ODC1 — 118 ClinVar variants
All ClinVar germline ODC1 variants across every classification, each assembled from ClinVar, gnomAD, AlphaMissense, conservation and more. 55 flagged for review →
5 Pathogenic · 6 Likely pathogenic · 1 Conflicting · 2 Benign · 1 Benign/Likely benign · 38 Likely benign · 65 Uncertain significance
Full ODC1 gene report on Sugi Atlas → Gene function, pathways, protein structure, constraint & interactions⚑ Evidence disagreements 55
Variants where the independent computational evidence doesn't line up with the clinical picture — a QC signal for a second look, not a reclassification.
Predictors agree, ClinVar conflicts 1
ClinVar submitters conflict, but the independent predictors unanimously agree — a QC review flag, not a reclassification.
-
ODC1 p.Asp35Asn
Conflicting
Single submitter
neurodevelopmental disorder with alopecia and brain abnormalities
Predictors lean, ClinVar uncertain 43
ClinVar classifies these uncertain (VUS), but the independent predictors unanimously lean one way — a triage signal for review, not a reclassification.
-
ODC1 p.Ile251Met
Uncertain significance
Multiple submitters
Inborn genetic diseases
-
ODC1 p.Pro264Leu
Uncertain significance
Multiple submitters
Inborn genetic diseases
- ODC1 p.Ala215Pro Uncertain significance Single submitter
- ODC1 p.Ala388Thr Uncertain significance Single submitter
- ODC1 p.Ala39Thr Uncertain significance Single submitter
-
ODC1 p.Ala413Val
Uncertain significance
Single submitter
Inborn genetic diseases
- ODC1 p.Ala442Thr Uncertain significance Single submitter
-
ODC1 p.Asn256Lys
Uncertain significance
Single submitter
neurodevelopmental disorder with alopecia and brain abnormalities
- ODC1 p.Asn2Lys Uncertain significance Single submitter
-
ODC1 p.Asp204Asn
Uncertain significance
Single submitter
Inborn genetic diseases
- ODC1 p.Asp214His Uncertain significance Single submitter
-
ODC1 p.Asp304Glu
Uncertain significance
Single submitter
neurodevelopmental disorder with alopecia and brain abnormalities
- ODC1 p.Asp305Asn Uncertain significance Single submitter
-
ODC1 p.Asp424Asn
Uncertain significance
Single submitter
neurodevelopmental disorder with alopecia and brain abnormalities
- ODC1 p.Gly226Asp Uncertain significance Single submitter
-
ODC1 p.Gly240Arg
Uncertain significance
Single submitter
Inborn genetic diseases
- ODC1 p.Gly240Glu Uncertain significance Single submitter
- ODC1 p.Ile23Leu Uncertain significance Single submitter
- ODC1 p.Leu24Arg Uncertain significance Single submitter
-
ODC1 p.Met131Ile
Uncertain significance
Single submitter
neurodevelopmental disorder with alopecia and brain abnormalities
- ODC1 p.Met221Val Uncertain significance Single submitter
-
ODC1 p.Met315Thr
Uncertain significance
Single submitter
Inborn genetic diseases
- ODC1 p.Met386Val Uncertain significance Single submitter
-
ODC1 p.Phe13Tyr
Uncertain significance
Single submitter
Inborn genetic diseases
-
ODC1 p.Pro346Ala
Uncertain significance
Single submitter
Inborn genetic diseases
-
ODC1 p.Pro373Leu
Uncertain significance
Single submitter
Inborn genetic diseases
- ODC1 p.Pro438Ser Uncertain significance Single submitter
-
ODC1 p.Ser303Phe
Uncertain significance
Single submitter
Inborn genetic diseases
- ODC1 p.Ser458Thr Uncertain significance Single submitter
-
ODC1 p.Ser91Arg
Uncertain significance
Single submitter
Inborn genetic diseases
- ODC1 p.Ser91Gly Uncertain significance Single submitter
- ODC1 p.Thr404Met Uncertain significance Single submitter
-
ODC1 p.Thr63Ala
Uncertain significance
Single submitter
Inborn genetic diseases
-
ODC1 p.Thr79Ile
Uncertain significance
Single submitter
neurodevelopmental disorder with alopecia and brain abnormalities
-
ODC1 p.Thr83Ala
Uncertain significance
Single submitter
Inborn genetic diseases
-
ODC1 p.Tyr122Asn
Uncertain significance
Single submitter
Inborn genetic diseases
-
ODC1 p.Tyr279Cys
Uncertain significance
Single submitter
Inborn genetic diseases
-
ODC1 p.Tyr350His
Uncertain significance
Single submitter
Inborn genetic diseases
-
ODC1 p.Tyr406Phe
Uncertain significance
Single submitter
ODC1-related disorder
-
ODC1 p.Tyr41Asn
Uncertain significance
Single submitter
Inborn genetic diseases
-
ODC1 p.Val191Asp
Uncertain significance
Single submitter
neurodevelopmental disorder with alopecia and brain abnormalities
-
ODC1 p.Val192Ala
Uncertain significance
Single submitter
ODC1-related disorder
-
ODC1 p.Val218Ile
Uncertain significance
Single submitter
Inborn genetic diseases
Predictors split 11
The independent predictors disagree with each other — read with care.
