (14)
Showing all 14 pathogenic / likely-pathogenic ClinVar records, ranked by ClinVar review status (expert panel → multiple submitters → single submitter), then by number of submitting labs.
| Variant ID | HGVS | Classification | Review | Submitters |
|---|---|---|---|---|
| 663980 | NM_012092.4(ICOS):c.58+1G>A | Likely pathogenic | criteria provided, multiple submitters, no conflicts | 2 |
| 940397 | NM_012092.4(ICOS):c.181del (p.Ile61fs) | Pathogenic | criteria provided, single submitter | 1 |
| 1359008 | NM_012092.4(ICOS):c.61G>T (p.Glu21Ter) | Pathogenic | criteria provided, single submitter | 1 |
| 1449576 | NM_012092.4(ICOS):c.318T>G (p.Tyr106Ter) | Pathogenic | criteria provided, single submitter | 1 |
| 2002817 | NM_012092.4(ICOS):c.17G>A (p.Trp6Ter) | Pathogenic | criteria provided, single submitter | 1 |
| 2003841 | NM_012092.4(ICOS):c.357del (p.Phe119fs) | Pathogenic | criteria provided, single submitter | 1 |
| 2993769 | NM_012092.4(ICOS):c.291C>A (p.Tyr97Ter) | Pathogenic | criteria provided, single submitter | 1 |
| 4728975 | NM_012092.4(ICOS):c.272dup (p.Ser91fs) | Pathogenic | criteria provided, single submitter | 1 |
| 573877 | NM_012092.4(ICOS):c.394+2T>C | Likely pathogenic | criteria provided, single submitter | 1 |
| 2585218 | NM_012092.4(ICOS):c.136_139del (p.Asp46fs) | Likely pathogenic | criteria provided, single submitter | 1 |
| 4871840 | NM_012092.4(ICOS):c.285del (p.Leu96fs) | Likely pathogenic | criteria provided, single submitter | 1 |
| 4959479 | NM_012092.4(ICOS):c.501+2T>A | Likely pathogenic | criteria provided, single submitter | 1 |
| 871366 | GRCh37/hg19 2q33.2(chr2:204820359-204821488)x0 | Pathogenic | criteria provided, single submitter | 1 |
| 5501 | NM_012092.4(ICOS):c.59-594_501+93del | Pathogenic | no assertion criteria provided | 1 |
Per-variant reference — Sugi Variant
Explore ICOS’s pathogenic and likely-pathogenic variants individually — each with its ClinVar classification and conditions, applied ACMG criteria (ClinGen expert panel, where curated), the calibrated in-silico predictors (AlphaMissense, REVEL, SaProt, conservation), gnomAD frequency, and the predictor-disagreement QC signal — on Sugi Variant.
SpliceAI
Top 10 splice-impact sites by Δscore (adjacent positions with the same effect merged into one range; 34 predictions of 285):
| Position(s) | Effect | Δscore | Sites |
|---|---|---|---|
| 2:203942270 | donor_gain | 1.0000 | |
| 2:203955631 | acceptor_gain | 0.9900 | |
| 2:203955786 | donor_gain | 0.9900 | |
| 2:203956657–203956658 | acceptor_loss | 0.9900 | 6 |
| 2:203956766–203956767 | donor_loss | 0.9900 | 5 |
| 2:203957884–203957885 | donor_loss | 0.9900 | 5 |
| 2:203936873–203936874 | donor_loss | 0.9800 | 3 |
| 2:203955634–203955635 | acceptor_loss | 0.9800 | 6 |
| 2:203955836 | donor_gain | 0.9800 | |
| 2:203955972–203955973 | donor_loss | 0.9800 | 5 |
AlphaMissense
123 missense substitutions predicted likely pathogenic (of 1,313 scored), across 43 residues. Top 20 hotspot residues, ranked by the number of likely-pathogenic substitutions (of those reachable by a single-nucleotide change), then by mean score:
| Residue | Likely-pathogenic substitutions | Mean am_pathogenicity | Max am_pathogenicity |
|---|---|---|---|
| C109 | 7 | 0.851 | 0.908 |
| C42 | 7 | 0.814 | 0.901 |
| C63 | 7 | 0.721 | 0.810 |
| C83 | 7 | 0.696 | 0.767 |
| F94 | 5 | 0.792 | 0.845 |
| F31 | 5 | 0.786 | 0.857 |
| F51 | 5 | 0.781 | 0.879 |
| Y107 | 5 | 0.655 | 0.780 |
| P116 | 5 | 0.653 | 0.731 |
| F119 | 4 | 0.833 | 0.899 |
| F114 | 4 | 0.776 | 0.817 |
| W142 | 4 | 0.670 | 0.756 |
| F95 | 3 | 0.816 | 0.816 |
| F33 | 3 | 0.794 | 0.794 |
| I40 | 3 | 0.785 | 0.877 |
| M53 | 3 | 0.762 | 0.832 |
| G146 | 3 | 0.689 | 0.696 |
| G157 | 3 | 0.666 | 0.692 |
| L96 | 3 | 0.656 | 0.702 |
| F182 | 3 | 0.648 | 0.648 |
HPA cancer prognostics
RNA cancer specificity: Low cancer specificity
Human Protein Atlas survival analysis — favorable = higher expression predicts better survival.