- ODC1 p.Gly84Arg Likely benign Multiple submitters
-
ODC1 p.Ala283Ser
Uncertain significance
Single submitter
Inborn genetic diseases
-
ODC1 p.Arg165Cys
Uncertain significance
Single submitter
Inborn genetic diseases
-
ODC1 p.Arg365Leu
Likely benign
Single submitter
Inborn genetic diseases
-
ODC1 p.Glu182Gly
Uncertain significance
Single submitter
Inborn genetic diseases
- ODC1 p.His146Tyr Uncertain significance Single submitter
-
ODC1 p.Leu363Phe
Uncertain significance
Single submitter
Inborn genetic diseases
-
ODC1 p.Met375Ile
Uncertain significance
Single submitter
Inborn genetic diseases
-
ODC1 p.Thr396Met
Uncertain significance
Single submitter
neurodevelopmental disorder with alopecia and brain abnormalities
- ODC1 p.Val194Ile Uncertain significance Single submitter
-
ODC1 p.Val77Met
Likely benign
Single submitter
Inborn genetic diseases
All ODC1 variants
Pathogenic 5
- c.1242-2A>G Multiple submitters neurodevelopmental disorder with alopecia and brain abnormalities
- c.1241+1G>T No assertion criteria neurodevelopmental disorder with alopecia and brain abnormalities
- p.Gln419Ter No assertion criteria neurodevelopmental disorder with alopecia and brain abnormalities
- p.Lys448Ter No assertion criteria neurodevelopmental disorder with alopecia and brain abnormalities
- p.Trp414fs No assertion criteria neurodevelopmental disorder with alopecia and brain abnormalities
Likely pathogenic 6
- c.914-1G>C Single submitter
- p.Asp433fs Single submitter neurodevelopmental disorder with alopecia and brain abnormalities
- p.Gln418Ter Single submitter
- p.Pro438fs Single submitter neurodevelopmental disorder with alopecia and brain abnormalities
- p.Trp356fs Single submitter neurodevelopmental disorder with alopecia and brain abnormalities
- p.Trp443Ter Single submitter neurodevelopmental disorder with alopecia and brain abnormalities
Conflicting classifications of pathogenicity 1
- p.Asp35Asn Single submitter neurodevelopmental disorder with alopecia and brain abnormalities ⚠
Benign 2
- p.Pro423= Multiple submitters
- p.Arg369Cys Single submitter
Benign/Likely benign 1
- p.Gly253Arg Multiple submitters Inborn genetic diseases
Likely benign 38
- p.Ala258Val Multiple submitters Inborn genetic diseases
- p.Gly84Arg Multiple submitters ⚠
- c.276+7G>A Single submitter
- c.450-17A>C Single submitter
- p.Ala156= Single submitter
- p.Ala20Thr Single submitter Inborn genetic diseases
- p.Ala452Thr Single submitter Inborn genetic diseases
- p.Arg178Lys Single submitter Inborn genetic diseases
- p.Arg365= Single submitter
- p.Arg365Leu Single submitter Inborn genetic diseases ⚠
- p.Arg369His Single submitter
- p.Arg449Cys Single submitter Inborn genetic diseases
- p.Asn3Thr Single submitter Inborn genetic diseases
- p.Cys217Gly Single submitter Inborn genetic diseases
- p.Gln129Arg Single submitter Inborn genetic diseases
- p.Gly276= Single submitter
- p.Gly321= Single submitter
- p.Gly387= Single submitter
- p.Gly446Arg Single submitter
- p.Ile189Thr Single submitter Inborn genetic diseases
- p.Leu14= Single submitter
- p.Leu59= Single submitter
- p.Lys115= Single submitter
- p.Lys349Gln Single submitter
- p.Met381Ile Single submitter Inborn genetic diseases
- p.Pro427= Single submitter
- p.Ser309= Single submitter
- p.Ser32Phe Single submitter Inborn genetic diseases
- p.Ser33Phe Single submitter Inborn genetic diseases
- p.Thr157Ala Single submitter Inborn genetic diseases
- p.Thr173Met Single submitter Inborn genetic diseases
- p.Thr301= Single submitter
- p.Thr390= Single submitter
- p.Tyr317= Single submitter
- p.Val225Ala Single submitter Inborn genetic diseases
- p.Val296Glu Single submitter Inborn genetic diseases
- p.Val77Met Single submitter Inborn genetic diseases ⚠
- p.Ser309Leu No assertion criteria ODC1-related disorder
Uncertain significance 65
- p.Ile251Met Multiple submitters Inborn genetic diseases ⚠
- p.Pro264Leu Multiple submitters Inborn genetic diseases ⚠
- c.1241+2T>G Single submitter Inborn genetic diseases
- c.1241+3A>C Single submitter
- c.1241+3A>T Single submitter
- c.585-2A>G Single submitter
- p.Ala215Pro Single submitter ⚠
- p.Ala283Ser Single submitter Inborn genetic diseases ⚠
- p.Ala388Thr Single submitter ⚠
- p.Ala39Thr Single submitter ⚠
- p.Ala413Val Single submitter Inborn genetic diseases ⚠
- p.Ala442Thr Single submitter ⚠
- p.Arg165Cys Single submitter Inborn genetic diseases ⚠
- p.Asn256Lys Single submitter neurodevelopmental disorder with alopecia and brain abnormalities ⚠
- p.Asn289fs Single submitter
- p.Asn2Lys Single submitter ⚠
- p.Asp204Asn Single submitter Inborn genetic diseases ⚠
- p.Asp214His Single submitter ⚠
- p.Asp304Glu Single submitter neurodevelopmental disorder with alopecia and brain abnormalities ⚠
- p.Asp305Asn Single submitter ⚠
- p.Asp424Asn Single submitter neurodevelopmental disorder with alopecia and brain abnormalities ⚠
- p.Glu182Gly Single submitter Inborn genetic diseases ⚠
- p.Glu8del Single submitter
- p.Gly102Arg Single submitter Inborn genetic diseases
- p.Gly226Asp Single submitter ⚠
- p.Gly240Arg Single submitter Inborn genetic diseases ⚠
- p.Gly240Glu Single submitter ⚠
- p.His146Tyr Single submitter ⚠
- p.Ile23Leu Single submitter ⚠
- p.Leu24Arg Single submitter ⚠
- p.Leu363Phe Single submitter Inborn genetic diseases ⚠
- p.Met131Ile Single submitter neurodevelopmental disorder with alopecia and brain abnormalities ⚠
- p.Met221Val Single submitter ⚠
- p.Met315Thr Single submitter Inborn genetic diseases ⚠
- p.Met375Ile Single submitter Inborn genetic diseases ⚠
- p.Met386Val Single submitter ⚠
- p.Phe13Tyr Single submitter Inborn genetic diseases ⚠
- p.Phe65fs Single submitter
- p.Pro346Ala Single submitter Inborn genetic diseases ⚠
- p.Pro373Leu Single submitter Inborn genetic diseases ⚠
- p.Pro438Ser Single submitter ⚠
- p.Ser167fs Single submitter
- p.Ser303Phe Single submitter Inborn genetic diseases ⚠
- p.Ser34del Single submitter
- p.Ser410Leu Single submitter
- p.Ser458Thr Single submitter ⚠
- p.Ser91Arg Single submitter Inborn genetic diseases ⚠
- p.Ser91Gly Single submitter ⚠
- p.Ter462Tyr Single submitter
- p.Thr396Met Single submitter neurodevelopmental disorder with alopecia and brain abnormalities ⚠
- p.Thr404Met Single submitter ⚠
- p.Thr63Ala Single submitter Inborn genetic diseases ⚠
- p.Thr79Ile Single submitter neurodevelopmental disorder with alopecia and brain abnormalities ⚠
- p.Thr83Ala Single submitter Inborn genetic diseases ⚠
- p.Trp356Ter Single submitter
- p.Tyr122Asn Single submitter Inborn genetic diseases ⚠
- p.Tyr279Cys Single submitter Inborn genetic diseases ⚠
- p.Tyr331fs Single submitter ODC1-related disorder
- p.Tyr350His Single submitter Inborn genetic diseases ⚠
- p.Tyr406Phe Single submitter ODC1-related disorder ⚠
- p.Tyr41Asn Single submitter Inborn genetic diseases ⚠
- p.Val191Asp Single submitter neurodevelopmental disorder with alopecia and brain abnormalities ⚠
- p.Val192Ala Single submitter ODC1-related disorder ⚠
- p.Val194Ile Single submitter ⚠
- p.Val218Ile Single submitter Inborn genetic diseases ⚠