2 prognostic cancer types:
| Cancer | Prognostic | p-value |
|---|---|---|
| Cervical Squamous Cell Carcinoma and Endocervical Adenocarcinoma (TCGA) | favorable | 0.00046 |
| Head and Neck Squamous Cell Carcinoma (TCGA) | favorable | 0.000645 |
Disease associations
OMIM: gene MIM:604558 | disease phenotypes: MIM:607594
GenCC curated gene-disease
1 curated gene-disease records:
| Disease | Classification | Inheritance | Records |
|---|---|---|---|
| immunodeficiency, common variable, 1 | Strong | Autosomal recessive | 4 |
ClinGen Gene-Disease Validity
Expert-panel classifications — Definitive > Strong > Moderate > Limited > Disputed > Refuted.
1 validity classifications:
| Disease | Classification | Inheritance |
|---|---|---|
| common variable immunodeficiency | Definitive | AR |
Genomics England panels (PanelApp)
Clinical diagnostic gene panels including this gene (5 panels, 5 green/diagnostic-grade). Confidence: green = diagnostic, amber = moderate.
5 panels:
| Panel | Rating |
|---|---|
| COVID-19 research | green |
| Gastrointestinal epithelial barrier disorders | green |
| Infantile enterocolitis & monogenic inflammatory bowel disease | green |
| Intestinal failure or congenital diarrhoea | green |
| Primary immunodeficiency or monogenic inflammatory bowel disease | green |
Mondo (1): immunodeficiency, common variable, 1 (MONDO:0011864)
Orphanet (2): OBSOLETE: Common variable immunodeficiency (Orphanet:1572), Late-onset combined immunodeficiency due to ICOS deficiency (Orphanet:695183)
HPO phenotypes
32 phenotypes (HPO-id order):
| HPO | Term |
|---|---|
| HP:0000006 | Autosomal dominant inheritance |
| HP:0000007 | Autosomal recessive inheritance |
| HP:0000403 | Recurrent otitis media |
| HP:0000509 | Conjunctivitis |
| HP:0001287 | Meningitis |
| HP:0001744 | Splenomegaly |
| HP:0001904 | Autoimmune neutropenia |
| HP:0002014 | Diarrhea |
| HP:0002090 | Pneumonia |
| HP:0002110 | Bronchiectasis |
| HP:0002240 | Hepatomegaly |
| HP:0002664 | Neoplasm |
| HP:0002665 | Lymphoma |
| HP:0002716 | Lymphadenopathy |
| HP:0002718 | Recurrent bacterial infections |
| HP:0002720 | Decreased circulating IgA concentration |
| HP:0002721 | Immunodeficiency |
| HP:0002729 | Follicular hyperplasia |
| HP:0002837 | Recurrent bronchitis |
| HP:0002850 | Decreased circulating IgM concentration |
| HP:0002960 | Autoimmunity |
| HP:0004315 | Decreased circulating IgG concentration |
| HP:0005387 | Combined immunodeficiency |
| HP:0006532 | Recurrent pneumonia |
| HP:0010976 | Decreased total B cell count |
| HP:0011108 | Recurrent sinusitis |
| HP:0011462 | Young adult onset |
| HP:0011463 | Childhood onset |
| HP:0011839 | Abnormal total T cell number |
| HP:0011840 | Abnormal T cell physiology |
| HP:0030388 | Decreased class-switched memory B cell proportion |
| HP:0410301 | Partial absence of specific antibody response to unconjugated pneumococcus polysaccharide |
GWAS associations
17 associations:
| Study | Trait | p-value |
|---|---|---|
| GCST004866_12 | Alopecia areata | 2e-20 |
| GCST003988_11 | Hypothyroidism | 1e-15 |
| GCST004302_16 | Primary biliary cholangitis | 1e-13 |
| GCST000719_1 | Alopecia areata | 4e-13 |
| GCST006627_46 | Diastolic blood pressure | 3e-12 |
| GCST000612_31 | Celiac disease | 6e-9 |
| GCST004904_18 | Body mass index | 4e-8 |
| GCST005568_31 | Rheumatoid arthritis (ACPA-positive) | 4e-8 |
| GCST003045_68 | Ulcerative colitis | 1e-7 |
| GCST002931_2 | Aluminium levels | 3e-7 |
| GCST003043_157 | Inflammatory bowel disease | 5e-7 |
| GCST005569_4 | Rheumatoid arthritis | 5e-7 |
| GCST001762_612 | Obesity-related traits | 1e-6 |
| GCST005588_17 | Idiopathic dilated cardiomyopathy | 5e-6 |
| GCST009391_779 | Metabolite levels | 5e-6 |
| GCST009391_806 | Metabolite levels | 5e-6 |
| GCST009391_736 | Metabolite levels | 7e-6 |
EFO canonical traits (from GWAS)
7 canonical traits:
| EFO ID | Trait name |
|---|---|
| EFO:0004736 | aspartate aminotransferase measurement |
| EFO:0004340 | body mass index |
| EFO:0009094 | idiopathic dilated cardiomyopathy |
| EFO:0006336 | diastolic blood pressure |
| EFO:0010391 | sphingomyelin 16:0 measurement |
| EFO:0010396 | sphingomyelin 22:1 measurement |
| EFO:0010394 | sphingomyelin 18:1 measurement |
Drugs & pharmacology
Drug and pharmacology data
Is drug target: yes
ChEMBL targets (2): CHEMBL3712953 (SINGLE PROTEIN), CHEMBL5482971 (PROTEIN-PROTEIN INTERACTION)
Drugs by curated mechanism of action (ChEMBL)
Drugs whose curated ChEMBL mechanism of action targets the ICOS protein itself — single-protein targets only (drugs acting on a protein family or complex that merely includes it are excluded). Includes antibodies and oligonucleotides that bioactivity screening does not capture.
4 curated-mechanism drugs:
| Drug | Modality | Max phase |
|---|---|---|
| FELADILIMAB | Antibody | 3 |
| ROZIBAFUSP ALFA | Protein | 2 |
| VOPRATELIMAB | Antibody | 2 |
| MEDI-570 | Unknown | 1 |
PharmGKB: 1 entry (CPIC guideline: no)
GtoPdb / IUPHAR curated pharmacology
(IUPHAR/BPS Guide to Pharmacology — expert-curated)
Target class: other protein — CD molecules
Most potent curated ligand interactions (1 total), top 1:
| Ligand | Action | Affinity | Parameter |
|---|---|---|---|
| feladilimab | Binding | 8.87 | pKd |
ChEMBL bioactivities
6 potent at pChembl≥5 of 19 total, top 6 by pChembl (potency: 10 = 0.1 nM, 6 = 1 µM).
| pChembl | Type | Value | Unit | Molecule |
|---|---|---|---|---|
| 5.73 | IC50 | 1870 | nM | CHEMBL5591374 |
| 5.43 | IC50 | 3680 | nM | CHEMBL5592269 |
| 5.35 | IC50 | 4480 | nM | CHEMBL5591374 |
| 5.35 | Kd | 4470 | nM | CHEMBL5590462 |
| 5.33 | IC50 | 4680 | nM | CHEMBL2171562 |
| 5.25 | IC50 | 5650 | nM | CHEMBL5429501 |
PubChem BioAssay actives
6 with measured affinity, of 28 total; 5 most potent distinct compounds. Largely complementary to BindingDB; screening values are coarse (µM, 4 dp), so sub-nM hits tie at the floor.
| Compound | Assay | Type | Value | Unit |
|---|---|---|---|---|
| (2S)-4-amino-2-[[(2S)-2-[[(2S)-2-[[(3S,9S,12S,18S,21S,27S,30R,35R,38S,41S,44S,47S)-30-[[(2S)-2-amino-3-(4-hydroxyphenyl)propanoyl]amino]-41,44-dibenzyl-9,27-bis[(4-hydroxyphenyl)methyl]-38-(2-methylpropyl)-2,8,11,17,20,26,29,37,40,43,46-undecaoxo-18-propan-2-yl-32,33-dithia-1,7,10,16,19,25,28,36,39,42,45-undecazapentacyclo[45.3.0.03,7.012,16.021,25]pentacontane-35-carbonyl]amino]-4-methylpentanoyl]amino]-3-phenylpropanoyl]amino]-4-oxobutanoic acid | 2115250: Inhibition of ICOS/ICOSL (unknown origin) interaction by ELISA method | ic50 | 1.8700 | uM |
| (1R,4S,10S,13S,19S,22S,28S,34S,37S,40S,43S,46R,49S,55S,58S,61S)-37,40,58-tribenzyl-4,22,61-tris[(4-hydroxyphenyl)methyl]-43,49-bis(2-methylpropyl)-13-propan-2-yl-65,66-dithia-3,6,12,15,21,24,30,36,39,42,45,48,51,57,60,63-hexadecazaheptacyclo[44.17.4.06,10.015,19.024,28.030,34.051,55]heptahexacontane-2,5,11,14,20,23,29,35,38,41,44,47,50,56,59,62-hexadecone | 2115249: Inhibition of ICOS/ICOSL (unknown origin) interaction by TR-FRET assay | ic50 | 3.6800 | uM |
| 2-[3-[(1R,4S,7S,13S,19S,22S,25S,28S,31R,34S,40S,43S,49S)-40-benzyl-19-[(2S)-butan-2-yl]-22-(hydroxymethyl)-25,28-bis[(4-hydroxyphenyl)methyl]-4,49-bis(2-methylpropyl)-3,6,12,18,21,24,27,30,33,36,39,42,48,51-tetradecaoxo-53,54-dithia-2,5,11,17,20,23,26,29,32,35,38,41,47,50-tetradecazapentacyclo[29.20.4.07,11.013,17.043,47]pentapentacontan-34-yl]propyl]guanidine | 2115251: Binding affinity to ICOS (unknown origin) assessed as dissociation constant | kd | 4.4700 | uM |
| N-[3-(benzylamino)-6-chloro-9H-pyrido[3,4-b]indol-8-yl]pyridine-3-carboxamide | 1977233: Inhibition of C-terminal IgG1 Fc region fused human ICOS extracellular domain (1 to 141 residues)/C-terminal polyhistidine tagged human ICOSL extracellular domain (1 to 258 residues) interaction incubated for 1 hr by TR-FRET assay | ic50 | 4.6800 | uM |
| N-(6-chloro-7-methoxy-9H-pyrido[3,4-b]indol-8-yl)-4-methylpyrimidine-5-carboxamide | 1977233: Inhibition of C-terminal IgG1 Fc region fused human ICOS extracellular domain (1 to 141 residues)/C-terminal polyhistidine tagged human ICOSL extracellular domain (1 to 258 residues) interaction incubated for 1 hr by TR-FRET assay | ic50 | 5.6500 | uM |
CTD chemical–gene interactions
11 total (human), top 11 by PubMed support.
| Chemical | Actions (top 5) | PubMed papers |
|---|---|---|
| Air Pollutants, Occupational | affects expression, increases expression | 2 |
| Benzo(a)pyrene | decreases expression, increases methylation | 2 |
| Nickel | increases expression | 2 |
| (+)-JQ1 compound | decreases expression | 1 |
| Acetaminophen | increases expression | 1 |
| Air Pollutants | increases abundance, increases expression | 1 |
| Dieldrin | increases expression | 1 |
| Ozone | increases abundance, increases expression | 1 |
| Tobacco Smoke Pollution | increases expression | 1 |
| Aflatoxin B1 | increases methylation | 1 |
| Sodium Selenite | increases expression | 1 |
ChEMBL screening assays
7 unique, capped per target: 7 binding
Representative assays (with source publication via chembl_document):
| Assay ID | Type | Description | Source paper |
|---|---|---|---|
| CHEMBL5580017 | Binding | Binding affinity to ICOS (unknown origin) assessed as dissociation constant | Design of cyclic peptides as novel inhibitors of ICOS/ICOSL interaction. — *Bioorg Med Chem Lett* |
Cellosaurus cell lines
6 cell lines: 4 cancer cell line, 2 spontaneously immortalized cell line
First 10 cell lines (id-ordered, not curated):
| Cellosaurus | Name | Category | Sex |
|---|---|---|---|
| CVCL_A7ZZ | Raji-hICOS | Cancer cell line | Male |
| CVCL_B8HQ | Abcam HCT 116 ICOS KO | Cancer cell line | Male |
| CVCL_B8WZ | Abcam MCF-7 ICOS KO | Cancer cell line | Female |
| CVCL_B9K0 | Abcam A-549 ICOS KO | Cancer cell line | Male |
| CVCL_D7BJ | Abeomics CHO-K1 ICOS | Spontaneously immortalized cell line | Female |
| CVCL_E5IS | CHO-K1/ICOS | Spontaneously immortalized cell line | Female |
Clinical trials (associated diseases)
Via MONDO — disease-level, not drug-specific.
Predicted chemistry — Sugi Predict
The predicted patent-compound landscape for ICOS across ~30M SureChEMBL compounds — explore on Sugi Predict.
Related Atlas pages
- Associated diseases: immunodeficiency, common variable, 1, common variable immunodeficiency
- Targeted by drugs: Feladilimab
- Disease cohort memberships (association, not causation — diseases whose associated-gene cohort lists this gene; a subset are also under Associated diseases): alopecia areata, celiac disease, hypothyroidism, immunodeficiency, common variable, 1